Ola kinoMaʻi a me nā kūlana

Spondiloepifizarnaya dysplasia o ka luna, a malaloʻaoʻao: nā kumu a me nā 'ano o ka hana

Nei, na hihia o ka spondiloepifizarnoy dysplasia. Kēia mea i ke kaʻina o ka maʻi i loko o ka ulu o ka iwi'aʻaʻa i loko o ke kanaka kino. Spondiloepifizarnaya dysplasia ia akulla i X-Ray examinations, a ua māheleʻia i loko o ka papa kuhikuhiE pūʻulu ekolu:

  • Plastispondiliya generalized palapala.
  • Epifiznaya dysplasia Plural palapala.
  • Epiphyseal dysplasia, metaphyseal.

Hiʻona o ka maʻi

People me keia maʻi hemahema'opihia vertebrae, a lawe i ole shape. Oe e loaʻa ia ma ka radiograph. Spondiloepifizarnaya dysplasia ke'ākoʻakoʻa no i kekahi ano o ka loaa pathologies o ka spine. No laila, ma ka mea e kuhikuhi i ka maʻi, he mea pono e hoohalike mau X-Ray kiʻi, a i hana ma kekahi mau makahiki.

I ka papa kuhikuhiE symptom o ka maʻi mea e emi ka lōʻihi o na lala (mau lima a me nā wāwae). 'O kēia ka hopena disproportionately'ūhā mua a me ka hip-nui. Spondiloepifizarnaya dysplasia aʻole e pili mai ka wawae a me ka lima, pela ka mea, i ka maʻamau nui. I kekahi manawa, he mea he deformation o ka holo ana.

symptoms dysplasia

Ka maʻi hiki ke 'akomi i ma ke kēia symptoms:

  • Ai i pau ka moni e ulu ana, a lilo pōkole.
  • Ua hoʻemi ka hoʻoneʻe o ka spine.
  • Ua lŘlŘ lolo hoʻopilikia (spinal).
  • Mīkini'opihia o nā aʻalolo aa.
  • ? Ac? Aaioea kyphosis.
  • Ribcage barela hoʻokino.
  • Mauae i loko o ka lani.
  • Myopia loa palapala.

Mau pathologies e ho'ōla hoʻonāukiuki aku i kekahi mau hoʻololi. Mau nā:

  • curvature o ka spine.
  • Lordosis loa palapala.
  • Ke deformation o na ami iho varus a valgus palapala.

Myopia hiki no hoi i hoʻomaka ai me ka predisposition kiʻekiʻe i degenerative loli ma ka retina palapala.

Kumu dysplasia spondiloepifizarnoy

I ka papa kuhikuhiE ololi ua manaoia e ia i aaiaoe predisposition no i spondiloepifizarnaya dysplasia lala i Konakele. Nā kumu i e okoa. Mau nā:

  • Aaiaoe.
  • Hereditary.
  • Haoʻa i ke hoʻoukaʻia ma luna o ke kino.

Inā spondiloepifizarnaya dysplasia o ka luna, a malaloʻaoʻaoʻikeʻia ma ka i kakahiaka nui elemakule, ka mea, ua ukuia ke kūpono o ka makana o ka haawe ana ma luna o ke kino iwi. Ināʻo ia ua hiki ke malama i ka loiloi mua kahua o ka hoʻonaʻauao, ka mea i hiki wale mai maikai o ke kāpaeʻana ia.

ʻike, i loa e kau ma luna o ke kumu o ka hookahi kiʻi me Hoʻololi 'vertebrae, no ka mea, ke olelo e pili ana i ke alo o nā maʻi' ē aʻe o ka spine. Ka hoʻoholo 'ua i ka nānā' ana ma luna o ka helu o nā kiʻi i i ua hana no ka manawa lōʻihi ma kekahi mau makahiki. hiki loa ke wale ala kauka ike i ke kiʻi o ka maʻi.

ʻike, o ka dysplasia

Ka mua i loaʻa spondiloepifizarnaya dysplasia o ka luna, a malalo lala, ke kiekie o ka pahiki o ke hoolaia.

ʻike, ua lawe mai i loko o kekahi mau aoao kauka.

Mau nā:

  • hoʻomanawanui ninaninau kauka (neonatolog, he orthopedic surgeon).
  • Radiography o na ami o ka lima a me ka wawae.
  • US (ultrasound nana).
  • MRI (ʻume mākenēki resonance kiʻi).

Mau ka loaʻaʻana kāu kiʻina hana i manaoia e ia i ka loa informative. Ka mea, kōkua hoʻomalu ike i maʻi loa, a loaʻa hewa ma kaʻike,.

Inā spondiloepifizarnaya dysplasia 'akomi i ka wā kamaliʻi, ke keiki Ua kokoke 90% -e hiki wale mai o ke ola.

lapaau ana i ka maʻi

Spondiloepifizarnaya dysplasia lala ia ma kekahi aoao. Ka mea, hilinaʻi ma ka kahua o ka maʻi a me ka makahiki.

Ma nā pēpē i a me na kamalii uuku lapaʻau ua lawe mai ka hoʻohana kūikawā orthopedic nā mīkini home. Ka mea, hoʻohui a koho na ami a me ligaments koho. Ua apono 'no ka fixation, a ua ālai' deformation.

I kekahi manawa e hana i ka iapaau ana i loko o ia kaʻaoʻao 'aʻole i lawe mai i ka makemake hopena, a laila, i ke keiki ma lalo o kekahi mau anesthesia emi i ka dislocation, a i puna bandages no ka paʻa ana hoʻi.

Inā ka hoʻomanawanui mea he luna 'ano, he mea pono e lawe maiʻoki kino. No hoi, ka mea, ua hoʻohana 'ia ka wā o ka 2-3-makahiki keiki. Ma hope oʻoki kino, a me ka mehana hoike ana o ka maʻi pono e mau physical Inc (physiotherapy) a komo kūikawā kāohi 'ia ai a me corsets.

Ka loa ka hoʻokō hana ua lawe mai i loko o ka luna '. Kauka paipai aku me ka Inc hui me kūikawā massages.

Nui: kanaka ma ka iwakālua o ka makahiki a me kaʻike, o "spondiloepifizarnaya dysplasia" i pololei ole mau kanaka i ka ukana kino a me ka iwi mīkini.

Life expectancy a me ka hou kēla

I ka wā o nāʻaoʻao spondiloepifizarnaya luna, a malalo dysplasia i akomi a ua malamaia lakou nei, ma ka manawa, ke kēla no ka wā e hiki mai ke ola e maikaʻi. Inā ka maʻi ua wehe ae ia i ke aumoe, a laila, ma laila e hoʻomaka ai kekahi manawa 'oe a maʻi (relapse).

Ma nā keiki no nā mākua (8-18 makahiki) e hoʻomaka li nui i loko o cartilage o ka ami, a me keia, ma ka huli, me ka nui loa complicate i ka lapaau, a me ka mea uuku loa ka manawa o ka noho pakele o ka maʻi, e e.

Inā ka iapaau ana ua haawi mai ai, a me nā hualoaʻa kanaka pakele o ka maʻi, ka mea hiki ke alakai i ka loa maʻamau ola. Inā i ka maʻi, e hoola i ke keiki, ia e hoʻomau i ka ulu a me ka hoʻomohala me ka pilikia makapō a me na abnormalities a me deviations.

kāohi ana

Spondiloepifizarnaya lala dysplasia He pinepine ka congenital maʻi, i ka ulu o ka i mea aneane hiki ole ke kilokilo. Nolaila, he mea hiki ole i pili i nā ana o ka Kāohiʻana.

I mea e pale aku i ka hanana o ka maʻi i loko o ke keiki a me ka keiki, ia mea pono e kali i ka ukana ma luna o kona iwi a me ke kino. No keia mea mea mea pono ke kanaka hoʻoponopono kona wahi, a 'aʻole i ka noho ana ma mua.

E emi i ka manawa o ka maʻi a me ka hooulu ana o kanaka, ka poe i predisposed i kona helehelena, ia mea,ʻaʻole e pono ke koho i kekahi 'oihana, i a ia e pono no ka lōʻihi manawa e noho ana ma kekahi kūlana.

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