Ola kino, Maʻi a me nā kūlana
ʻaʻa puʻuwai angiomyolipoma: He mea pilikia loa i ka ola, kumu, Symptoms a me ka iapaau ana
Pehea ka hakuʻala angiomyolipoma, paha ka mea, ua ola hooweliweli? Keia ano hoʻohuʻu komo i loko o pathological kaʻina interlayer momona, Muscle nā'aʻaʻa, a me kaʻaʻa puʻuwai epithelium. I hou benignʻeho ninoieo o ka momona.
E like me ka rula, angiomyolipoma ua haawi ai i nā puʻupaʻa. Ka maʻi mea e loli i ke kanaka o kekahi mau makahiki, akā, ma mua kanaka ia mea oi, he pono ole. By kamepiula pūʻulu nā kanaka mai ka 40 a hiki i 60 makahiki. It E e kaulana ia hihia pinepine kākau i loko o nā wāhine. Pehea nui o ka mai, a me ka mea eliminates kaʻaʻa puʻuwai angiomyolipoma? Lapaau, a me ka pilikia posed e ka maʻi, e e ho'ākāka 'ia i loko o kēia' atikala. I ka manaʻoi hoʻokoe 'hoʻokumu pū Inc pathology hiki ke loa eliminated.
maʻi? ueo
Angiomyolipoma - he benignʻeho ma ka hakuʻala. I ka maʻi i hoi loaa kekahi inoa - "ʻaʻa puʻuwai hamartoma". Neoplasm ua hoʻolaha like mesenchymal pathologies ka hoohuoi ana pahee nā'aʻaʻa.
Kilakila mau ano o ka maʻi: sporadic ano o iniiaiie a aaiaoe maʻi.
Ma ka hihia mua, i kaʻeho e loli ai i ke kino iho, me ka aaiaoe aʻe, a ma ka lua o ka hihia, ua hoʻokani ke kūlana alakai mai nā kūpuna mai.
Aia Ua hoi he pono kaawale maʻi Bourneville-Pringle, a tuberous sclerosis. I ka mea, wahi a poino i nā puʻupaʻa, akā, i mea nui i nā symptoms.
Inā kaʻeho ua IIeEeAIEUIeXAIIUE ma ka hema a me ka pololei hakuʻala diagnosed unilateral lesion. Inā ka abnormality ua diagnosed i loko o nā puʻupaʻa, ke kumu e olelo aku e pili ana i kaʻeluaʻaoʻao palapala. Unilateral palapala e hoʻomōhala ana i loko o 75% o ka hihia.
Eia hou angiomyolipoma hiki e typical a me ka atypical.
Ma kekahi typical ano o ka pöpö lepo hoÿokahi i loko o ka increasingly he Muscle'aʻaʻa, a me ke kino momona, a me ka 'inikua hoʻomaʻamaʻa mea hou, he pono ole.
Ka wā atypical ano o adipose'aʻaʻa mea ole. He complicates lapaau. No ka mea, momoma'aʻaʻa ua wehe 'ia me ka palena haʻahaʻa hopena. I keia palapala ka pilikia e diagnose. Ma keia hihia, no ka pahiki o delineation wahahee o benign hikoko, a malignant hikoko.
He aha ka mea i luku mai i loko o ka maʻi?
Nō kāu, i ka wa a ka maʻi i loko o ka pathological kaʻina āpau i komo a me cerebral cortex o ka hakuʻala. Nani kōkua ai i nā ke kahua o ka mea hōʻikeʻikeʻuʻuku, a ua paʻa i ka pāʻia mai ola'aʻaʻa.
He aha ka fraught me ia i ka maʻi iʻaʻa puʻuwai angiomyolipoma (hema a me ka pono puʻupaʻa)? Mea weliweli a no ka mea, i kekahi manawa e hoʻomōhala ana i loko o ke kupaianaha ha i. Kēia ka hana i loko o laua i io aʻe, e laʻa me incorrectly wae Inc a me ke alo o nā pathologies i loko o ka hakuʻala.
Neoplasm ke germinate i loko o ka emi vena cava, ka lymph aka wahi i kahi kokoke paha perirenal hoailona. Ma kekahi mau hihia, e hoʻohuli ai i nā a me ke koko moku, a i nahae, a hoʻonāukiuki i nā hanana o ke kahe ana ke koko.
He nui nā kanaka kahaha no ka mea pilikia loa angiomyolipoma? Pinepine diagnosed vascular kinking. A ma laila nōʻoni iho fractures a hiki i, pili na kahe ana ke koko, e hali ana i ka hoʻoweliweli 'ana i ke ola o ka hoʻomanawanui. Koko i loko o ka abdominal lua, a hue ia. Vascular paia, i pihaʻi me Muscle'aʻaʻa i mānoanoa o ia mea, a puni, e like me ka Muscle'aʻaʻa ka loa a me ka hapa 'ia' iho i loko o ka lua. Ka hopena ia o ka perforation, i olelo hooweliweli aku aneurysm a me nā pilikia complications.
Nā kumu o ka maʻi
Ka hooulu ana o ka maʻi hiki ke kena ae la ia e pau loa ia i kekahi mau kumu.
No ka helu o precipitating kumumea i ke noonoo:
- Hāpai keiki. Ke ano o kaʻeho hilinaʻi nui ma hormonal pae. E like me ka makou i ike, na wahine i gestation maoli i ka nui o ka estrogen a me ka progesterone, i hiki ke malama i ka impetus no ka hooulu ana i ka maʻi.
- Ke aaiaoe kēia manawa. Mea i olelo ia ma luna, ua abnormality hiki ana ma ke alo Bourneville maʻi - Pringle. Kēia maʻi He aaiaoe. ʻepekema, Ua loaʻa nā'ōewe i hiki ke loaa mai ia lakou.
- Aʻano o ka maʻi keʻano o ka hanaʻana i loko o nā puʻupaʻa, i a me nā aʻe, e pono hoʻonāukiuki iʻeho. Inc, ma keia hihia komo ai i ka wehe 'ana o nā mea a pau e hele pū ana mai.
- I ka hoike ana mai o nā neoplasms. No ka laʻana, angiofibroma e hoʻomōhala ai. Kēia pathology ka loa, he pono ole. I ho'ākāka 'ia i loko o ka' atikala o ka maʻi hoʻomaka e hoʻomōhala ma lalo o kona aoao.
symptomatology
Pehea hoike mai ai ia ia iho,ʻaʻa puʻuwai angiomyolipoma? Ka oi pilikia loa i ka maʻi? Me ka 'eleu lapaau o ka maʻi hiki ke lawe mai loa eliminated. Akā, me ka maalea maʻi moe i loko o ka mea ana i ke ano hiki ke komo i loko o koʻu manaʻo ke kakahiaka kahua o ka hoʻonaʻauao symptoms. Hoike ana e maopopo iʻeho kaua.
No ka helu ana o symptoms E e noonoo.
- A manao o ka naau ma ka hema a me ka pololei hakuʻala, e like me ka hope. Discomfort kānāwai i loko o ka abdomen, a malalo hoʻi. Pain hiki e huki, aching a kūmūmū. Ka mea, i wehewehe aku e ka mea i oi aku i loko o 'ana e haʻalele a me' ē aʻe ka neʻe 'ana. Kēia mea ma muli o ke kūloko hemorrhages.
- Lele i loko o ke koko,. Ka mea, ke'ākoʻakoʻa no i maopopo kumu a me ka pinepine lawa.
- Ke admixture o ke koko i loko o ka mimi.
Inā kaʻeho i loaʻa nui nui, ka mea hiki ke 'akomi i ka palpation.
Ka hopena o ka maʻi
Ināʻaʻole lawe i lapaʻau mai i loko o ka 'eleu kūpono, ka mea e loaʻa ka hopena i hooweliweli i ka hoʻomanawanui ka ola. Ka mea mua, e uhai i nā ipu, a me ka alo o ke kahe ana ke koko i ana peritonitis. Me ka nui hemorrhage i loko o ka abdomen he mea he hoʻoweliweli 'o ka make.
He aha ka fraught me kaʻaʻa puʻuwai angiomyolipoma? Ina ka mea, ua ola hooweliweli ina e loaa nui nui? Ma keia hihia, no kaʻeho hiki i puʻe i pili nā loko, pale lākou piha hana. No ka laʻana, a me ke pio o ka hakuʻala akau mea'opihia i paiiaʻi na, a hiki akepaʻa. Neoplasm i rupture, a i poses ka hoʻoweliweli 'ana i ke ola.
Kekahi nui complication ka necrosis paha ka make. Ma kēia hihia, na puʻupaʻa hoʻi ua oki ka hana.
Mai poina i ka benignʻeho hiki lālā i loko o ka malignantʻeho.
lapaʻau '
ʻaʻa puʻuwai angiomyolipoma (kumu, symptoms, ohe. a i ho'ākāka 'ia i loko o kēia' atikala) Pono 'eleuʻike. No ka hoʻokō lapaʻau e halihaliia oia iwaho kupono ana manaʻo.
Ka mua pono ka ultrasound keia hookolokolo ana, a e kōkua kuhikuhi i kaʻeho. Ma kekahi mau hihia, e hali ana maiʻume mākenēki resonance kiʻi mea kūpono.
High degere o ka hoʻokōʻana i ka mau koko a me ka mimi ho'āʻo ma. He mea hiki ke hōʻike 'ana i ke kūlana o ka urinary nenoaiu.
Nō hoʻi, i ke ano o ka biopsy ua hoʻohana 'ia. E elucidate i ke ano o ka hakuʻalaʻeho ua laweʻia no ka Ikepili ma kinowaiʻoki kino a puncture. Keia papa hana i ka mea hiki ke diagnose i ke alo o ka maʻi 'aʻai.
I ka hoʻohana 'ana ai'
Aia ka hōʻike o ke kiʻekiʻe laulā o kekahi ai 'ana i nā mea kūpale o ka pae. Ma hope o ka papa, i ka mākau alu makahiki, ma kekahi hihia, e e hoemiia kaʻeho ma ka nui ma ka hapalua.
Inā he mea he loa kokololio ulu o ka angiomyolipoma, laila, io iʻoki lāʻau lapaʻau hana.
Me ka pili ana i ka lapaʻau hoolaʻi aoao, ia manawa aole e haawi i kekahi hopena.
hana ana kāu kiʻina hana
Hana hakuʻala angiomyolipoma hoʻohana, paha ka mea, ua ola hooweliweli ina koiʻoki kino? Ma kekahi mau hihia, ia mea he hoʻoweliweli 'a me ka pono ka manaʻo wehe'.
Ma muli o ka hopena o ka lapaʻau 'ana i ke kaʻina hana hoʻomohalaʻia e ke akamai kanaka Inc manao, a ua koi' ia e lawe i ka mooolelo na nui aʻe i ke kahua ma luna a me ka hooulu ana o kaʻeho, kona nui a me ka wahi.
I kulike ai me kaʻikena mau hae ma ke kahua o ka oncology,ʻeho, ke anawaena o ka i mea oi aku 4 knm, ua eliminated e hoʻokaʻulua 'ana i kūpono. Keia hana ua ka nānā 'ana ma luna o ka papa'āweʻaweʻa kemika ka mālamaʻana o ka hoʻomanawanui ka kulana. Ke hoomanawanui Ua hōʻike paʻa ana ultrasound, a m-Rayʻike, i hookahi no ka makahiki.
ʻeho nui i oi mamua o 4 knm pono'ano'ē lapaau.
Kaawale mai ka nui loa o ka paepae nui, ka PAaIEN no kaʻoki kino nei:
- hoike? aaieou maʻi e holomua Ka maʻi 'aʻai symptoms;
- kokololio ka hoʻonuiʻana o kaʻeho;
- imua o kaʻaʻa puʻuwai 'ole, a lilo ia i maʻi;
- recurring hematuria.
I oncology hana no kaʻoki lāʻau lapaʻau 'uao manaoia hoʻohana o ka hahai' ana i kūpono.
- Resection o kekahi mau 'hapa o ka hakuʻala, a hahau aku la i ka benignʻeho. Oia ka hana i hiki ke malama i ke kino.
- Embolization. Ma keia hana, ke artery ua komo kuikawa i hoʻomākaukauʻia. Artery nourishes AML. Oia ano he hoʻonui overlapping lumen. Kēiaʻano hana lawelawe 'ana me ka hoomakaukau kahua muaʻoki kino. Ma pohihihi keia hoopii, embolization hana me he kuokoa iaoia o ka lapaau.
- Enucleation. Iloko o ka hana, ke surgeon e lawe aku oe i kaʻeho me ka poho i kaʻaʻa puʻuwai nā'aʻaʻa ma ke kaiāulu.
- Cryoablation. He eiiiaaoeiiiue ala e hoʻopau hikoko ma ka hau. Kēia hana o ka lapaʻau ua hoʻohana nui dala o kaʻeho wale no.
- Loa hapa nephrectomy. Me ka nui nui o kaʻeho ka surgeon hoʻoholo e loa wehe i ke kino.
- Laparoscopy. Kēia iaoia komo ai i ka manaʻo o ka helu ana o punctures e ae, e komo i loko o ke keʻena, a manipulators o ke kino.
Outlook
Hana angiomyolipoma pilikia loa? Prognosis a ola holo 'awelika i ka maikaʻi nā mea kū. ʻeho no i ka waeʻano o benign hikoko aia i loko o ka mea hōʻikeʻikeʻuʻuku. Kēia wehewehe i ke ano hope o ka lapaau. Ma ka hapanui o nā mea maʻi, ma hope oʻoki kino he mea he piha ke ola.
ka hopena
Pehea kaʻaʻa puʻuwai angiomyolipoma, ina paha ia o ke ola-hooweliweli, ka mea, ua ho'ākāka 'ia ma kēia' atikala. Pathology pili i ka helu o nā maʻi mea, akā, ua susceptible ke Inc. Ke kumu nui kekahi meaʻike, a me ka lawe ana mai i ka pololei lapaau.
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