Ola kino, Lapaau
Congenital hypothyroidism
Congenital hypothyroidism mea he maʻi o ka endocrine. I ka maʻi ua wehewehe aku ma ka emi i loko o ka papa hana ma ka thyroid gland. Congenital hypothyroidism ua diagnosed kākaʻikahi (kekahi hihia o ka elima tausani). Ka pilikia o kēia maʻi aie i ka mea i ka nele o hormones negatively e loli ai i ka ulu ana o ke ko mākou hopohopo'ōnaehana a me ka psychomotor oihana o na keiki, iaʻi ia.
Hypothyroidism i loko o ke keiki e hoʻomōhala ana i loko o ka opu. Ka loa, he pono ole maʻi prone kaikamahine ma mua o nā keikikāne.
Hypothyroidism mea he keiki hiki ke wehewehe aku ma ka piha a hapa ka nele o ka thyroid gland. Ua hakumakuma na mana pili i ka nele o kona hormones: thyroxine, triiodothyronine. Penei, ka unborn keiki ua hoailono aku la pathology ka hoohuoi ana negatively ka maʻamau ana a me ka hoohana ia ana o kona kino.
Congenital hypothyroidism ua wehewehe aku e likeʻole ka haunaele ma ka functioning o ka pituitary gland, thyroid gland a me ka hypothalamus. Ka hapanui o na hihia o ka maʻi i ka iniiaiie külana.
I keia la, i ka oaeuiinoe kumu o ka maʻi i manaoia e e aaiaoe kāna hana. Ka hapa nui o na hihia (80%), sporadic maʻi hoʻomaopop 'ana i loko o nā hua'ōlelo, e hookupaa aku i kekahi' ano o ka hereditary EYI 'ole e pili ana me ka hookaawale heluna mea,ʻaʻole hiki.
Congenital hypothyroidism kiʻekiʻe mea nui hou pohihihi keia ano o ka maʻi, aole i ma mua o ka puke Paipala. I ka maʻi ua wehewehe aku ma ka haunaele i loko o ka 'ole "kauoha oaio" - pituitary gland - thyroid gland i hanaʻia i ka mana hoʻomalu.
Congenital hypothyroidism mea he nui pilikia i ke ola a me ka ola o na keiki.
Keia mea kuhikuhi manawa a hiki i ka hopena o ka nele o hormones i loko o ka thyroid gland i loko o ka ulu ana o ka spinal kaula a me ka lolo, loko pepeiao a me nā hale i loko o ka'emi ko kahua. It E e kaulana ia ma ka kekahi kahua o ka nele o ka operability i irreversible a me ka untreatable. Children me congenital hypothyroidism i hope ma ka psychomotor a me ka somatic? Acaeoey. Ka pono kiʻi Ua laila, i kapaʻia ma ka hoʻomaʻamaʻa cretinism. Keia ano ua manaoia e ia i ka oi loa o nā mea a pau ano o ka psychomotor immaturity.
E like me ka mea hōʻike i kekahi mau hoailona o congenital hypothyroidism hiki ke 'akomi i hanau. Kekahi o na symptoms i kūpono 'ana i ke keiki ka.
I ka papa kuhikuhiE symptoms o ka maʻi e e hoʻolaha like:
- haawi kali hou aku; (oi ma mua o eha pule);
- na hoailona o ka immaturity i hanau, hoʻowahāwahā i ka "kia-ʻia" hāpai keiki;
- i ke kaupaona ana o ke keiki, e oi aku 3500 nā huna;
- ka pilikia i loko o ke kaʻina hana o ka hoola ana o ka umbilical eha, hooloihi ae i mau lāʻau kū-Natal jaundice;
- nani o ka maka, a me na nā pale poʻohiwi ma ke kua o ka lima a me na wawae pauku;
- lethargy; apuupuu haʻahaʻa kahea ana, ilihune keiki omo ma ka umauma.
Nō kāu, retardation ma? Acaeoey hoike mai ai ia ia iho i loko o ka mua mau mahina o ke ola. Ma keia hihia, ua lohi nā mea maʻi fontanelle panina a me ka teething, brittle a me ka maloo lauoho.
Lapaau ana i ka maʻi ua nona i hoʻopiha i ka nele o ka thyroid hōmona. Ua hoʻohana levothyroxine paʻakai. Ke kanu'ōiwi o ka lāʻau, a ma kona ano maoli thyroxine i'ālike. It E e hoʻomaopopo i ka nele i ka hana 'ole ka' ole o ka thyroid gland hiki ole ke loa ola. Nolaila, hope Inc ua hoonohoia no ke ola.
IeAUPIIe, IAa IO, lapaau hoʻomaka i loko o ka hebedoma elua o ke ola ke keiki. Ma kekahi'āina (e like Germany) Inc ua waiho mai ka walu-iwa o ka lā ma hope o ka hanau ana.
I ka lā, hua mai la i kekahiʻano o analogues (kalepa ano) o ka levothyroxine. Ke kaumaha ma muli o ka nui o ka hana waiwai ia laʻau heluna. Inā pono, e hele i kekahi Analog 'ole' ē aʻe palapala ia e lawe i ka mooolelo.
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