Ola kino, Maʻi a me nā kūlana
Felty ka maʻi pale: Symptoms,ʻike,
Ma lalo o Felty ka maʻi pale pili i ka complication o rheumatoid arthritis, a ia lŘlŘ ma wale 1% o nā mea maʻi a pau me ka maʻi. Wela, Muscle atrophy, pigmentation a me ka susceptibility i infectious illnesses ano - IeAUPIIe, IAa IO pu a pau o kēia mau kumumea Felty ka maʻi pale. Pathologyʻike, ua nānā 'ana ma luna o ka mōʻaukala o rheumatoid arthritis, keʻano nui no keʻena hoʻokolohua kiko'î. Iapaau ana kŰiaʻai ana o corticosteroids, splenectomy. No ka lōʻihi manawa i pathology wehewehe aku e maopopo ano, a me ka lapaʻau kiʻi. I ka 1929, Felty AP ho'ākāka 'ia ma ka maʻi. O Paliuli a hiki i differentiated ka maʻi me he kuokoa nosology.
Felty maʻi pale: He aha ka mea?
I ka maʻi ua ho'ākāka 'ia ma ke alo o ka ekolu i ka wā hoʻokahi pathologies: ka rheumatoid arthritis, E hoomahuahua auanei spleen a me ka leucopenia (haʻahaʻa keʻokeʻo koko aeee). Kēia maʻi pale ua ana diagnosed i loko o kanaka mua o 40 makahiki, i hookuu i loko o ka nani ke keka.
Poe akamai i paipai i ke kumu o ka maʻi o ka autoimmune kaʻina. Ua puka mai me ka pololei komo o lymphoid nā'aʻaʻa a me ka mahope kahua o ka'ōnaehana paleʻea pono e like me kekahi nā mea'aʻaʻa. Pathology hoike aku me neutropenia me ka OAXA ka ho'ēmiʻana i loko o ia'ku i ka hapanui nā mea palahēhē, a me ka wā e hoʻomaka ai - i ka loa. No laila, i keia mea he splenectomy (ana o ka spleen) ua 'ike wale ka hoʻokō iaoia o ka lapaau.
Felty ka maʻi pale ua wehewehe aku ma ka 'ano, pinepine atypical. Maʻi e pākuʻi mua kekahi mau makahiki (5 a hiki i kahi o 10) maʻi ai-kapaia rheumatoid polyarthritis me i ka wā hoʻokahi komo i loko o pathological kaʻina interphalangeal ami, me ka loli iki ana degere o ka oolea.
Ma ka kekahi lima, i ka hapanui o nā mea maʻi i kēiaʻike, e hooponoponoia ia mea, ma ka typical hoikeana o connective'aʻaʻa. Kēia paha ia i ka mai kuni, i ke kahua o subcutaneous nodules, myocarditis, lilo o ke kaupaonaʻana, poliserozita.
Ke kumu nui
Ke etiology o ka maʻi mea IKE OLE IA. 'Aʻole i nā mea maʻi a pau me kaʻike, o "rheumatoid arthritis" e ulu i kēia pathology. Ma ka iwi ka lolo o ke ola i ke kanaka ke noke ala i lawe ia e keokeo koko keena. Nā mea maʻi i kēia maʻi pale, hoʻowahāwahā i ka kŘpa a haʻahaʻa holo, leukocytes i kekahi hana. Ka mea, e loaa i ka excessive dala ma ka spleen.
He aha hoailona Ukali aku Felty ka maʻi pale i loko o nā mākua?
- Articular maʻi pale (arthritis o na ami uuku).
- Mahuahua i ka nui o ke akepaʻa.
- Generalized lymphadenopathy (diagnosed i loko o 50% o ka hihia).
- Ka holumua ai mahuahua ma ka spleen nui (e like me ka manao ana palpation).
- Polyneuropathy.
- Pigmentation ma luna o kaʻili, na mai hehe ma ka Main.
- Eiei? Pulmonary fibrosis.
- Rheumatoid nodules.
A pau ma luna o hiʻona ka e ka mea e hiki ai i ka diagnose Felty ka maʻi pale. Nā symptoms a pau na nā mea maʻi i hoikeia okoa. No ka laʻana, i kekahi manawa hoʻonui o ka spleen ua malama wale ia ma na kahua o ka hoʻonaʻauao ma hope o ka maʻi? Acaeoey.
ʻike,
Ke kumu no ka hōʻoiaʻiʻo hope o ka lapaʻauʻike, o ka mea i ka wā hoʻokahi pu ana o ka splenomegaly a me rheumatoid arthritis. Ke koko ikea ai ua wehewehe aku ma ka anaemia, leukopenia, neutropenia. Ke immunoassay nō kāu huai ae RF kiʻekiʻe titers, ka CEC, i ke alo o antinuclear nā mea'aʻaʻa. E like me nā hualoaʻa myelogram ua diagnosed myeloid lolo hyperplasia me ka hoʻololi aiʻiliahi ke kelepona hele hehee wale. Instrumental ano o ka hoʻokolokolo 'ana (MRI, HI, ultrasound o na ami) e loa paha e hoʻolako iki ike. Felty ka maʻi pale ka loa nui e differentiate me ka cirrhosis a me ka sarcoidosis.
Walaʻauʻana me nā loina o ka lapaau
Inc, ma keia hihia komo ai i ka hulina kokoke loa i kahi. Rheumatoid arthritis ua malamaia lakou nei, me hae. Inc recurring nā mea palahēhē, a me ka arthritis me ai 'e kōkua rumatika ( "Azathioprine", "MTX").
Nā mea maʻi me ka nui nā mea palahēhē ka mea, ua pono ia e pule injections o ka ololi, i stimulates granulocyte lēpela. Ua kūpono i ka helu o ke keʻokeʻo koko keena.
XIX. Ai 'ke emi i ka symptomatology i pili ana i arthritis, Felty maʻi pale' ana. nā kēia nā: "Methotrexate", "Penicillamine".
Glucocorticoids i ka hoʻokō wale nō i loko o kiʻekiʻe dosages. I ole ia, ka mea, ua mahuahua ka likelihood o relapse. Ma ka kekahi lima, hooloihi ae i hoʻohana o glucocorticoids ke alakai i ka hooulu ana o intercurrent nā mea palahēhē.
Nā ana hoʻohālike no ka laulā o ke Inc:
- Mahuahua o ka helu ana o granulocytes i 2000 / mm o.
- Ka ho'ēmiʻana i loko o ka mea hiki wale mai o infectious complications o ke ano.
- Ka ho'ēmiʻana o ke kuni ho'āhewa wale.
- Ka ho'ēmiʻana o ulcers ma luna o kaʻili hoikeana.
I kaʻoki kino ua paipaiʻia?
Felty ka maʻi pale Pehea'ē aʻe e hiki ai oe i lanakila? Lapaʻau ma kaʻoki kino ua paipai ina lāʻau Inc ua ineffective paha no ka mai o kekahi kumu, ka mea, ua contraindicated. Ma keia hihia, ia mea IeAUPIIe, IAa IO he ninau o ke splenectomy. He nui no ka hoomanao ana i ka 25% o ka hihia o ka neutropenia recurs ma hope o kēia ina hana.
Ma lalo o splenectomy makemake ʻoki kino, oiai i ke kauka nō hoʻi ia moʻolelo paha hapa 'ia e lawe aku oe i ka spleen. I kēia lā, loaʻa nō nā nā papaha o ia ke kaʻina hana: laparoscopic a me ka hamama splenectomy.
Laparoscopy ua hana ka hoʻohana 'ana mau anesthesia. Ma keia hihia, no ka hana kŰia noi o ka lahilahi mea hana me ka pahupaʻiwikiō ma ka hopena, i ua kapaia he laparoscope. Ke surgeon i mau incisions liʻiliʻi i loko o ka abdomen ma i hoʻolauna iā 'na mea paahana no mahope manipulations. Ke loaa au, e like me ka rula, 'aʻole i koi nui manawa.
Open splenectomy komo ai i ka nui incision ma lalo o ka iwi, ma a ka surgeon e lawe aku oe i ka spleen. Ma hope o kēia wehe 'ana o ke kino i ke kino o ka hana, e wae i mai koʻohune a me nā mea hoʻomaʻi mai i ke koko ua markedly hoemiia.
hiki complications
Complications i loa ke nānā mai, a e hoike mai ai ia ia iho i loko o ka palapala o ka ruptured spleen, i ka ulu ana o ka ai-i kapaia o ka puka hypertension, gastrointestinal kahe ana ke kokoʻelemakule 'ia nā haumāna nā mea palahēhē.
ka hopena
Felty ka maʻi pale - he kŘpa a ke nānā maʻi, akā, e aho ka complication o ka pau pūʻulu o pathologies i keia la i diagnosed kākaʻikahi. 'aʻole i kēia manaʻo i ua hiki ole i kona lapaau, aʻaʻole i ka imi palapala hōʻoia no kōkua i ke kauka kūpono. N symptoms e Alert kela kanaka keia kanaka, a lilo i kumu no ka imi ana i aʻo mai i ka hoʻomalu. I ole ia, ka mea, ua mahuahua ka likelihood o ka mea hōʻemi o ka mau moku'āina a me ka ulu ana o pono hoʻopōʻino i ke ola complications, i loaʻa rupture o ka spleen wale. Ka mea wale nō ka hoʻokō hana AOAIAaOO e 'ike me ka splenectomy.
Mākou manaʻolana i nā mea a pau i ka hoakaka 'ike i loko o kēia' atikala i ka kumuhana makemake e maoli pono ia oe. E hoʻokaʻaʻike ola!
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