An autoimmune maʻi mea thrombocytopenic purpura

No ka mea manawa mua i autoimmune thrombocytopenic purpura, i ho'ākāka 'ia ma 1735 Verlgofa ka poe i malama i ka maʻi i loko o umi makahiki' ua kaikamahine la. Currently ma lalo o kēia inoa palapala hui autoimmune thrombocytopenia, kumu autoaggression ma i ke aloha. Ka mea, eʻikeʻia hemorrhagic diathesis me ka noho kaʻawale deficiency o platelets. Līkaia huʻi a me ka maʻi ano o ka maʻi.

kumu o ka

Huʻi thrombocytopenic purpura e ae aku ka hapanui keiki elemakule 2 i 9 makahiki. Thrombocytopenic purpura i keiki ua wehewehe aku ma ka ulia hookahi a me ka kokololio ke ola. ? Ac? O lapaʻau hoikeana pinepine paipai 'ia ka mea hoʻomaʻi maʻiʻaʻai o ke keena naehana'āpana a me digestive'āpana. I ka 10% o ka hihia o ka maʻi pili i ka hooulu ana o ka varicella mea hoʻomaʻi, Epstein-Barr mea hoʻomaʻi, immunization, BCG immunotherapy. Platelet luku aie i ka'ōnaehana paleʻea pane o ka meaola, aole ma mua o ka hana ana o ka mea hoʻomaʻi.

Maʻi ano o ka thrombocytopenia ka loihi o oi ma mua o 6 mahina ua kapaia idiopathic thrombocytopenic purpura. Ke kumu o ka maʻi mea IKE OLE IA. Thrombocytopenic purpura pinepine hoʻomaka ma ka adolescence, puberty. More, he pono ole i ka wahine.

Lapaʻau hoike ana e hōʻike i nā. Wehewehe aku ma ka chronically-recurring paha hooloihiia ko papa o ka maʻi. Pathogenetic kumu o ka maʻi ua heightened a hōʻeleu i platelet luku ma autoantibodies ku e ia lakou.

lapaʻau kiʻi

Ma kaʻili o nā mea maʻi me symptoms o ka microcirculatory kahe ana ke koko 'ano like punctate petechial poʻe noʻonoʻoʻole uuku subcutaneous hematoma, purpura i ku una i ka mucosa. Wehewehe aku ma ka kahe ana ke koko mai o mucous membranes o ka ihu, nui aʻe ana. Loli i ka ili pinepine i aia ma luna o ka mua ili o ke kumu, a me ka luna malaloʻaoʻao. Nō kāu i ke kahua o ka nui hemorrhage ma ka ka pahu kui ioauoa. Kēlā wā i kēia wā, aia i e kahe ana ke koko i loko o ka sclera, a me ka retina, kahe ana ke koko mai ka digestive'āpana. Ma nā wāhine, ma laila nō hemorrhages i loko o nā ovaries. I loa ano o kaʻaʻa puʻuwai maʻi kahe ana ke koko ke kānāwai.

Thrombocytopenic purpura ke alakai i ka pilikia complications e like me cerebral hemorrhage a me subarachnoid hemorrhage. Ano mea maikaʻi cuff ho'āʻo-Konchalovsky mahiai-Leed: ho okumu ana o hemorrhages ma ka ili mau o ka mīkini'opihia. Lymph aka wahi, ake a me ka spleen ole hooakeaia.

lapaʻau '

Ke kumu nui hiʻona o ke keʻena hoʻokolohua mea e emi i ka helu ana o platelets. ke koko clotting manawa ua i hehiʻana. Heparin wai koko i ua māhuahua. Ma na hihia a pau, nānā 'ana i ka mahuahua ana o immunoglobulin G platelets. Ma hope o nui kahe ana ke koko i ho'ākāka 'huʻi hemorrhagic anaemia.

lapaʻau

Inā diagnosed me ka thrombocytopenic purpura, e hoomanawanui i hoʻomaka lapaau me corticosteroids. Ma lapaʻau, e hoomanawanui i malama i ka napoo mahuahua ma ka platelet helu a piha kala ana. I ka nele o ka laulā o corticosteroids a me immunomodulators hoakaka ia delagil. Me ka ineffectiveness o ka makeʻe kulana Inc i loko o 6 mahina Meu hana splenectomy.

Kekahi wahi o ka Inc - hooponopono o kiʻekiʻe nā māhele o ka immunoglobulin no intravenous ka pahu kui no 5 mau lā. Mau hoomakaukau inactivate nā mea'aʻaʻa i nakinaki a wehe mea hoʻomaʻi, mea koʻohune a me nā antigens.

I 80-90% o nā mea maʻi i loko o ka noho'na makaainana i ulu loaa ia lŘlŘ loko 1-4 mahina. Ma kekahi mau hihia, thrombocytopenic purpura hiki mau mai i 12 mahina. Ka maʻi He chronically relapsing: kahe ana ke koko manawa 'ē aʻe me ka manawa o ke kala.