Ola kinoMaʻi a me nā kūlana

He aha ka mea - he maʻi pale Rokitansky-Otto Küstner? Maʻi pale Rokitansky-Otto Küstner: mea, lalau mai, symptoms, lapaʻau

Surrogacy e leie aku na keiki i ka wahine, ka poe i ola kumu hiki ole hāpai i kekahi keiki ma luna o lākou iho. Lākou helu, e like me ka 'ikepili helu, mahuahua mai ka makahiki i ka makahiki. Kekahi o na kumu no ka hoʻopiʻi kū'ē 'ana i nā lawelawe o ka surrogate makuwahine o Rokitansky-Otto Küstner maʻi pale. Nā kumu o ka maʻi, i ka symptoms a me ka walaʻauʻana ano o ka lapaʻau e e kūkākūkā i loko o kēia 'atikala. Oe e hoi aʻo paha i kekahi wahine me keia maʻi pale i na keiki.

pathology ano

Maʻi pale Rokitansky-Otto Küstner-Meyer-Hauser - he ke nānā gynecological maʻi. iloko ona i kakauia na inoa o nā kānakaʻepekema i hooku iho la ia i ka piha ano o ka pathology ma kona inoa. ¶ A i loko o ka 'inikua moʻokalaleo he mau synonyms o ka maʻi: vaginal atresia, aplasia o ka uterus. Naʻe, ka mea e ole noonoo a pau aʻe 'ana i loko o ke kino, typical o ka maʻi pale. Eia kekahi, vaginal atresia kānāwai ma muli o ka li nui paha surgeries. Pinepine, i ka inoa piha o ka maʻi, e emi i ka mua nā inoa o nā kānakaʻepekema a me ka makahiki "MRKH maʻi pale".

Ke pathology Ua wehewehe aku ma ka piha a hapa kaawale o ka uterus, like hoʻi me 2/3 o ka vagina. Ma keia hihia, he mea i ka ulu kūpono 'ana o nā ovaries a me ka wahine. I waiho waho kiʻekiʻe 'īnea i ano (kino lauoho ma luna o ka wahine' ano, umauma). Rokitansky-Otto Küstner maʻi pale ua diagnosed kākaʻikahi (kekahi hihia no tausani 5. Girls nā pēpē i).

mōʻaukala 'ike

Ka mua wehewehena o ka maʻi lā hoʻi i ka 1829 makahiki. German kauka Carl Mayer kaulana i vaginal aplasia ua pinepine pu ma keʻano o developmental abnormalities. A iki ma hope, i ka 1838, he pathologist mai Austria Karl av Rokitansky maʻi pale hōʻikeʻano hou. He manao ia ina keia maʻi mea i kaawale uterus, ovaries akā, mālama i ka hiki e kuleana pili i loa. I ka 1910, i ka Kelemānia kauka Kelemānia Kyustner ua hoʻoʻuluʻulu manaʻo i ka loaʻa 'ike ma luna o ka maʻi, ho onui i kona mau loina. Ke gynecologist i hoakakaia examples pinepine pu ana me ka aplasia uterine malformations hakuʻala ulu. I ka 1961, Kumu Zhorzh Hauzer mai Kuikilana? Aaeaaaaony i ka manawa "Otto Küstner Rokitansky-Mayer-maʻi pale". Nä känaka 'epekema paʻi i kona mau loina lehulehu o nā mea maʻi i kēiaʻike, a hukihuki lakou i ka noonoo ana i ka insensitivity i kane hormones i waena o nā mea maʻi. I ka makahiki 1977, Houser mua hooku iho la ia i kekahi hōʻike o ka atypical Lolina o pathology. Ua haawiia ka nui na makana o kānakaʻepekema, ka maʻi pale i kapaʻia no ka discoverers o eha inoa.

Kumu o ka maʻi

ʻO loko o ka embryonic wā fetal waiho anatomical mā mea i emi iho Otto Küstner-Rokitansky maʻi pale. Photos o nā keiki kao i kēiaʻike, ma hope o ka hānau mai i oko, mai ka poe o ko lākou ola na¯. Mamuli o ke kauoha Muller ka kumumanaʻo, ka fetus keka nā loko hoʻomōhala i ka lua o ka malama ma hope hapai ana. Ka hopena o ka hopena maikaʻi 'aʻe ma luna o ke kino o ke hapai i keia manawa hiki i kela maʻi i loko o nā keiki. Ma ka hanana o ka maʻi pale no hoi e loli ai connective'aʻaʻa dysplasia fetus ma i ka haunaele o kona 'ole ia lŘlŘ. Pathological loli alakai i ke kūpono 'ana o ka hemahema nā loko, i kekahi hoike ana o i mea no ka Otto Küstner-Rokitansky maʻi pale.

He aha kumumea ho ololi i ka hanana o ka maʻi i loko o ke kamaiki i hāpai keiki?

  1. Ikaika toxicosis.
  2. HIV i loko o ka makuwahine.
  3. Ka pilikia o ka abortion.
  4. E lawe i kekahi mau lapaʻauʻia (e like me corticosteroids).
  5. Alcohol hainā.

Ka maʻi pale Ua i hoʻolaha like hereditary maʻi. Eia naʻe, ma ka lapaʻau me ka hana pono, aia no na hihia a pau ma ka pathology diagnosed kekahi mau wahine o ka hookahi ohana.

Lapaʻau hoike ana mai o ka maʻi

Otto Küstner-Rokitansky maʻi pale ua hoʻomaka ana i ka hoike ma ka puberty ka wā malaila puberty meaola. Nā kaikamahine i nā ua hoʻokōʻia ka umauma, hoʻololi ka huahelu, he mea kino lauoho i aikane oe wahi. Haʻi kiʻekiʻe moe ano mai e ae kēia ola pilikia. He nui nā kaikamāhine manao papa'āweʻaweʻa kemika eha ma ka lalo abdomen wahi, ehaeha ma ka lalo hoʻi. Naʻe, i ka wa e kaawale aku o ka menstruation hiki aku ai, eʻimi i kōkua mai i ka gynecologist. Kekahi kumu no ka makaikai ana i ka hoʻomalu paha e ka pilikia o ka aikane oe ano. Pomaikai ole oe ma ka ho'āʻo 'o moe ke keakea ole pinepine ka hopena i trauma i ka perineum paha rupture o ka bladder. Hōʻike o ke kīnā o ke kino underdevelopment ke malama me ka rudimentary uterus me'āno'ē fallopian paipu. Kahi o 40% o ka maikai ke keka MRKH maʻi pale hui me malformations o ka urinary nenoaiu.

Mea Maluna o ka maʻi

Like nui no hoi na anomalies o embryonic? Acaeoey, Rokitansky-Otto Küstner maʻi pale i kekahi mau degere o ka oolea. ʻO ka nui o kela a me keia o ia me ka nānā 'ana i ke oolea o fetal abnormalities. He ekolu ano o ka maʻi.

  1. Typical MRKH maʻi pale (64% o na hihia a pau). Ua Ua wehewehe aku ma aplasia o ka uterus a me ka vagina.
  2. Atypical MRKH maʻi pale (24% o na hihia a pau). Ma keia maʻi, ke kaikamahine nalo uterus a me ka vagina, aia no he dysfunction o na ovaries.
  3. MURCS-ē aʻe (12% o na hihia a pau). 'O kēia ka loa hanahana loa ano o ka maʻi pale, a ua wehewehe aku ma kāna hana helu ma luna, a ua complemented ma ka'āno'ē kūpono' ana o ka iwi.

Ano o ka maʻi e hoʻoholo i ka pākōlea kou akamai, a kōkua kauka e i ka olelo wanana a no ke ola.

ki ina hana like o kaʻike,

He aha nana mea pono e hōʻoia i ka maʻi pale Rokitansky-Otto Küstner? Symptoms o ka maʻi i ole na wale ana no kaʻike,. hoʻomanawanui ninaninau hoʻomaka me ka pilikia makapō nana. I ka 75% o ka hoopii, ka mea aole e hoike aku i kekahi aʻe 'ana, no ka mea, ka mea kiʻekiʻe hiʻona hoʻopili like i kūmau. A laila, he kaha ma ka gynecological noho. Ke kaikamahine me ka hymenʻike, ua lawe mai ka mea o kaʻimiʻana. No ka typical pōkole vagina maʻi pale (i ka 2 knm), i mea ole ka hopena o ka cervix moana. Kekahi PalekanaEND_LINK koho mea he rectal ninaninau, iloko a ke kauka probes fallopian Tube a me ka uterine lua. Keia papa hana i ka mea e hiki ai e loiloi i ka degere o ke kahua o nā loko.

Papa ana o basal ana wela kōkua ho oholo i ka pae ana o ka menstrual kalapona e hōʻoia i ka piha ana o na ovaries. Eia hou, i ke kauka prescribes koko e ho'āʻo ai no hormones, MRI a me pelvic ultrasound. Ma pakahi aku la ia mea a pau e koi laparoscopicʻike.

Nā Papahana O Ka lapaʻau

Aia kaʻaoʻao hoʻokahi wale e hoola Rokitansky-Otto Küstner maʻi pale - aikane oe ea. Ana ma ke kahua o ka vagina kapa colpopoiesis i kona mālamaʻana lapaau i io i ka XIX kenekulia. Initially, ka hana hoʻohana i ka pono o na wahine me malamaia uterus hana. I kēia mau nā mea maʻi i ole mai i ke koko o ke kino, a me ke kiʻekiʻe o loaa i loko o ka abdominal lua. E like me ka hopena, ka mea, ua ua diagnosed me neoplastic keʻano o ka hanaʻana, a i pu e loa ka eha, a me ka like complications.

Currently paʻa colpopoiesis mau aoao:

  1. ? Anoe o ka vagina me ke kōkua o ka inflatable hoʻonui. Ke hana i ka lōʻihi manawa. Kona manaʻo mea hiki wale ina ka vaginal loa mea ole emi o 4 knm.
  2. Ho okumu neovaginy hapa o ka sigmoid AeXIeAaOIePEAaI paha ili o ka abdomen. Hoikehonua, loea ae, e hooponopono i ka mā me abdominal incisions - laparoscopically. Kauka pinepine makemake keia hana, i ke kahua o kaʻimi hoʻopunipuni vagina.

Ka mea maikaʻi makahiki no ka colpopoiesis o ka manawa mai ka 16 a hiki i 21 makahiki. Kēia manawa, i ka maturation hope o ka meaola. Ka manao wale no o ka vaginal ea - ā nā wāhine, e loaa i ka piha ke keka ola. E ole kona imperforate e ole haalele regular ke keka, ma ke kamepiula kekahi bougienage ina hana.

Complications ma hope oʻoki kino

He aha e na complications ma hope oʻoki kino e halawai me nā mea maʻi me kaʻike, o "Rokitansky-Otto Küstner maʻi pale"? Lapaau ana i ka maʻi ua i kekahi manawa pu e kekahi adverse hopena. Colpopoiesis - keia mea he nui hana. Like me kekahi 'ē aʻe' ano o keʻoki kino, he mea hiki i ka ulu ana o complications. Iwaena o lakou, i ka loa, he pono ole i sepsis a me ka peritonitis. Nō hoʻi, he nui nā mea maʻi ma hope o ka papa o ka lapaau, na kauka diagnosed kuʻi nukeliu neovagina pā. Kēia pathology e hoʻomōhala ai ma muli o ka nele o ka pololei, ke keka ola. Nolaila, kauka ikaika paipai aku i na wahine ole i ka malama ole ke keka.

Ei ma hope o ke ola

Loli ma ke kino i ka hana i loko o na wahine a me kaʻike, o "Rokitansky-Otto Küstner maʻi pale" Aʻole 'ae' e lawe mai reproductive hana i loko o ka kūlohelohe alanui. Eia naʻe, kēia ano o IVF a me surrogacy kōkua i na nā mea maʻi i liluwelo keiki. ʻepekema, Ua nei hōʻike maikaʻi hopena o kekahi mau pou uterus transplant hana. Ma hope o ka manawa, paha, transplantation o ke kino, e kōkua wahine me keia insidious maʻi ma luna o lākou iho, e amo keiki.

Infertility a me ka maʻi pale Rokitansky-Mayer-Otto Küstner

Hiki au i na keiki i kēia maʻi? Kēia ninau kupu mai ka nui loa na wahine, ka poe eʻalo i ka pathology. Ma neia hope aku, o kela mea keia o ia makemake e ho'āʻo i ka kūlana o ka makuwahine. Ka hapanui o na wahine a me keia maʻi pale hiki ole ke hoʻomanawanui i ke keiki. Inā na ovaries e functioning maʻamau, no laila poe akamai i paipai nā mea maʻi 'āinana apau me ka lawelawe ana o ka surrogate makuwahine. Ma keia hihia i ka pēpē ua hapai?

Ma ke kahua mua o ka surrogate makuwahine polokalamu, a me ka hana ino wahine ua hoakaka ia hormonal ai '. Ka hoʻohanaʻana i ai 'i loko o ka wā e leie aku oe, e synchronize lākou menstrual pōʻaiapuni. A laila, artificially inseminated ka wahine i ka hua maʻi pale MRKH me ka sperm o kana kane. I loko o kekahi mau lā o ko lākou mau "ulu" i loko o ka meakino i mimics i ka waiwai o ka fallopian paipu. Ma hope o nā lāʻekolu, i poe akamai i hoomaka e mālama '-implantation e hoomakaukau ai: ho oholo i ka wahine o ka embryo, i ke alo o ka chromosomal mā a me hereditary maʻi. Ma ka lima o ka lā originated embryo ua hoololiia i loko o ka uterus o ka surrogate makuwahine. I kekahi manawa, he papalua podsazhivanie, no ka mea hoike, i ka kolu a me ka lima ia o ka lā.

Ka helu o nā embryos hoololiia e oko ma luna o ka mea e like ai o ka aaiaoe mea, makahiki o ka hoʻomanawanui. Ma ka noi 'ana o ka wahine, i ka ua hanaʻole hua undergo cryopreservation ina hana. E like me ka hopena o keia hapai ana i loko o ke ao nei i loko o 9 mahina he mea he olakino pēpē. Naʻe, i kēia hana i nā kākoʻo a me nā hoa paio.

Kaawale e noonoo surrogacy. Ma na hana kūikawā nā keʻena lāʻau lapaʻau ma laila nō i ka ai-i kapaia o na wahine o ka waihona ipu, ka mea i makemake ia i ka like hana. IeAUPIIe, IAa IO ia mea opiopio, ola kaikamahine. Kekahi o na kumu no ka io ia ia i ka? Aaieou mea he maʻi pale Rokitansky-Otto Küstner-Meyer-Hauser. i hiki ke loaʻa Photos wā e hiki mai surrogate makuwahine i loko o kēia hōkeoʻikepili. Ka a pau kaʻina, mai ke koho ana o kekahi ikehu biomamy a pau hāpai keiki, hooponopono oaio papa lunakiaʻi. Pela ka mea, mea pono, e leka uila i ka poe akamai, e makemake ana ia ma mua o ke komo i loko o ka huli 'ana no ka hoʻoponopono. Wale ma keia aoao e noho paulele i loko o ka wā e hiki mai ola o kāu keiki.

e hōʻuluʻulu

Maʻi pale Rokitansky-Mayer-Otto Küstner - mea he aaiaoe maʻi wehewehe aku ma ka wa e kaawale aku ai hypoplasia o ka uterus a me ka vagina. Ua nui na kaikamahine ma mua puberty e ole e ike e pili ana i ola pilikia. Amenorrhea ke kumu no ia e ike i kekahi gynecologist. Ua ua i ka? Eaia ma ke akamai ka mea mua i ike i ke ola ana o ia i ka maʻi pale. Ma ka kekahi lima, ia mea typical ke maldevelopment o ka uterus a me ka vagina, a ma luna o ka mea 'ē aʻe - i ke alo o nā haumāna ke keka' ano. I kēia lā, loaʻa nō kekahi mau lapaʻau koho no ka maʻi. A pau o ia i mau ke hou, a inā. Ke Inc o ka maʻi mea, e wehe i ke kina ma aikane oe lula ea. E like me ka hopena, i ka hoʻomanawanui ke kiʻi pohaku uinihepa, o ka pilikia a me ka manaʻoʻike physiological, loaa ia ia ke ola a me ka hiki i na keiki. Me ka pili ana i ka hope wahi, ka mea pono kōkua o ke surrogate makuwahine.

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