Ola kinoMaʻi a me nā kūlana

Symptoms pili me ka hemolytic-uremic maʻi pale a me kona lapaʻau

No laila, i ka mea e pono ai i ike mua o nā mea a pau no i ka hemolytic-uremic maʻi pale (abbreviated - HUS). Kauka ke kaila kēia maʻiʻano nui me ekolu symptoms: huʻiʻaʻa puʻuwai e hemahema, hemolytic anaemia, thrombocytopenia. It E e hoʻomaopopo i ka hope hiʻona ua ana hoikeia loa maopopo. I ka maʻi ua diagnosed kuhikuhi i kahi mau keiki liilii.

hiki kumu

O ka papa kuhikuhi aʻe i ka pili me ka hemolytic-uremic maʻi pale - he allergic naoh i ka lapaʻauʻia, e like me ka mea hoʻomaʻi maʻiʻaʻai. Ua mea Logical i ka maʻi hoʻomaka e hoʻomōhala ma hope huʻi naehana hanu a me ka opu nā mea palahēhē paha i loko o nā mea maʻi loaa antibiotics. Me ka pili ana i ka pathogenesis o HUS, ma keia mau mea, o ka mea nui e ua pili i ke alo o autoimmune reactions. Ma kekahi mau hihia, ka mea, e hiki e ala i systemic microangiopathy.

symptomatology

He aha hoailona i ana, kena ae la ia e hemolytic uremic maʻi pale? It E e hoʻomaopopo i ka papa o ka maʻi ma kauka conventionally puunaueia i ekolu manawa. Mua, prodromal, hiki mau mai lā kekahi i mau pule. ʻO ka lua, o ka ai-kapaia "ulia au" - mai kekahi i ekolu pule. A laila, hiki mai ka loaa au ( 'ole make) o ka hoʻomanawanui.

Ka mua loa o ka maʻi me ka a pau kohu kaʻapu kōheoheo, a ua hele pu me ia e symptoms e like me ka luaʻi, loa opu eha, diarrhea me ko läkou 'o ke koko. Kekahi nā mea maʻi i loko o kēia kahua ia convulsions, drowsiness, a me keia poho o ka ike paka i. Ma hope o ka prodromal manawa i loko o na mea he nui nā mea maʻi hele mai i ka hiki ke ola. Me ka haemolytic uraemic maʻi pale hou pili hoʻomalu like haemolytic anaemia, thrombocytopenia, a me kaʻaʻa puʻuwai lesions. Kauka e olelo aku i ka lapaʻau kiʻi, e like me ka rula, kapa hoʻohanohano ma ka polymorphism. Ma kekahi nā mea maʻi, symptoms e Kīwala'ō hemolytic ka hoʻoponopono ulia, kekahi - na hoailona o ka huʻi ʻaʻa puʻuwai ole. Common i na hihia a pau noʻonoʻo i ka hoailona o hemolytic anaemia - eia kahi mea akaka ma ka waenakonu o ka HUS.

Hemolytic-uremic maʻi pale i loko o nā keiki i loko o ka lua o ke kahua ua wehewehe aku ma kekahi deathly pallor o ka ili. Ma ke alo o ka jaundice hiki ke 'akomi i hyperbilirubinemia. Direct Coombs 'ho'āʻo mea IeAUPIIe, IAa IO io, kuu iho la hemoglobin, i ka helu ana o erythrocytes hoemiia. Nō hoʻi, nā mea maʻi pinepine ihu e kahe ana ke koko.

lapaʻau '

Kauka pele diagnose HUS, ma muli i ekolu papa kuhikuhiE ana hoʻohālike: ke alo o hemolytic anaemia, thrombocytopenia purpura a me ka uremia. I mau, ka lapaʻau kiʻi mea reminiscent o Moshkovitsa maʻi pale (hakuʻala maʻi, koko clots i nā ipu, a no laila, ma luna o. D.), Me ka mea wale likeʻole i i ka hope ua ana ike ma mua na keiki, a me mikrotrombozov ia lŘlŘʻano nui i loko o ka naʻau a me ka akepaʻa.

Hemolytic uremic maʻi pale: lapaʻau

Suppression autoaggression - i ka ka pahuhopu nui o ka lapaau. E like me ka rula, kauka hoouna mai i na koa mai, e ole intravascular coagulation. Well kōkua heparin a me ka prednisolone. Inā ka lapaʻauʻia,ʻaʻole i kōkua, ka mea, ua hoike mai hemodialysis.

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