Ola kinoMaʻi a me nā kūlana

Gilbert ka maʻi pale. Konaʻike, ka hopena

Gilbert ka maʻi pale, ia mea no ka mea maʻi? Gilbert ka maʻi pale - ka loa mehana lapaʻau Lolina ooieoeiiaeuiiai hyperbilirubinemia. Ka maʻi hōʻike UGT1A1'ōewe mutation. No ka mea, o aku la ia ia, i ka'ūhū ua encoded ma kekahi UDP. Gilbert ka maʻi pale ua wehewehe aku ma ka penei:

  1. Ke kiekie pae o ke koko bilurbina
  2. Hapa ole glyukuroniltransferazy
  3. E kaawale aku ai hepatic loli
  4. Ka ho'ēmiʻana o ke kiekie bilirubin aie i ka hana o ka phenobarbital

No ka mea mua manawa Gilbert ka maʻi pale i loaʻa i loko o 1901, Palani kauka Gilbert me Nikolao ka Augustin, a Lereboullet P. Ua hōʻike 'o ka maʻi pale me "he' ohana cholehemia". Ma hope o ia, ia i? Aaei he mau inoa, akā, i papani ai hoi i Gilbert ka maʻi pale. Kēia maʻi pale pinepine ia lŘlŘ i loko o na kanaka elemakule 25-30 makahiki.

Symptoms typical no ka maʻi

Ma kānaka, he mea luhi, pono maluna quadrant colic ana. I ka papa kuhikuhiE hoike ana o ka maʻi pale o ka nui, a me ka pena waihoʻoluʻu. I kekahi manawa e hana i ka yellowness mea ole kekahi ', a me ke kanaka e ao hou e pili ana i ka maʻi wale nō ma hope o ka mea e paa ana ia i ka biochemical meaola. Aia he mau ke ano o ka maʻi. Episodic a me ka maʻi. Inā he kanaka ua kāohi overloading kou kino, i ka jaundice ke kānāwai. Eia hou, ka waiʻona hainā, pololi paha e he "e hoʻomaka" no ka hooulu ana i ka maʻi.

Gilbert ka maʻi paleʻike.

Nohona ma bilubirin i ka maʻi i ia i ka pae ana o 21-51 mmol / l, a pau ia mea hiki, e hoomahuahua i ka kiʻekiʻe o 85-130 micromoles / hano. E kuhikuhi i kēia maʻi, e pono e hele i ka kūikawāʻike. Ua hiki e ana o kekahi mau ano.

  1. Hoao ana me ka pololi. ʻano nui hoʻohana haʻahaʻa-momonaʻai, ma ka liʻiliʻi loa - e hookeai ana au no ka 48 hola. Pela ka lehulehu o ka bilirubin i loko o ka piʻi pū koko.
  2. Hoao ana me ka pentobarbital. I ka hana o keia ka lapaʻauʻia hiki aku i ka stimulation o ka'ūhū ha awina glyukuroniltrasferazu, hiki hoemi i ka nui o ka bilirubin.

lapaau ana i ka maʻi

Kekahi kūikawā lapaʻau, i mau, ole, no ka mea, o ka hiʻona o ka meaola,ʻaʻole i ka maʻi. Just maʻi contraindicated keu haawe ana, ka mea pono ma hope he kupaianahaʻai. Kanakaʻona mau inu no ia i kekahi kanaka e hiki ke hookapu, no kā lākou hana ke alakai i ka ulu ana o ka maʻi. Akā, e pono ke kuai hoomanao ana ma na hihia o Gilbert ka maʻi pale mea,ʻaʻole e pono ke hoole vaccinations. Ma amplification jaundice kauka i hoakaka ia i kekahiʻai, wikamina Inc ua kuhikuhi.

Gilbert ka maʻi pale ole

Ka poe i loaʻa Gilbert ka maʻi pale, i ka hopena o ka ukupanee, e like me pehea ka maʻi, e loli i ke akepaʻa. hiki ole i kekahi mau waiwai e ma nā mea a pau, akā, he maikaʻi, e hana ultrasound o ke akepaa, me pono me ke koko hoao no bilirubin. I ke akepaʻa koe kōna ma luna o ka loaʻaʻana o Gilbert ka maʻi pale, e pono e pili ana i kaʻai, a kali iho e hana. I kekahi manawa, i ka waiwai o ka mea maʻi ke hoike like transient pigment steatosis. Holo nōhie, e malama i loko o nā kānaka i kēia mau loa. Nolaila, na kanaka e loaa ana mai o ka maʻi pale Pono e kanaka hoʻoponopono i ko lakou ola.

He aha e na Time] i ka poe mai?

Kēia maʻi hiki ke manaoia he Lolina o ke kūmau. Mau kanaka i manaoia e e kŘpa a ola, i ka nui no laila, i loko o ka kūikawā lapaʻau ka mea, e ole e pono ai. I loko nō o ka mea i hyperbilirubinemia hiki ke mālama no ke ola, Gilbert ka maʻi pale, aole ia e alakai i ka make. Aia ka he manawa kūpono no psychosomatic kāna hana, a me ka cholelithiasis. e ole ikea i ka hopena o keia maʻi a hiki i 20 makahiki, akā, mau pu ia e kekahi kanaka, me ka hou aku e hiki ke hana nā kūpuna mai ololi. Ka mea nui wale nō mea i keia mai ua i maopopo ka hopena ma luna o kanaka haʻawina.

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