Eisenmenger maʻi pale: mea, lalau mai, Symptoms,ʻike, iapaau ana

Ma cardiology i ka nui, a me ka congenital malformations ma ka pau ana o ka manawa, ua ano na umi o ka "palena iki" ana. i ho'ākāka 'ia ma kekahi o ia no ka lōʻihi manawa, a anaʻia ma ante- a me ka neonatal wā, akā, ua nō huli loa no ke kanaka noiʻi. Kekahi o ia mea Eisenmenger maʻi. Ka maʻi pale Ua hōʻike 'ia ma ke kakahiaka nui iwakālua kenekulia ma ka hale hoʻokamakama'Aukekulia pediatrician a me kēia manawa, oia kekahi i kona inoa.

ka wehewehena

Eisenmenger maʻi pale (Eisenmenger) - keia 'aʻe' Natal kūpono 'ana o ka naau Muscle, i ka loaʻa o ke alo aku o ka hewa i loko o ka septum ma waena o nā ventricles, ke aorta otzerkalennoe kulana a me ka ulu i ka nui o ka ventricle akau. Mea pōmaikaʻi, ua kina hiki e ana hoʻohana, a hou ulu keiki, a ulu ma ka like me kā lākou mau na¯.

'ikepili helu

I ka manawa, ma kahi o elima pakeneka o na hihia a pau o cardiac anomalies i loko o nā keiki e kaili Eisenmenger maʻi pale. Congenital naau maʻi hiki ke puunaueia me nā naʻau mai o nā pēpē i a me kahi mau keiki liilii. Kekahi mau kauka i hui untreated kekahi hemodynamic ka haunaele o keia maʻi pale.

Maʻi pale a eiiieaena

Līkaia kaawale eiiieaena a me Eisenmenger maʻi pale. Maʻi pale - he inoa uncorrected aʻe 'o ka holo ana o ke koko, e holo alaʻokoʻa i ke kūpono' ana ma waena o nā cavities o ka naau ventricles. A eiiieaena nā ho'ākāka 'ia kāna hana i loaʻa i loko o ka fetus a keiki.

etiology

Ke kaʻina hana o ka Pehea keia maʻi pale ua hana, a hiki i ka hopena mea ike ole ia, nä känaka 'epekema a me na kumu e nō ho'āʻo ana e imi i ka wehewehe. Naʻe, ka mea e hoʻokele kokoke pono e nana i nā kumumea aie i a Eisenmenger eiiieaena ikeia. Ke kumu hiki ke maheleia i mau waeʻano: na, a aaiaoe, a mawaho paha? Aneie loa.

1. Kamaʻilio e pili ana i ka pono hereditary EYI o keia maʻi hiki ole ia, aka, ina he first- a lua-laina hoahanau, ua ike ka haunaele o ka ho okumu ana i nui nā loko, he mea mau i ka manawa e ke keiki a lakou e alaʻe.
2. Kaʻapu kōheoheo i ka antenatal wā. Ke kamepiula waeʻano kikowaena hapai wahine e noho ana i loko o nui kulanakauhale, e hana ana i loko o hoʻopōʻino hana ole ana me ka Nine Inch a physical contaminants.
3. Lawe lāʻau. Kekahi ai 'pilikia, e lawe i ka hanau keiki ana. No laila, ma mua hapai ana a ma ka pule mua ma hope o ka obstetrician e e kuka me nā mea a pau i ka loaa kālā. E like ina mea O pono he headache papa.
4. Ka hoʻohanaʻana i nā wikamina a me'aiaola kumukanawai o dubious mea e like ai. IeAUPIIe, IAa IO mau waiwai i hewa ole, akā, ma ka pohihihi keia hihia ka mea, hiki i poino i ka? Eaia iʻaʻole i hanaʻia i ka iwi o ke keiki ole o kona kūloko ma nā loko.
5. Ke alo aku o kekahi o na makua-i-loa-manawa maʻi maʻi.

O ka holo ana, i kēia mau kumu mai i ka hōʻike ua hōʻike hewa ma luna o Eisenmenger maʻi pale. Symptoms, konaʻike, a me ka lapaʻau e kūkā mai ma lalo nei.

pathogenesis

A i kekahi kanaka i ka anatomical hiʻona i ike, eʻoiaʻiʻo ma laila e e haunaele i loko o ke koko holo. Aie i ke alo o ka nui ventricular septal kina, e like me no ka mea, o ka mea hewa kulana o ka aorta e hui venous a aortic koko i loko o ka naʻau lua. Ie hana shunt a me ka shunt, mai haʻalele i ka akau. Over manawa, i ka puʻe i loko o ka pulmonary kumu, piʻi pū, i kekahi manawa ka mea, e hiki oi aku ka poʻe i loko o ka aorta. Kēia, ma ka huli,ʻo ia ka reflex spasm o ka liilii, na moku koko i loko o ka pulmonary holo. ? Ac? Aaioea pulmonary hypertension. Inā ka mea mau i ka lōʻihi manawa, alaila, he mea he uku 'ai hanaʻia naʻe o nā pā o capillaries a me ke koko stasis ia lŘlŘ i loko o ka ia maʻiʻaʻai.

Clinicians kaʻana "keʻokeʻo" a me ka "uliuli" Eisenmenger maʻi pale. Ma ka hihia mua, ka shunt mea i loko o kona Classic mana,ʻo ia hoʻi, mai haʻalele i ka akau, a ma ka lua o ka - ma ka mea ku ole.

symptoms

Ma na kamalii uuku a me na keiki opiopio kuikawā hoolaha symptoms mea pilikia. Helu a me ka 'imi naʻauao' ana o nā keiki e, mai ae aku. Inā makahiki i Konakele. E ku pono ana shunting, laila, i ke kanaka pokole o ka hanu, uliuli nasolabial triangle a me nāʻaoʻao, ka luhi, palpitations a arrhythmia palpable eha o ka angina type. Typical o ke kulana e hoʻomanawanui iki mai lawe e emi i ka symptoms - squatting. A e lilo hiki pono o ka hanu.

No ka mea, he pono ole maʻi puʻuwai hiki pinepine lohe hoopii o headaches, nosebleeds, a me ka puʻu i ke koko. Oe ke hoʻololi i ka leo ma muli o ka mīkini'opihia o ke aʻalolo a hāʻule pahū wale o na arteries dilated. Pinepine i kekahi ke malama pathologies e like protrusion o ka pahu 'ano o ka kuapuʻu, a hoʻololi i ka maʻi phalanges o na manamana i drumsticks, e kuhikuhi ana i ka cardiopulmonary e hemahema, a ua kapaia o Eisenmenger ka maʻi pale. Kumu, symptoms,ʻike, ka mea ike i kela cardiologist.

Ka luna 'hiki e huikau ma ka bronchitis, pneumonia, endocarditis mea koʻohune etiology, kahe ana ke koko mai ka ia maʻiʻaʻai, a me kā lākou mau naʻau hoouka. Me ka lapaau, i ke ola i loko o expectancy kanaka e hoomanawanui i mea ole oi ma mua o ke kanakolu makahiki.

lapaʻau '

Eia naʻe, hōʻike ka wā o ka maʻamau ninaninau i ka maʻi mea,ʻaʻole hiki. I mea e hōʻoia i ka presumptiveʻike, noi aku kūikawā ano o ka hana noiʻi.

1. X-na kukuna o ka pahu, a e hōʻike i ka pilikia makapō loli ana o ka naau contours a me ka nui o na moku.
2. Angiography hewa e like kiʻi 'ana i kūpono o vascular? Acaeoey ua hoʻohana' ia pinepine, akā, i loko o keia hihia ia mea i kekahi, a hiki wale huai ae loli loa inā pilikia ka haumāna hoʻomalu.
3. ECG ka hōʻike ana ma ia hihia, ina ka mea, ua paʻa ma lalo o ka Holter kanaka hoʻoponopono. A laila, i ke kauka e ole e elima minuke nana, a no ka piha ka lā i ka 'ike, aʻo ia nō e hiki ke kuhikuhi i loli ma ka hoihoi kōmi.
4. Echocardiography - ultrasound o ka naau o. An maikaʻi hana no kaʻimiʻana mā ma ka cavities o ka naau a me ke koko kāna hana.
5. Cardiac catheterization, ma keia hihia - i ka loa a me ka oluolu ike loea iaoia o ka noiʻi. Ua kōkua e kuhikuhi i nā mea a pau mā, ho oholo i nā 'ano o ka hookahi naau, a kūkulu i ka lapaau.

O ia ka leo e like me ka paakiki e diagnose Eisenmenger maʻi pale. Symptoms (maʻi lapaau multistage a me ka manawa-e hoopau ana) kona nonspecific pathology ua hoʻonalonalo i like me ka hoʻomaopopo like maʻi, a ola,ʻoiai i ka noonoo ana o kekahi mau nā loea.

lapaʻau

I loko nō o ka mau loa confrontation ma waena o surgeons a me nā kāhuna, i loko o ka hihia o keia maʻi, ka mea hooholo i ke ami hoi ana pono i makeʻe kulana lapaʻau ia e hana i loko iho, aole ia e haawi i ka i makemake ai, a me ke ake hiki ole hoʻolako hale lio kala ana. Nolaila, he lākou o nā ana, ua hoʻololi i, e hoʻopau i ka Eisenmenger maʻi pale:

1. Kahe mau (me ka laekahi Ke Kai, keia ua kapaia "phlebotomy"). Simple a me ka pilikia-noa 'ana. Ua Ua hoʻohana 'ia i loko o nā mea maʻi me ka pathology ai i ka mau o ka manawa o ka makahiki. Ma mua a ma hope o ke kaʻina hana pono hoʻoholo ma ka (viscosity) o ke koko a me ka hemoglobinʻilikai.
2. Ho ohana i ke o ana ka oxygen. Hoʻohana 'ia me he adjunct Inc, e hana me ka cyanosis a me ka hypoxia kiʻekiʻe. Eia hou, ka mea, i ka psychosomatic ia ma luna o ka hoʻomanawanui iki mai.
3. Anticoagulants. Ka mea, e mai i ka lawa kiʻekiʻe o ka hoike i hiki ke kiʻi mai o ka frying pā i loko o ke ahi, a me kahi o ke koko thinners, e kiʻi i kona piha nesvorachivaemost.
4. Other lapaʻauʻia:
   - diuretics no ka wehe pulmonary edema;
   - pāʻoihana e hoʻoikaika 'hemodynamics.
5. ʻoki lāʻau lapaʻau 'ana i kūpono:
   - pacemaker e compensate no arrhythmia;
   - piha wehe 'ana o ka ventricular septal kina panina, a he'āno'ē shunt.

Penei nō pehea e hana Eisenmenger maʻi pale E e kamaʻilio me kou kauka 'ole i kekahi mau hoʻomalu. No laila, pehea e haawi hiki ole i kekahi kumu o ka pomaikai e kekahi i kekahi hana.