Ola kino, Maʻi a me nā kūlana
T-aeea lymphomas: ano, symptoms,ʻike, a me ka lapaau prognosis
T-aeea lymphomas loa pinepine diagnosed i loko o nā mea maʻi i loko o wa elemakule, akā, nā pōkiʻi a me na keiki e hoi prone i ka maʻi. A me na kanaka e ae, mai ka mea oi pinepine ma mua o nā wāhine.
He aha mea he T-aeea lymphomas
Lymphoma - he malignant lesion lymphoid'aʻaʻa a me nā nā loko. Ma ka hihia o T-ke kelepona hele lymphoma, ka maʻi e loli ai i kaʻili a me ka lymph aka wahi ( 'o ia hoʻi ka epidermotropny ano). Ke kumu o hehee wale i ka pae'āina i loko o ka hanana o neoplasms i T-lymphocytes (aeee mea maʻamau hoʻolako kūpono'ōnaehana paleʻea muli o). T-aeea lymphoma (kiʻi poe ma lalo nei) hiki ke hana me ka hopena o ka hoʻomāhuahua o pathological'aʻaʻa ke kelepona hele hehee wale.
Kumu a me ka hoʻopukaʻana kumumea
- nā kūpuna mai
- Immunodeficiencies.
- Hooloihiia waiū i adverse aʻe: UV pāhawewe,ʻano pākīkē Nine Inch konohiki.
- Makahiki kēia lākiō (ʻelemākule e hoʻomanawanui iki mai).
- Ke alo o nā mea hoʻomaʻi i loko o ka meaola (HIV, Epstein-Barr, hepatitis C, B, T-lymphocyte mea hoʻomaʻi), intestinal maʻi.
- Ke alo o mutations i loko o ka'ōnaehana paleʻea'ōnaehana, hui, a me ka'aʻaʻa transplantation, immunosuppressive Inc hookohu.
A pau kēia mau kumumea i ke ano hoomainoino ma (pakahi, hoʻonāukiuki aku i ka ulu ana o ka maʻi), stress, malnutrition, ko mākou hopohopo overloads, ka hoʻokō 'ole e like me ka? Eia o ke koena a me ka hana.
Mea Maluna
- T-aeea lymphoma ili. Similar lymphomas pele hoʻomōhala i ka hopena o kekahi mau mutations o T lymphocytes, e alakai ana i ka kipi multiplication o ka hope, a, nolaila, pili ia i loko o ka papa o na epidermis. Wehewehe aku ma ka hana ano o ka poʻe noʻonoʻoʻole polymorph hanana lymphomas (plaque, hikoko, kakou, blisters). A me ka mea mua e hoomanawanui i ohumu o ka hanana scaly a itchy mau kiko o, e ho'ōla hoano hou ana ia i loko o plaques, a a laila i loko o kaʻeho foci.
- ʻike ākea T-aeea lymphoma. Kēia manaʻo nā mea a pau i ka lymphomas i T-aeea a NK-aeea me Kinohi (koe nae neoplasm oʻiliahi T-aeee a me T-lymphoblastic leukemia). Muli o kona kulana pinepine, mau lymphomas ana me ke koko lesions,ʻili, iwi ka lolo, a na nā loko, a ma ka lymph aka wahi, eiei? Infiltrative hoʻololi malama.
- Angioimmunoblastic T-aeea lymphoma. like hoailona iho la i lymphoid'aʻaʻa (ma histological ninaninau o ka lymph aka wahi) immunoblast a me ka wai koko keena, me ka mahope piha hou 'ana o kona' ole a me ke kahua o ka'āno'ē moku koko Ua hoike aku.
- T-aeea lymphoblastic lymphoma. Novobrazovanie, a ua nānā 'ana ma luna o abnormalities o T keena. T aeee mai i oʻo, kā lākou nucleus i ole ma ka shape, ka mea koke, a uncontrollably haule. Pilikia keia ano o ka lymphomas mea pohihihi keia. Inā e 'ike i ka like kumu palena pauʻike, me ka huʻi leukemia.
- Ole-Hodgkin ka T-aeea lymphoma. Ua ho he nui pūʻulu o ka hikoko mea i haku no oʻo T-lymphocytes, a aole e hai aku i ka Hodgkin ka maʻi (a laila, Hodgkin ka maʻi). No a hiki i keia pae e hooponoponoia ia mea, ma ka histological ninaninau (me ka chlamydia ma e hoomakaukau ai ia akulla kekahi ke kelepona hele hehee wale Berezovsky-Sternberg ma 'ole-Hodgkin ka lymphomas i kekahi).
developmental ke kahua
- I ka make ana o kekahi lymph wahi.
- Ka laha o kaʻeho no nā lymph aka wahi mea i ke aupuni 'ma kekahiʻaoʻao o ka diaphragm.
- Mau lymph hale ma na aoao a elua o ka diaphragm.
- Lymph aka wahi, a na nā loko, imua o metastases i loko o nā puʻupaʻa, iwi ka lolo, akepaʻa a me nā loko o ka gastrointestinal'āpana.
General symptoms
Ke alo a me ka wa e kaawale aku o kekahi lapaʻau hoike ana hilinaʻi nui ma luna o ke 'ano o kaʻeho a me kona wahi. Eia naʻe, loaʻa nō symptoms i mea hoʻomaopop 'ana i loko o nā mea a pau aneane T-aeea lymphoma:
- Sweating i ka po.
- Rapid kaumaha poho mea groundless.
- Granulosarcoid.
- Low-papa hana ma ke kino ana wela.
- Pinepine luhi a me ka apathy.
mycosis fungoides
Mycosis fungoides - kekahi o ka loa pinepine hoikeana i emi iho T-aeea lymphoma. Ua ua loaʻa i loko o he kanahiku pakeneka o nā mea maʻi i kēia maʻi, a he ekolu ano: panina, decapitated a me erythrodermic.
Panina mycosis fungoides hele ma kahua o ka hoʻonaʻauao ekolu o? Acaeoey.
- Erythematous - mai ka lapaʻau symptoms like i ka psoriasis, eczema, a no laila, ma luna o. Hoʻomanawanui iki mai hōʻike i ke alo o na kohu o ka'ololaha a hoʻopoepoe kinona, me kaʻoiʻoi lua penei, o okoa nui like 'ole, me ka a pink-lila waihoʻoluʻu a me ka scaly ili honua. Na oihana mua i pinepine aia ma luna o ka maka, a me ka torso, ke kiʻekiʻe o mahuahua ma ka nui a me ka hele 'ē aʻe'āpana. Oia lesions mai i pane i ka lapaau, aʻaʻole hiki ke mālama 'ia no ka lōʻihi manawa, a koke nalo. A, hiki ke hui kakou me ka ohane, i ua ole pani ma kaʻike mau mea.
- Patchy infiltrative - ia lŘlŘ ma hope o kekahi mau makahiki o ka hoouka kaua. I wahi o ka luna kohu plaques me ke anuanu, ua hoʻokōʻia paha nepravilnymi akā akaka palena, he poni a me kaha onionio ma luna o kaʻili kai. Ma ka paena o ka nalowale plaques, he mau mea o nā mea eleele a me ka ili atrophy. Ka ohane ame, piʻi pū, e lilo ia i unbearable. Aia He He kokololio kaumaha poho a me ka wela, lymphadenopathy i e ike.
- ʻeho - ma-paena paha plaques ma ka ili, aole ua i hoololi i ke ano o ke anuanu ulaula a me ka melemele painlessʻeho palapala spherical paha kānaka flattened kinona, ua like no me ke Fish ua inaina i ka. Ke anawaena o ka ia me ka ho okumu papa koa, mai kekahi a hiki i ka iwakalua o ka millimeters, a me ka helu i e okoa. I ka wā o kaʻeho ua luku, ola ulcers i hanaʻia i loko o kona wahi, i ka hohonu o ka i hiki a hiki i ka fascia a iwi. Loa pinepine e loli ai i ka spleen, lymph aka wahi, maʻiʻaʻai a me akepaʻa. Narostaet intoxication a me ka nawaliwali ka hoomaopopo ana. E hoomanawanui i make o ka naau e loaa, amyloidosis, pneumonia.
Eritrodermicheskoy palapala ua wehewehe aku ma ka muli o ke narostaet ola ka ohane, redness a me ka nani, i ka helehelena o ka confluent erythematous-squamous wahi lilelile, hyperkeratosis o nā kapuwaʻi, a he mau pama, e like me lauoho me keia poho. A ho'ākea a pau lymph aka wahi i loko o ka axillary, inguinal, femoral a me cubital like. Ka wā e loaʻa ka mea, plotnoelastichnye painless palpation lymph nā pākeke i soldered i na nā'aʻaʻa a puni (ili). Lihodradka malama (mai i ka 39 degere), ke kaupaonaʻana poho, po kaheʻana a me ka luhi. Lethal hoʻokūkū Ua hiki i ka wa e pili ana i exacerbating intoxication a me ka naʻau 'ole.
Ma ke alo o ka decapitated palapala i ola ili ka mea, he mau plaques, e ho'ōla e loaa malignant harater. Make ia lŘlŘ i loko o nā mea maʻi i loko o ka makahiki.
Lapaʻau hoikeana o cutaneous lymphomas
T-aeea lymphoma o ka ili pinepine ia lŘlŘ ku ei ka backdrop o ka lōʻihi-nei, a kūpono hana o dermatological ka maʻi. Hoʻonāukiuki kona hanana hiki herpes nā mea hoʻomaʻi, pāhawewe, sunburn, a no laila, ma luna o. Similar lymphomas ana i loko o nā kahua o ka hoʻonaʻauao: iniiaiie (kaʻina ua IIeEeAIEUIeXAIIUE i loko o nā dermis), kiʻekiʻe (wā ili lesions i ka hopena o ka lymphocyte infiltration o ka na nā loko).
I ka papa kuhikuhiE symptoms i:
- Polymorphic ili wikiwiki.
- E ala maneo.
- Ke alo aku o ka liʻiliʻi, i lalo nā kumumea i loko o nodular palapala.
- Helehelena yellowish plaques, a laila e hoano hou ana iʻekeʻeke o ka hyperpigmentation a me ka atrophy (wā plaque palapala).
- Ka lapaʻau kiʻi ua like no me psoriasis (ma ka melkouzelkovoy type).
- Dryness, nani, redness a me ka ihi o ka ili (me erythrodermic 'ano o ka maʻi).
Symptomatology o kaʻike ākea lymphomas
Ke Kalinika maʻi hilinaʻi nui ma luna o ke kahua a me ka 'ano o pathological kaʻina.
Wehewehe aku ma ka mahuahua o lymphoid'aʻaʻa i loko o ka'ā'ī, groin a me ka axillary wahi.
E hoomanawanui i ohumu o excessive sweating, loa ke kaupaonaʻana lilo, nele o ka ikaika loa ka makemake, mau nawaliwali, kuni, a ma ke alo o ka hooakea aku spleen a me ka ake (i mea nō, he pono ole) - ma ka pokole o ka hanu, recurrent cough a me ka manao o ka naau i loko o ka'ōpū.
lapaʻau '
- Nana, ohi o ka hoopii a me ka anamnesis oncologist.
- General koko a me ka mimi Ka Ikepili.
- Koko biochemistry, e like me oʻu ho'āʻo i nā mea'aʻaʻa i ka hepatitis nā mea hoʻomaʻi.
- A biopsy o ka poino lymph wahi (a e leie aku oe e hōʻoia i kaʻike, a T-aeea lymphoma).
- 'Amelika.
- MR.
- HI.
- Onkoskrining kino.
- Immunofenotipirovannoe mahele.
- Hakakino aaiaoe kālailai.
- Cytogenetic Ka Ikepili.
Inc
Iapaau ana o T-aeea lymphoma hilinaʻi nui ma luna o ka palapala a me ke kahua o ke kaʻina.
No ka laʻana, no ka mea erythematous ke kahua mycosis fungoides kūikawā anticancer Inc ua i hoonohoia, a me ka mea ma waho corticosteroids a me interferon ua hoʻohana 'ia.
Ke Anati-ʻeho lapaʻau mea e lawe mai chemotherapy a me ka radiotherapy.
I kulike ai me keʻano o ka maʻi (palaualelo,ʻano pākīkē, a me ka hoomaikaiʻano pākīkē) me ka nānā 'ana i ka lōʻihi a me ka haku mele' ana o ka lapaau, a me ka hoʻopulapula.
Palaualelo lymphoma ua ole waleʻia, akā, wale mau ike ina ke kaʻina progresses, na nā kaʻa mokulele hoʻololi i.
Ma ka iapaau ana oʻano pākīkē ano o ka pu ana i ka chemotherapeutic ai 'a me Rituximab (monoclonal lāʻau lapaʻau kino).
I ka wa e hele mai i ka nuiʻano pākīkē lymphomas, i koi 'ia ai' i e lawelawe i loko o ka iapaau ana o ka huʻi leukemias.
Muli o kona kulana pinepine, chemotherapy hui me anei i aeea transplantation.
Naʻe, i ka loa ka hoʻokō iapaau ana no ka lymphoma mea e hoʻomaka he kanakolu pāhawewe Inc (e like me ia i ho'ākāka 'ia ma Elekta Synergy), a ma hope o ka loaa ana i ka chemotherapeutic konohiki.
Complications loaa ana chemotherapeutic Luna e like me: akemāmā, umauma, a no laila, ma luna o. Ka pāhawewe ke Inc hiki e huikau ma ka hooulu ana o coronary atherosclerosis.
Ma hope oʻana lapaʻau mea he muli o hoʻopulapula.
T-aeea lymphoma: kēla
- I ka 'eleu ka loaʻaʻana o ka maʻi (loiloi mua ke kahua) a paha o ka pono lapaʻauʻelima-makahiki ola i kela mea kanawalu-kumamalima pakeneka, a no pediatric hoʻomanawanui iki mai - i kanaiwa pakeneka.
- E pili ana i angioimmunoblastic lymphoma ei loaa ole ia. Ka awelika ola expectancy i loko o nā mea maʻi me ia i kaʻike, he elua me ka hapalua wale, a - ekolu makahiki. Ke ola ana o ka wale hoʻokahi-hapakolu o nā mea maʻi i ka manawa o elima makahiki.
- Ma ke alo o ka T-lymphoblastic palapala prognosis hilinaʻi nui ma luna o ke alo / kaawale o ka lesion o ka iwi lolo. Inā ka iwi lolo ua i loli, i ka neʻeʻana o IeAUPIIe, IAa IO maikaʻi. I ole ia, i ka hana hou wale iwakalua pakeneka o nā mea maʻi i loko o hiki ke manao ia.
- Prognosis a ola Fish avium hilinaʻi nui ma luna o ka palapala a me ke kahua o ke kaʻina. Ke'ī mai, i ka wa a ke ola hookolokolo palapala - mai a hiki i ka umi makahiki, a me ka noho lakou malaila prognosis i loko o ka hihia o ka piʻiʻana o ke pneumonia, a no laila, ma luna; eritrodermicheskoy palapala sorovozhdaetsya hui likeʻole complications kūpono i ka make ia lŘlŘ i loko o elua - elima makahiki; ana o ka headless ano o ka hune prognosis, make ia lŘlŘ i loko o ka makahiki.
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