Ola kino, Maʻi a me nā kūlana
Ichthyosisʻili: mea, lalau mai, symptoms, lapaʻau
Medicine anao? Aou kekahi pūʻulu kaawale o ka maʻi, i ka mea i kauoha aku e loli ma ka superficial, ahu iho o ka ili i ka aaiaoe kiʻekiʻe. Ma muli o ka 'aʻe' ana i ka ili undergoes kekahi loli, a lilo like i ka iʻa unahi. Kēia maʻi ua ili mai iā ia, a hiki ke hoike mai ai ia ia iho i kekahi mau makahiki kanaka, nānā 'ole o ka lāhui, ka wahine a me ka kaiapili kūlana. Ichthyosis hiki ke kaheaia poorly, a ua i hāʻawi ai i ke ahonui i kekahi pilikia, a hiki eʻano pākīkē, a hiki alakai i ka make. ichthyosis a me ka ichthyosiform ili mai i ke kaupaonaʻanaʻAno a, Eia naʻe, i kŘpa a pono ole a me ka pilikia i ka pono. He nui ka poe e alakai 'inikua keʻena hoʻokolohua e hana paakiki e somehow lawelawe alaplpa i ka pathology, a e ola maʻalahi no nā mea maʻi.
He aha ka ichthyosis
'āno'ē ho okumu ana o ka stratum corneum - ichthyosis. Kona kumu i ku pono i ka abnormalities ma ka aaiaoe kivila o kekahi a me nā makua -ʻo ia, i loko o ka X-chromosome. Aia, ua nui na maʻi i hoike mai ai ia lakou iho, a nana e like ichthyosis, akā, ma ka mea ka mea e ole. No ka mea, panic i loko o nä ma like symptoms mea i pono. Na maoli maʻi ke hoike wale i ka hoʻomalu, a me ka hapanui o ia e like i ka ili maʻi i ana ola. ichthyosis a ichthyosiform ili mai i keʻano o ka laha ', akā, no ka lapaʻau i kauoha aku i hookaawale ai ia i loko o kekahi mau pūʻulu. E aʻo hou e pili ana i kela a me keia o ia mau mea - ma lalo nei.
maʻamau ichthyosis
I kapa ichthyosis vulgaris, ka mea, o kekahi o ka loa, he pono ole ano. Ka maʻi hoike mai ai ia ia iho ma ka kakahiaka nui elemakule, akā, e like i kālā, 'aʻole i pepehi keiki ma lalo o 3 mahina o ka makahiki.
Ka loaʻano pākīkē maʻi hoi i ka 'īnea i maturation o ke ahonui, a me ia mea ma kahi o 10 makahiki o ka makahiki. Once na hormones stabilize ke kanaka, e hele mai i loko a me ka hoʻoikaika 'ana i ili ano. Kekahi hoouka hele mai i loko o ke kauwela wa pono, akā, me ka anu Snap maʻi hoʻomaka e holomua. Nā keiki kāne a me nā kaikamāhine me ka like ole e kūkulu i kēia maʻi. ano o ichthyosis ua hoololiia mai ka lawe (kekahi makua) i ke keiki. Ka maʻi poʻe hahai iā hoomanawanui ma ke ola, i ke ana i ka hoʻoikaika 'ana a me ka worsen.
Nā symptoms o ichthyosis vulgaris
Ichthyosis vulgaris loaʻa kona inoa, mai ka mea ia ia i makemake e flaunt. I ka maʻi e loli ai i kaʻili, pāpālina, lae a me nā lehelehe contours oi loa aku hoi. Ua uhi ia ka ili me ka uuku whitish unahi loa ka nohoaliʻi maka. Lākou mau helehelena, a ua hoʻokino e like me ka hua palaoa bran, no ka mea, ua kapaʻia pinepine ia ichthyosis o ka ili "ringworm pityriasis". Loli ana i wahi mea i malama i ka kauluwela a li nui, akā, me ka ili i maloʻo a me ka flaky. Ka maʻi Aʻole i pili i ka lauoho a kui makua ahonui, a i ole i ia pilikia nui.
Recycle - wale palapala wahi o ka wahi, ma manawa, flaking i wahi loa, akā, ua loli nā wahi o ke kino. Pinepine ia mea i ke kuli, a me ka kuʻekuʻe aku, puhaka, a malalo wahi hoʻi, i kekahi manawa na puupuu wawae. 'Aʻole i kēia lakou aloha ia ichthyosis, e like me ka? ueony, groin wahi a me na wahi he nui ili pā. Ma ke ano o ka mai, a me ka nui a me ke kinona o flakes maʻamau ili ichthyosis e māheleʻia i loko o kekahi mau ano: alodio ichthyosis, xeroderma serpentine, kui kele,ʻeleʻele, a lustrous (pearlescent) ichthyosis.
e pili pū ana nīnūnē
Young keiki a me koʻu hoomanawanui ana'ku ia adolescents loaʻoi aku ichthyosis. Nā kumu e like aʻe 'ana o nā nā loko, a kino nenoai.
- Ke keiki lohi e ulu ana a me ka ho onui ana ke kaupaonaʻana, nana angular, deviations ma ka noʻonoʻo kūpono 'ana.
- Hoʻokāʻoi secretion o sebum a me ka hou, e like me ka no - ka lauoho 'ole ua wāwahiʻia, ka mea hiki ke haule iho mai. Nail papa e hoopaa, he wiwi, a me ka brittle.
- Hoʻonāwaliwali i ka'ōnaehana paleʻea'ōnaehana, a no ka mea, pinepine koʻu hoomanawanui ana'ku ia keiki, mai mea hoʻomaʻi a me ka hoʻoʻino maʻi.
- O ka wawahi pūnao a me ka thyroid hōmona pūnao.
- I ke koko naʻokoko aei mai, a hiki laila alakai i ka maʻi o ka naau a me ka vascular nenoaiu.
- Ulu ka "makapo" - He ano kahi kanaka mai ole hoomaopopo ukana i loko o ka pouli.
mau pilikia a pau i maopopo loa i maopopo i loko o ke kau hoʻoilo. He mea pono e uku kūikawā noonoo i ke kino a me ka ola. He pono keia mau mea hou ea a me ka lā.
Ano o ichthyosis i loko o ka recessive ano
Ka maʻi Ua recessive ichthyosis i loko o ka palapala lewa i loko o ka hōʻike ikaika o ka ili kaha onionio ma luna o ke kino holoʻokoʻa, a ua nakinakiʻia ma ka hoohanau: ae aku i kēia palapala wale kane laʻelaʻe 'ia. Girls kākaʻikahi kiʻi maʻi, akā, i nā moku halihali mokulele. E like me ka makuwahine, e hoʻolele i ka maʻi i kāna mau keiki kāne, ma hope i ke hoʻouna i hereditary chromosome i kā lākou mau kaikamāhine. No laila, hiki ke hoʻomau loa.
No kaikamahine recessive ano o ka maʻi hiki e ona. Oia hihia i pohihihi keia, a hiki wale nō hana inā nā kona mau makua i ua iho mailoko o, a laila ka mea, e hāʻawi pathologic X chromosome kaikamahine. Ka maʻi mea, ua hanahana loa, mau kaikamahine kākaʻikahi ola.
Symptoms o recessive palapala
Loa pinepine loli poo, ka lauoho thinning, haule mai, hiki mai piha'ōhule. Flakes nui a me ka mānoanoa o ia mea, e like konaʻena pepa i ka uala eleele malu ai. Nā mea maʻi e loaa ana, mai kāna hana o na nā loko. E hoʻomōhala iwi kāna hana a me ka noʻonoʻo 'retardation, ao corneas, eia na hihia o ka epilepsy.
Congenital ichthyosis i loa
Congenital ichthyosis - ka loa luna 'pathology, i e mehana' ole loa. Ka pakeneka o ke ola mea uuku loa, na keiki i pepehi i loko o kekahi mau hola ma hope o ka hanau ana. Ma pohihihi keia hihia, he keiki hooponopono iho i e hoola. Ka maʻi mutates i loko o kekahi ano, erythroderma, no ka laʻana. I loa pohihihi keia hoopii, i hiki pono ke kapaʻia he hana mana, i ka maʻi loa emi ana o ia me kona mau makahiki, a nui loa uuku au ke kanaka.
Symptoms o ka loa
Congenital ichthyosis i loko o nā keiki hoike mai ai ia ia iho i loko o ka helu ana i kāna hana, a malformations. Mau keiki i hanau prematurely, me ka haʻahaʻa hanau ke kaumaha. Skin bebe nana e hoole, a kohu kapa kila, a haawi mai i ka mawae, a e oozing koko.
I kekahi manawa, i ka wa o ka ulu ana o ke keiki ka ili ua wāwahiʻia, ka mea'ē aʻe nā loko, nā'aʻaʻa a me mucus hoʻomau i ka hoʻomōhala maʻamau. Ka ili mea ole laholio, ka mea paa a me ka huli i ka pili a hiki i ka mea ma waho lole. Maka a me ke kino a pau i ke keiki ka loa ino, a lawe o kahi ku pono helehelena.
Ke kumu no ka mea kiʻekiʻe make ana i loko o nā pēpē i aie i ka mea i ka keratin mea Hoʻonui i ka pono a me ka pulls ole loa clogs nui nā loko. Keiki hiki ole hanu a me kaʻai, na nā loko i mā ma ka? Acaeoey, pili maʻiʻaʻai. Mau keiki i kapaia "Harlequin", a me ka maʻi ahulau - ". Harlequin symptom"
Congenital ichthyosis mehana
Inā congenital ichthyosis e hoʻomōhala ana i mehana (benign) palapala, ke keikikao i loaʻa ka manawa e ola. Keratinized'aʻaʻa ulu ole no ka nui me ka nui palapala. Kūloko nā loko, a hiki ina ka mea i ino, e hiki ke lawe mai kona nui kuleana pili i.
Symptoms o ka mehana
Ichthyosis i na keiki ke loli ka holoʻokoʻaʻili, a wale kekahi pauku. Ma ia mau wahi, ka ili i ulaula, edematous palpated lalo o ka wepa, pakahi aku la ia i loko o nā wahi a pau o ka ili wrinkles. Pathological wahi ma luna o ka maka i ke hoinoino la kona helehelena, kihi loa 'ilikai ke poʻi a me ka ihu a me ka waha wahi. Akā, i ka manawa o ke ola i loko o kēia mau keiki i.
Ichthyosis i loko o "maikaʻi loa" ano
Oia ili ichthyosis mea kekahi manawa pioloke me ka lauoho zoster. Ua hoikeia mai ma ka cii ma ka ili ua lena (kukuli, kuʻekuʻe aku ami). Foci uhi me ka nodules uuku i i kainuʻu pū me ka nui ka lā'ī poni unahi.
Kāohi
Ichthyosis - he ili maʻi i hiki ole ke Hāʻule maila lākou, akā, he mea hiki, e wńnana i ka hanau ana o ke keiki me ka maʻi. Aia i kekahi wahi lihi iki o ka 'ohana hoʻolālā-oaio? A mea i aʻo geneticists. Poe akamai, e lawe i ka mooolelo a pau o ka mea kiko'î a, o ka oi aku ina he opiopio hui a me ko lakou mau hoahanau i Ua hihia o ka ichthyosis. Aaiaoe? E hoohalike i ka maomeka a me ka Loaʻaʻia ka pilikia o ka loa mai i loko o ka fetus, a haawi koi e pili ana i ka wā e hiki mai ana o ke keiki hoʻolālā. Inā ka pilikia e kiʻekiʻe, keia mau i ke ao aku, e haawi aku i ka pēpē i ka hanau ana. Akā, e ia me ka mea i, ka olelo hooholo, e hilinaʻi wale nō ma luna o ka noho male.
Ichthyosis maʻi i loko o loa palapala - he maʻi weliweli loa. Ke keiki a make Ua aneane 100%. Oia hoi, ina e hiki ke ola kāu keiki, a, ia mea olelo lealea kona hae o ka poʻe e ola ana hiki ke kapaia hōʻoluʻolu. ʻAʻole e e hiki ke kūkulu i maʻamau ia i kekahi keiki. He nō e hoʻokuleana i na mea he nui comorbidities, o kela mea keia hele nei, e mea, e loaa ana i ka eha. Mare Leomakana pono hōʻike kuleana a me ka ole i ka malama ole i ke aʻo o ka poe akamai i.
lapaʻau
Oe i diagnosed me "ichthyosis"? Pehea e hana i kēia maʻi? Komo i loko o ka iapaau ana a me ka hooponopono ana o ka papa o ka maʻi, dermatologists, geneticists, kauka a me infectious maʻi. Tragically, ka maʻi pili i ka maʻi o aaiaoe, a he mea hiki ole i ka loa kiʻi pohaku uinihepa, o ka mea. Medicine hiki ke malama i wale i ka pono o ke ola o ka hoʻomanawanui i ka pae kūpono, a ma nā ala keakea mai i ka muli o nā mea palahēhē. Holika a me ka hinu mea e hoopalupalu a disinfect i ka loli ana i wahi, e hoomanawanui i e e pio, e hana ma ko lakou mau ola.
ichthyosis maʻi mea eiiieaena, a psychologically. Oe e pono ai i ka psychologist, aʻano nui kākoʻo o pili hoa. Ke rejection o ke kaiāulu hiki e kaumaha ana i ka ua pilikia ana o ke kanaka. Children Pono e kamaʻilio ai me lākou mau na¯. He nui no ka wehewehe ana i na keiki i keia maʻi mea i lele a me ka mea i pilikia no ia.
He pono e malama i hoʻonele. Mana pono e piha. Sunbathing, akā, eʻoiaʻiʻo, e pale aku sunburn a me ka overheating. Hōʻike 'ia e auau ma ka moana wai, a me ka auau me ka moana paakai. He pono e malama i ke ola i ke Aloha Hawaii, a ma ka iki maʻi, e kōkua mai kauka imi. Ke iki maʻiʻaʻai i loaʻa i loko o ka nāwaliwali, kino, hiki o ka hoʻomaka koke Hawaiʻi i loko o ka hale hānai maʻi me complications.
Traditional ano o ka hana maikaʻiʻole o ka ichthyosis
Healers e aʻo ai i ka nui o ka poe i hana eha iaʻi mai scaly ili. Ka mea, i nā mea a pau okoa, a i mea e somehow alleviate i ka maʻi, a ho'ēmi i discomfort. Eia naʻe, e hoomanao i ka hahai i ke aʻo ana o kanaka, ka poe i questionable pilina i ka lapaau, mālama nui e e hoʻohana. Inā i ke kupunawahine i loko o ke kuai, e e Kā e hoopahee auanei oe i ka lāʻau ' "mai na mai hehe ichthyosis Shleymana", a ma ke ano maoli hakuʻole, ia mea maikaʻi, e malama mai keia "intern" aku. Akā, ma ka lapaau malaila maoli ku koi. Ma mau, mau kī a me nā bato ma ka decoction o ka lau nahele. Aia nā ideas mai ka hale me ka hinu e kālele ana ma luna o hydration, no kou kino a me ka ili disinfection. A pau o ia mea, i mai maoli nā mea hoʻohui, a hoomoa ia ma ka hale, he mama. Paha oe e kekahi mau pono a me ka hemahema hoi ideas koho no lakou iho.
Ma luna o ka huli 'ana no ka laau na kanaka e loaa ana mai aaiaoe maʻi, aaiaoe a me ka keʻena hoʻokolohua hana i loko o na aina. E mākou manaʻolana i ka laau, e e loaʻa koke, a me mākou nō e hiki ke hoomaemae iho i kanaka a pau mai ia i ka maʻi kaʻawaʻawa loa, a hiki pilikia loa.
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