Ola kinoMaʻi a me nā kūlana

ʻo Hanoka, ka maʻi: pathogenesis, symptoms, ka loaʻaʻana

Hemorrhagic vasculitis (ʻo Hanoka,-Schonlein purpura maʻi) no i loaa ia lakou, kena ae la diatheses mea eʻoi aʻe mahuahua ma permeability o ka moku pā. He nui na ano o kona hoike ana. Ka inoa "ʻo Hanoka,-Schönlein" e hele wale aku no. Kaʻia "gemorrragichesky vasculitis" ua wale hoʻohana 'ia ma ka wahi lulu lapaau mai 1959.

ʻo Hanoka, ka maʻi: pathogenesis

Ua Ua nānā 'ana i ka allergic li nui o ka poe liilii, moku ke koko a me ka capillaries. E like me ka hopena, ia exuded wai koko a me kaʻulaʻula koko aeee i aia i loko o ka puni'aʻaʻa. Histopathological lesions kiʻi kokoke i ka ia me ka periarteritis nodosa. Akā, ia mau ipu a mea i poino ma ka hemorrhagic vasculitis, he uuku.

ʻo Hanoka, ka maʻi: symptoms

Ua loli aiʻano nui ui kanaka. Alakai symptom - he poʻe noʻonoʻoʻole ma luna o nā wāwae me ka exudative-hemorrhagic külana. Nā nodules paha e okoa nui like 'ole, akā, nui uuku symmetrically hoolilo. Ka poʻe noʻonoʻoʻole Ua pinepine pu e hui eha, ka ohane, malaise, a me he ala i loko o ke ana wela i ka a pau. Inā ka maʻi ka loa paʻakikī, a laila ka mea i haliilii ae a merge i loko o nui hemorrhagic mau kiko. Oe i 'ike kahe ana ke koko mai o ka make ana o ka nui kulekele. 10-15 lā ma hope o ka poʻe noʻonoʻoʻole ana mae, akā,ʻaʻole loa. ka mea, reappears pinepine. No ka mea, o periarticular edema, hoʻololi i loko o na ami. I kekahi manawa,ʻo Hanoka, o ka maʻi ua hou huikau ma hemorrhage i loko o na nā'aʻaʻa, a na nā loko. Inā ka mea, ia lŘlŘ i loko o ka papa o ka opu a me ka naʻau liʻiliʻi, i ka'ōpū ka pahi eha. Brain hemorrhage ua pu ma ka hooulu ana o ka lōlō a me ka paresis. I kekahi manawa, na loli i typical no hemorrhagic vasculitis, ana i wale i loko o ka na nā loko, a me nā ipu koko o ka retina, a he aha ka mea i nā maka, a Central ko mākou hopohopo kahua.

ʻo Hanoka, ka maʻi: shape

Ka mea, he eha: rheumatoid, uila-hoʻokēʻaiʻana, oluolu, a me ka abdominal purpura. Kēlā me kēia no ia i kona ho'ākāka symptoms. Simple purpura, e laʻa me, pu ma hemorrhagic rashes ma luna o kaʻili a me ka mucous membranes. Ikeia ma mau malaise, mehana. Ma rheumatoid purpura nā loli ana i loko o na ami (i hookuu i ke kuli). Ka mea, lilo loa eha, hu nui ae la. KŘpa a pono ole i ka a me ka opiopio kanaka keiki ia lŘlŘ abdominal purpura. I ka mea e ala intestinal a me ka'ōpū kahe ana ke koko. Loa abdominalʻeha e ho'āhewa wale. Ka luaʻi malama admixture o ke koko, e noho pā holoi. A pau kēiaʻike manaʻo pū 'oe me ka ala i loko o ke kino ana wela. I ka Ia manawa malaila, a me ka ano poʻe noʻonoʻoʻole. Emi pinepine ka mea, e pākuʻi mua abdominal maʻi pale ole ana ma hope. Fulminant purpura i ka ia symptoms, akā, ua nui no ka paʻakikī i, mai ka lā mua e 'ai pono i ka make.

ʻo Hanoka, ka maʻi: iaia

He nui ke differentiate ia mai hemophilia a me thrombocytopenic purpura. Kuokoa ana ua nānā 'ana ma luna o ke alo o ka papa, a pono-ike exudative hemorrhagic poʻe noʻonoʻoʻole, hui ana na eha, a me ka maʻi puʻuwai i ka mau. Noonoo pono i ka hopena o ke kālailai e lawe i ka mooolelo o ka helu ana o platelets - ka mea, e maʻamau, pono ole hoʻololi i e nā hoailona o ke koko coagulation, mīkini'opihia o ke koko clot.

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