Hirschsprung ka maʻi: symptoms i na keiki, Hawaii photo, kumu,ʻike, lapaʻau

Kekahi o ka undistributed pathologies o Hirschsprung ka maʻi. Symptoms i loko o na kamalii i hoikeia ma ka ikaika constipation. I kekahi manawa, i ka maʻi ke hana i loko o nā mākua. Akā, ka hapanui o nā keiki e ae mai ia ia. He He congenital maʻi i ua ili mai iā ia. Ua Ua diagnosed ka hapanui i loko o nā keikikāne. Ua hoike koke ma hope o ka hanau ana. A hiki i ka iapaau ana mea wale nō ka hoʻokōʻoki lāʻau lapaʻau 'uao.

pathology ano

Ua i ho'ākāka 'ia i ka maʻi i loko o ka makahiki 1887 ma ka Denemaka pediatrician Harold Hirschsprung, hope i kēia maʻi, a kapaʻia kona inoa. Initially, ua kapaia keʻano congenital gigantism AeXIeAaOIePEAaI. Pathology i kekahi inoa. Ua Ua kapaia congenital agangliozom AeXIeAaOIePEAaI. He aha ka Hirschsprung ka maʻi i loko o nā keiki?

Symptoms (Hawaii photo hōʻike pathology) e dictated e ke kanaka ano, a me i na paia o ka AeXIeAaOIePEAaI ka mea,ʻaʻole i hanaʻia nā aʻalolo ganglia. ʻo ia ka mea, ka pāʻana i nā nāʻiʻo i nei e kō ai ma ka liʻiliʻi. I ka wa e kaawale aku o ka ganglion nā aʻalolo ke kumu o ka Muscle'aʻaʻa i mea ole functioning. Nolaila, i ka ai, aole ia e holo i loko o ka naʻau liʻiliʻi nui. Kēia pathology ua kapa Hirschsprung ka maʻi. Symptoms i na keiki i kāheaʻia me constipation, maʻiʻaʻai a me ka li nui.

Ka mea hiki wale mai o ko Hirschsprung ka maʻi - 1 i ka 5000. O ka mea wale nō kekahi o nā pēpē i elima tausani ae aku mai keia maʻi. Loa pinepine i ka maʻi, e like me ka hōʻike ma luna, ua diagnosed i loko o nā keikikāne.

pathology hookomo ana i

ʻOiai ke ahulau i hōʻike i ka makahiki 1887, ka mea, i na mea he nui makahiki, e kuhikuhi i na kumu o ka muli a me ka hooulu ana i kēia maʻi.

Kauka e haawi mai kekahi mau kumu e hoonaukiuki i ka ulu ana o kaʻawaʻawa loa maʻi like Hirschsprung ka maʻi i loko o nā keiki.

Nā kumu o ka maʻi.

1. E like me ka hopena o ka hoʻokolokolo 'ana i ka mea i hoʻokumu i ka pathology ho okumu ia lŘlŘ a hiki ma ka utero. Nā aʻalolo huhui waina a lākou, a e lawe mai i ka mea mana ma ka digestion, e hanaʻia i loko o ka fetus mai ka 5 a hiki i 12 pule o ka hāpai keiki. Ma pohihihi keia hihia, no ka hooulu ana o nā aʻalolo keena ma ka digestive oihana o ke keiki mea i paʻa. Ma ka liʻiliʻi nui, ka mea, i ole hana. Nā kumu o kēia maʻi ua nō,ʻaʻole möakäka hou. Ua Ua manaoio ana pela hoikeia mutations ma ka DNA.
2. 'Ōlelo Aʻo i ka nā kūpuna i loko o ka hanana o kēia maʻi. Inā he mau hihia o ka maʻi i loko o ka 'ohana, a laila, i ka likelihood i ke keiki e hanau e maʻi, Ua kiʻekiʻe. No ina ka fetus mea kane, no ka mea, na keiki i loaa mai i kēia maʻi, he 4-5 manawa hou ma mua o kaikamahine pinepine.
3. I? Eou kahi malaila ua mahuahua ka pāhawewe, ka hapanui keiki hanau me Hirschsprung ka maʻi.
4. Ololi mea e pono ai i ke ano o ka maʻi o Down ka maʻi pale.
5. Pathology hiki hoʻomōhala i ka hopena o ka endocrine kāna hana i loko o ka makuwahine.

Mea Maluna o ka maʻi

He nui na ano o keia pathology like Hirschsprung ka maʻi (i loko o na keiki). Symptoms eʻikea au i loko o ka keiki, e hoike i ka ano o ka maʻi.

Aia nō i ke kēia mauʻano o ko Hirschsprung ka maʻi:

1. Compensated - constipation ana i ka wanaʻao elemakule. Makuakane me ia ma ka mea o ka hoʻomaʻemaʻe enemas no ka lōʻihi manawa.
2. Subkompensirovanaya - enema aʻole i kekahi e pono ai ia. E like me ka hopena, hoʻololi iho ia lŘlŘ kaumaha ka ho'ēmiʻana. Ke hoʻomanawanui Kahalaopuna kaʻehaʻeha a me kaʻeha i loko o ka abdomen. Ma keia palapala ana i ka maʻi ua malama i keʻano o ka dyspnea, anaemia. Pūnao undergoes mea hou.
3. Asthma - ka naʻau liʻiliʻi hiki ole e ua holoiʻia me ka hoomaemae enemas a me laxatives. Ma hope iho o kēia mau ana, i ka manao o ka naau ma ka lalo abdomen a me bloating, aole i pau. Ka wā e hoʻololi i kaʻai a kaumaha physical hoounauna hiki hoʻomōhalaʻoi intestinal iaʻi. Ma-hoʻomanawanui keiki i kēiaʻano o ka maʻi i ma subtotal a me ka huina pio.
4. Huʻi - na naau oʻu iaʻi i na kamalii uuku.

maʻi symptoms

I ka maʻi ke hoike mai ai ia ia iho i nā lā mua o ke ola. No ka laʻana, ina o ka naʻau liʻiliʻi eʻaʻole kahe i loko o ke keiki i nā lā mua o ke ola, ka mea i pono, e nana i ka bebe, e kuhikuhi i na kumu a me kaʻike,. Paha keia mea Hirschsprung ka maʻi.

Symptoms i na keiki, ka mea e hoʻolohe, e nana me keia. Child hoole ai. He Ka me constipation. Nā naʻau liʻiliʻi mea i nele. Pehu'ōpū. Aia ka maʻi o. Kēia mea he PAaIEN i ka pēpē Hirschsprung ka maʻi. Symptoms i loko o na keiki ana, i hookuu i loko o ka malama mua o ke ola.

Naʻe, i ka maʻi hiki e iho i manao nui hope. No laila, 'oe e pili loa kanaka hoʻoponopono i ka moku'āina o ke ola i koe. Koke e kelepona i kou mau kauka ina e ike i na hoailona ua like no me Hirschsprung ka maʻi i loko o nā keiki.

Symptoms o ka maʻi i ke hana i na kamalii uuku ma lalo o hoʻokahi makahiki.

• constipation;
• 'ole' ana i ka ho onui ana ke kaupaonaʻana;
• ka puhi mai o ka abdomen;
• ka luaʻi;
• diarrhea.

I ka manawa kūpono o ka hanana o ka maʻi ua hoike hope i loko o ke ola.

Pu ma ka malaise kēia symptoms:

• maʻi constipation;
• noho mai ribbons;
• ka liʻiliʻi loa hoakaka hookuu.

He aha hou aʻe nō ia e lohe?

I ka papa kuhikuhiE symptom o ka maʻi o ka naʻau liʻiliʻi nui i maʻi constipation. I ka breastmilk hanai ana i ka symptom e ole ana. Ola symptoms e ala wale i ka manawa ia mea manuahiʻai hoʻolauna i loko o kaʻai o nā hunahuna. Ua relieves ka noi o ka enema. Akā, me ka pono ole, ua malamaia wale i loko o ka kakahiaka kahua o ka hoʻonaʻauao. A laila, e hoʻohana i enema ekolu pohaku, e haawi aku i ka makemake hopena.

Hoʻololi i ka nui a me ke kinona o ka abdomen, Aia haʻahaʻa-wrenching'ōpū - ka mea, Aloha no hoi nā hoailona e pono ka uku hoolohe ia. I ka hoʻohālana ua hoʻoneʻe AeXIeAaOIePEAaI a me ka opu i asymmetric ole shape.

Ka luaʻi e ia lŘlŘ i loko o kēia maʻi, e kokua i ke kino pakele o ka noho, kaʻapu kōheoheo iā ia.

Hirschsprung ka maʻi hiki ke 'akomi i kekahi ma ka adulthood. Mau hoʻomanawanui iki mai kamaʻilioʻana, e hana eha iaʻi mai ka kamaliʻi constipation. Ka mea, e pono ai ka lapaʻauʻia, e kōkua naʻau i ka hele. Ka mea, ohumu o ka paakikiʻeha i loko o ka abdomen, pinepineʻalo me ka flatulence.

pathology lapaʻau '

He nui ke koke kuhikuhi i ka maʻi.

ʻike, a Hirschsprung ka maʻi i loko o nā keiki mai nā 'o ia ano:

1. Rectal ninaninau. Hōʻike ma ka rectum nele hue. Aia mea a piʻi aʻela ka haʻawina o ka sphincter.
2. Sigmoidoscopy. Ka loaʻaʻana o nā pilikia i loko o kaʻoʻoleʻa loa o ka rectum, a me ke kaawale ana o kekahi mea uuku nui o feces.
3. X-Ray. Huai ae kaʻeho, a hoomahuahua i ka loop o ka AeXIeAaOIePEAaI.
4. Ergography. AeXIeAaOIePEAaI puka lou, a mahuahua nui mai i 10-15 knm ma anawaena. Ka mea pili i ka mea a pau abdominal lua.
5. E hooholo ia ana o barium mai paha. Ke Akä naÿe no nä konohiki hele ma ka gastrointestinal'āpana, hoopaa iho la i loko o ka AeXIeAaOIePEAaI. Mai laila ia mea he lōʻihi manawa, aole ia i hele mai. I kekahi manawa, hoʻokaʻulua mai i 5 mau lā.
6. Ultrasound intestinal wahi.
7. Anorectal manometry. Ana puʻe i loko o ka naʻau liʻiliʻi.
8. Kolonosokopiya. Hookupaa iho la ia a hōʻoleʻia kāna e kaʻikepili i hoike X-Ray.
9. A biopsy o ka rectal pa no Swanson. Hoʻoholo i ke alo o nā aʻalolo ganglia i loko o ka AeXIeAaOIePEAaI ma ka extracting apana nahaha AeXIeAaOIePEAaI pa.
10. Histochemistry. Nā pūʻulu i ka ha awina o ka'ūhū acetylcholinesterase'aʻaʻa.

makeʻe kulana lapaʻau

Mai hilinai aku maluna o ua Inc. Hirschsprung ka maʻi maikaʻiʻole i loko o nā keiki ua lawe mai i loko o ka hapanui o na hihia wale nō eʻoki kino. Makeʻe kulana Inc nui lawelawe 'ana me ka makaukau no ka houʻoki kino.

Hoomakaukau lapaʻau nā:

1. A kekahiʻai, iʻai. Paipai ia ai ka lau, hua, haleʻuwī waiū huahana, ai mea 'aʻole ole i kinoea ho okumu.
2. Lomilomi, physiotherapy, gymnastics. Ka mea, hoʻoulu intestinal motility.
3. Hoʻomaʻemaʻe enema.
4. Intravenous aaieieno? O proteinaceous medicaments a me electrolyte pāʻoihana.
5. Nā wikamina.

ʻoki lāʻau lapaʻau lapaʻau

O, ka mea, e leie aku ka hoʻomanawanui ma hope o hoʻopulapula kiʻi pohaku uinihepa, a Hirschsprung ka maʻi.

Ka loa pono makahiki o ke keiki no kaʻoki kino ua noʻonoʻo no 2-3 makahiki. E hoomakaukau oukou i ke hoʻomanawanui no kaʻoki kino ma ka hale. I loko o kekahi mau pule, e pono e hahai i kaʻai, na naau oʻu ka neʻe 'ana i ke kōkua o enemas. Specialʻai pono e waiho ma ka hele ana i kahuna lapaau e pono e lawe i ka mooolelo o ka makahiki o ke keiki, a pau nā hiʻona o ke kino, e like me ka pono me ke kahua o ka? Acaeoey o keia kaʻawaʻawa loa mai me Hirschsprung ka maʻi i loko o nā keiki.

Ma hope o kaʻoki kino, ke kamaiki e e ike ia e kekahi kauka i loko o 2 makahiki. I keia manawa, ke kauka i kekahi kanakaʻai no kāu keiki. Na makua e malama i ka maka ma luna o ke keiki noho. ? Aeiiaiaiaaia e waiho i nā hunahuna enema kēlā lā, i hoʻokahi a me ka ia manawa. He mea pono e kūkulu i ka reflex na naau oʻu neʻeʻana.

ka hopena

Hirschsprung ka maʻi mea pilikia loa. Ua hiki ke hōʻike i koke. Ma keia hihia i ke keiki e loaa mai abdominal eha, nausea, ka luaʻi, lōʻihi manawa. I nā mākua Pono e kanaka hoʻoponopono i ka regularity o ka noho, a me ka keiki ma ka iki aʻe 'ana e hele i ke kauka.