Cystic fibrosis mea he keiki: na hoailona, symptoms, lapaʻau

Kekahi o ka loa he ākea maʻi i i ili ka cystic fibrosis. Ke keiki hua mai ma pathogenic huna e hiki aku ai i ka hoʻohuikau 'ana i ka digestive'āpana, naehana nenoaiu. Characteristically, i ka maʻi o ka maʻi a me ka pinepine hoike mai ai ia ia iho, ina nā makua i ka kekahi hemahema'ōewe. Inā he paena me ka mutation i loko o kekahi o na makua wale, na keiki e ole ke loaa i ka maʻi. IeAUPIIe, IAa IO, cystic fibrosis ua diagnosed i ka makahiki mua o ke ola (a hiki i loko o ka opu).

I ka moolelo o ka maʻi

Cystic fibrosis i na keiki e hoʻomōhala ana i ku pono i ka hoʻohuikau 'o ka' ole o ka chromosome 7 (o kona poohiwi). Ma keia hihia, ke mucus i loko o ke kino i oi ÷. Ua ua ike i ka uhi o ka malu o kēia 'ano ma ka aneane pau loa na nā loko. Manawa a hiki i keia ili ua huakaʻi o ia, a e hookaawaleiaʻe oukou, keu mucus lākou ma ka hoʻomaʻemaʻe ia. Akā, inā e hiki i, nakolo, ka h ÷ secretion stagnates accumulates. Ma ia he 'ia, a me ka pathogenic microorganisms hoolaha, e alakai ana i mau maʻiʻaʻai. A laila loli nā loko o ka digestive'ōnaehana, ka meaola poino mai muli o ka oxygen. No ka mea manawa mua ua i ho'ākāka 'ia ma ke keiki cystic fibrosis i ka 1938 ma D. Anderson. A hiki ia manawa, he nui ka helu o nā keiki make mai pneumonia a me nā maʻi i i ke kumu ma ka cystic fibrosis. More 'ike e pili ana i ke ahulau i waho ma ka hopena o iwakalua kenekulia. Ua aneane na iwakalua noho o ko mākou Honua - i ka lawe ana o ka cystic fibrosis'ōewe mutating. Kēia kina ua i pili i kaʻinoʻano o na makua i ka hapai ana, me ka lawe ai '. Pū ma luna o kona alo, aole ia e pili i ka noho lakou malaila? Aneeo kulana. Ka mea, e ae mai i ka ia nā kaikamahine a me nā keiki.

ano o cystic fibrosis

Ka maʻi hiki i ekolu walaʻauʻana kinona.

• Ka mua hoʻokahi - akemāmā. Ua lŘlŘ ma ka hola 15-20% o ka helu ana o na hihia a pau. Wehewehe aku ma ka mea i ka bronchi e puka liiiU me ka manoanoa mucus. Ma hope o kekahi manawa, e hiki i ka pau puka liiiU mea. Ka ike ole ia e lilo ana i ka maikaʻi? Aneii lepo no ka koʻohune a me germs. Over manawa, ke akemāmā'aʻaʻa sila, e ikaika. Cysts ikeia. E möakäka hou hana mea pulmonary wale deteriorates. A kanaka ke make mai suffocation.
• Cystic fibrosis, he keiki ke i, a me ka intestinal palapala. Ma keia o Nyos i ka digestive'ōnaehana, ke ai ua poorly hōʻuluʻulu manaʻo. Oia ano kumu o ka hooulu ana o ka mimikō, peptic ulcer, ake cirrhosis, a no laila, ma luna o. N. Ua ua loaʻa i loko o 5% o ka hihia.
• Ka loa, he pono ole palapala - hui. Ua Ua diagnosed i loko o 75% o nā mea maʻi i kēia aaiaoe maʻi.
• Loa pohihihi keia (ma kahi o 1%) i, a me ka atypical palapala.

Cystic fibrosis o na maʻiʻaʻai i loko o na keiki

Kēia palapala no ka maʻi ua pinepine haawiia e like me ka ÷ naehana hanu. IeAUPIIe, IAa IO, ua hoikeia na symptoms i loko o ke keiki koke. Cystic fibrosis o na maʻiʻaʻai i loko o nā keiki he symptoms ia cough, mau nawaliwali, haikea ili. Over manawa, Hoʻonui i ke cough, ka mea, ua pu ma ke kala ana o ka mucus manoanoa. Pana kinoea hoolilo keʻano o ka hanaʻana. Hiki ai hanaʻia naʻe i ka manaʻo kōkua o ka manamanalima. Pinepine keiki me ka cystic fibrosis, a me ka pilikia mai pneumonia, a ia lŘlŘ ma ke 'ano nui. naehana'aʻaʻa loli purulent li nui. Pneumonia i maʻi. Paha ka ka hoʻonuiʻana o connective'aʻaʻa i loko o ka ia maʻiʻaʻai. Over manawa, eia na hihia i ke ano o ka "pulmonary naau".

Pulmonary cystic fibrosis symptoms i loko o nā keiki a me nā mākua mea ano like: zemlyanistogo ili kala like 'ole, ka pahu loaʻa bochkopodobnuyu' ano ino fingertips. Nō hoʻi, ma laila ka pokole o ka hanu, a hiki ma ka maha. Aie i ka ka ho'ēmiʻana o ka ikaika loa ka makemake a me ka hoemi ke kaupaonaʻana o ka hoʻomanawanui. Eia naʻe, symptoms ke hōʻike nui hope. Kēia mea - he oi maikaʻi ano no ka hoʻomanawanui.

Ke kahua me cystic fibrosis akemāmā pele

Aia i kekahi mau kuʻina o ka maʻi papa.

1. Ke kahua mua ua wehewehe aku ma keʻano o ka cough, IeAUPIIe, IAa IO maloʻo, a me ka sputum. a me ka pokole o ka hanu kānāwai i loko o kekahi mau hihia. A kūikawā hiʻona o keia kahua i ia mea, ke mau a hiki i ka makahiki kakaikahi (i ka 10).
2. Ka lua o ke kahua - o ka muli o bronchitis i loko o ka maʻi palapala, i ka loli ma ka phalanges. Ikeia e auaaeaiea me ka puʻu. Kēiaʻano o ka maʻi kekahi mau loa o ka lōʻihi manawa - i ka 15 makahiki.
3. Ma ke kolu o ke kahua complications hoʻomōhala. Punk akemāmā'aʻaʻa, cysts hōʻike. E kū'ē i kēia kāʻei kua, ia mea hoomanawanui a me ka naau. Ka lōʻihi o ka wā o ka maʻi - 3-5 makahiki.
4. I ka ha o ke kahua (he mau mahina) ua wehewehe aku ma ka pio like kaumaha o ka naehana nenoaiu, naau. Ka hoʻokūkū Ua IeAUPIIe, IAa IO ona.

Symptoms o intestinal cystic fibrosis

Kēia palapala no ka maʻi wehewehe aku ma ka hoʻokō 'ole' ana i ka digestive nenoaiu. Intestinal cystic fibrosis i loko o ke keiki nui maopopo hoike mai ai ia ia iho i loko o ka wā o ke keiki i ukuhiʻia. Ma keia hihia, he mea omo ilihune o nā bipi kūpaluʻia, nā polokina (e hōʻuluʻulu manaʻo iki maikaʻi carbohydrates). Aie i ke kūpono 'ana o ka keʻano o ka hanaʻana o ka palaho i ka gut i hanaiaʻawahia i huiʻia, e pehu ae o ka'ōpū. A nui ka helu ana o na naau oʻu ka neʻe 'ana maoli. Inā diagnosed me "cystic fibrosis" (enteric palapala) i na keiki i kekahi 'ike rectal prolapse. Pinepine hoʻomanawanui iki mai ohumu o maloo waha. Utrudnyaetsya loaa maloo ka ai. Me ka hou Holomua o ka maʻi ua hoemi kino ke kaumaha.

I ka maʻi ua i wehewehe aku polyhypovitaminosis mai ka digestion pilikia kino i nele i nā wikaminaʻaneʻane a pau nā pūʻulu. E like me ka rula, na nāʻiʻo lilo aku i ko lakou leo, ili i emi laholio. One hou ano na hoailona o cystic fibrosis i loko o nā keiki (intestinal type) - i ka eha o ka okoa ano i loko o ka abdomen. Over manawa, ia e ia, a me ka peptic ulcer maʻi, a me ka mimikō (latent ano). I ka maʻi e loli ai nā puʻupaʻa, akepaʻa. Inā luku aku la ma ke akepaa, o ka noho iʻeleʻele. Toxins loaa i loko o ke kino, a hiki aku i ke koko a hiki i ka lolo. Ka mea, i ka hopena maikaʻi ia ma luna o nā aʻalolo keena, hoʻomōhala encephalopathy. Nō hoʻi ka poʻea pau i ka holo mahuahua ma spleen intestinal cystic fibrosis i loko o nā keiki. For the pathologically hoololi na naau oʻu (ma ka laau kea maluna ona pauku) ua hoike mai ia ma lalo nei.

Hui ano o ka maʻi

Kēiaʻano o ka maʻi ua wehewehe aku ma na hoailona o nā inhalational a me ka intestinal. Nō kāu, nā pēpē i malama oi pinepine, a hoʻolōʻihiʻia pneumonia, bronchitis. Ma aneane pau hihia, a me ka cough mea i loaʻa. Eia hou, i hui cystic fibrosis i keiki ua pu ma ka bloating, noho mea IeAUPIIe, IAa IO he wai, kona waihoʻoluʻu huli uliuli. Aia He He mea hoʻopili o ka oolea o ka maʻi, mai ka manawa i ka wa a na symptoms ikea mua. Nui, ina e 'akomi i ka hoailona mua ma ka kakahiaka nui elemakule, ka prognosis Ua noho lakou malaila.

meconium ileus

Cystic fibrosis hoʻonāukiukiʻana mai o ka mahuahua ma ka (viscosity) o ka meaola mea huna, a me meconium - palapala noho i loko o nā keiki. Kēia hualoaʻa ma ka blockage a me ka naʻau liʻiliʻi. Kēia palapala no ka maʻi ia lŘlŘ i hanau i ka wa meconium 'Aʻole i hele aku. Ke keiki i restless, pinepine regurgitates (e like me ka bile impurities). Eia he mea bloating, ili i haikea. E möakäka hou mai pele kōkua i ka hōʻoia 'ana i ke keiki me ka nui loa ho'ēmi i kā Hawaii hope (ināʻaʻole mea mahana). Ke kumu no keia kulana o ka wa e kaawale aku o trypsin. Meconium ileus Ua pilikia loa a me ka ponoʻoki lāʻau lapaʻau 'uao.

ʻike, no ka maʻi

ʻike, o cystic fibrosis i loko o nā keiki nā loiloi no hereditary a me ka congenital abnormalities. Nō hoʻi, ke koko hōʻike, mimi a me ka sputum hookuuia. Kaula a me ka coprogram. Ua apono 'oe e hoʻoholo i ke alo o inclusions o ke kaikea i loko o nā feces o ke keiki. Ka noiʻi 'ana a me ka ÷ naehana hanu'ōnaehana (radiography, bronchography, bronchoscopy). Pono a me ka spirometry, e like me ka mea e leie aku e loiloi i ka iaea ooieoeiiaeuiiai moku'āina o na ia maʻiʻaʻai. Inā e manaʻo ai he cystic fibrosis (symptoms i loko o na keiki i ole hoike aʻe) hoʻomaka aaiaoe noiʻi. Ka mea, kōkua hookupaa aku i ke alo o ka'ōewe mutation i mea kuleana no ka secretory hana o ka meaola. Neonatal neonatal loiloi ua hana (trypsin lehulehu ua hoʻokolokolo i loko o ka maloo ke koko ke kina ole). He informative lakou e maona ai a me ka hou hoao. Inā ka ipuhao hoikeia mai paʻakai Ion, chlorine i loko o ka mahuahua na dala, he mea hiki i ka olelo o ke ola ana o ka maʻi me ka pahiki kiʻekiʻe. Inā he wahine, ma a ka 'ohana, he mau kanaka me kaʻike, o "cystic fibrosis", kakali i ke keiki, i nā kauka waiho aku e nana i ka amniotic loli ma ka makahiki o ma kahi o 18-20 pule.

lapaʻau o cystic fibrosis

Ua mea waiwai 'ana i kumumanaʻo mea e kiʻi pohaku uinihepa, o ka maʻi he mea hiki ole. Eia naʻe, Inc hiki me ka nui loa hoʻoikaika i ka pono o ke ola a me kona lōʻihi like 'ole. Mua, he nui loa nā mea maʻi me ka likeʻike, o ka make ma mua o ka makahiki o 20 makahiki. Ano, eia nae, me ka pono a me ka 'eleu hana ke ola me ka nui loa aku. Intestinal palapala pono he kupaianahaʻai. Food E e waiwai ma ka kumuʻiʻo (iʻa, hua). Eia kekahi i hoonoho ia a me ka luna 'nā wikamina. I koi? Eaia nā'ūhū ( "Creon", "pantsitrat", "Festal" listen'ōlelo.). Ua mea waiwai 'ana i kumumanaʻo ana e e ia ma kona ola mau ai'. Ka mea i ka lapaau i hāʻawi mai i ka hopena, e hōʻike normalization o ka noho, ke kaupaonaʻana poho a me ka nele ana o ke ahiahi ka ulu ana kona. Abdominal eha nalo, a ma na feces ka mea,ʻaʻole ia akulla hoʻi o momona.

I ka pulmonary lāʻau ano o ka maʻi e pono ia e kōkua liquefaction o sputum a me ka bronchial hoihoi functionality ( "Mukosolvin", "Mukaltin"). He nui loa i loko o ka iapaau ana o pulmonary cystic fibrosis, e pale aku i ke kūpono 'ana o ke infectious keʻano o ka hanaʻana i loko o ka ia maʻiʻaʻai. Maikai keia, a me ka kuikawā hanu kino. It E e hana mau. No ka mea iapaau hiki ke lawelawe a me antibiotics. Poina e pili ana i ka maʻi no ka nui manawa e kōkua ana iā ia i ka'ano'ē iaoia, e like me ka transplantation o ia maʻiʻaʻai. Naʻe, ka mea, i kona drawbacks: i ka pilikia o ka rejection, i ka hooko ana o ka ai 'i inhibit i ka'ōnaehana paleʻea nenoaiu. Eia hou, i ke ahonui e ia i loko o reasonably maikai physical kulana. Ka hapa nui o kēia mau transplants hana wale aku no.

Koi i no nā mea maʻi me ka cystic fibrosis

Kauka ikaika paipai aku i nā mea maʻi i kēiaʻike, e e 'āwīwī vaccinations ku e whooping cough, a me ka like maʻi. He nui e hoʻopauʻia allergens: Ka Hānai Ā Huhu dander, uluna a me blankets mai ka manu hulu. Ua Ua hoi pololei pāpā i ka OE e uwahi ana. Oia kaʻike, pono i ka Kuhio hana maikaʻiʻole o nā keiki. Inā ke degere o ka oolea o ka maʻi mea i noho pilikia, i ke keiki e hele ana i ke kula, haʻuki na newa, i he 'ano kaila Aloha Hawaii. Lapaʻau o cystic fibrosis i loko o na keiki elemakule ma lalo o hoʻokahi makahiki komo ai i ka hoʻohana 'ana i nā mea huihuina kūikawā (Dietta keu, Dietta hoʻohui). Eia hou, i ka pono, e mahuahua, a me ka hookahi mahele lāʻau o 1.5 manawa. Eia kekahi hoʻolauna i loko o ka pēpē kaʻai mea he uuku ka nui o ka paakai (keia mea nui i loko o ke kau wela).

Special noonoo E e ahonui kuhikuhi kahua paʻa. Ka mea, e ia waiwai ma ka momona (holika, ka bata, ai) me ke omo o ka māhuaola wāwahi. Inu no hoi e pono nui. He waiwai e hoomanao i ka lalau'ūhū hoomakaukau koi kela la i keia. Ma waho aʻeo ia ke kumu o lapaʻau hiki ke hoʻohana ', a me ka loina Inc. Kōkua ai i nā lau nahele expectoration e like me marshmallow, makuahine-a-stepmother. Maikai ia i ka digestive'ōnaehana i ka dandelion, Elecampane. A me ka nui mea kāhinu, ua hoʻohana 'ia no ka inhalations (lavender, basil, husopa). I pono keia mau mea a me ka hooikaika ana me nā huahana e like me ka meli.

Time]

Eia naʻe, i ke ola expectancy no ka haawiia maiʻike, mea,ʻaʻole loa kiʻekiʻe. Ma awelika, e hoomanawanui i ola no ma kahi o 30 makahiki (i loko o Rusia), a i ka 40 a oi (wale aku). Eia naʻe, 'eleuʻike, a me ka pono lapaau me ka nui loa hoʻoikaika' ana i ka hoʻomanawanui ka kulana. Ka loa lakou malaila prognosis - i loko o ke kakahiaka hoikeana o cystic fibrosis (i loko o na kamalii uuku). Akā, ka mea, ua ike, a me ka hihia ma ka hoomanawanui me ka like maʻi noho no ka oi mamua o 70 makahiki. Keia koena unuhi i loko o ke ola expectancy ma Rusia a me na aina e aie i ke kālā kēia lākiō. Huakaʻi i ke kai e hoomanawanui i loaa ke ola-lōʻihi kākoʻo mai o ka moku'āina. Manawa a hiki i kēia mea, e alakai i ka maʻamau ke ola, e aʻo, e ho okumu i ka 'ohana, a i na keiki. Akā, Rusia hiki ole ponoʻole i nā mea maʻi me ka mea e pono ai na laau (a me keia'ūhū hoomakaukau, a me ka hana antibiotics, a me mucolytics). Wale he kaupalena helu o nā keiki loaa manuahi mālama 'a me ka pono ka lapaʻauʻia. Nā mea maʻi e noho ana i loko o ka kūikawā mooolelo o kona ola a pau. E hookaawale ia i ka hanana o ia i ka maʻi e nīnau i ka geneticist ma kekahi kahua o ka hāpai keiki hoʻolālā.

Manaʻoʻike kōkua paha no ka makua

A hailona no ka lehulehu ākea ke hoʻololi e kākoʻo makua nona ka keiki poino mai cystic fibrosis. Mua o nā mea a pau, mai panic. E Pono e kiʻi like ka nui o ka 'ike e pili ana i ka maʻi ma ka mea e pono ke kōkua i ke keiki, e lanakila kona hopena. He nui e mau maopopo ia ia o kona aloha.

Ka maʻi me ka nui loa e loli ai,ʻaʻole wale nō ke kinoʻano, akā, no hoi i kekahi mau loa ma luna o ka mea naʻau. No laila, i ka hihia hiki ole ke käpae '(, ka mea nae i hiki mai, a ma o ka upbringing o ola keiki). Kekahi manipulation hiki ke hilinaʻi, e lawe mai, a me ka muli loa hoʻomanawanui. Poe akamai i aku nei au ia, oiai na keiki mai ole aʻo wale lākou maʻi, akā, i lawe malama ana o lakou iho, ka maikaʻi aloha.

Na makua i i manaʻo wale nō i loko o ke kaua e kū'ē i cystic fibrosis, e pono e kamaʻilio me kā lākou mauʻohana, ka mea iʻalo me ka like pilikia. Ua hiki ke hana, a kuikawā Internet Usenet. Aia He He hailona o ke dala, ka mea hiki ke huli i nā kōkua manaʻoʻike a me ka waiwai. He nui no ka hoomanao ana ia i kaʻike, - i ka hoʻopaʻi. He nui kaulana kanaka e loaa ana mai ka aaiaoe maʻi, akā, i kēia i ole ia mau mea i loaa i loko o ke ola. Mea hoolea Grégory Lemarchal, puke kātuna Mea Keaka Bob Flanagan (ola mai i ka 43 makahiki) - kēia mau mea like kekahi ano he kumu hoʻohālike o ka pehea e noho a ulu me ia i kaʻike,. Eia hou kekahi, lapaʻau 'aʻole e ku malie: he global noiʻi' ana i mālama ma'ōewe Inc o cystic fibrosis i loko o ka United States. Inā, aka, e Makuakane me kā lākou mau Emotions pilikia, e hiki mau imi kōkua mai i ka psychologist.