Ola kinoMaʻi a me nā kūlana

Lefgrena maʻi pale: 'ehaʻeha ka, lapaʻau hiʻona, lapaʻau, Kāohi

Systemic maʻi i mau i ka mea pohihihi i ka 'inikua ao nei. Kekahi mea sarcoidosis, a i ole ho'āpono ka etiology, a hōʻike i ke ano o ka li nui o connective'aʻaʻa i loko o kekahi mau nā loko, a nā'aʻaʻa me ke kahua o ka granulomas. Lefgrena maʻi pale - he kūikawā no ka sarcoidosis ka heluna o kaʻili, intrasternal lymph aka wahi a me ami.

kumu o ka

Ke pathogenesis o ka ulu ana o ka autoimmune pane. Ka'ōnaehana paleʻea'ōnaehana crashes, a keʻokeʻo koko keena hoʻomaka e ku i ke olakino akemāmā keena, ami a me ka ili.


Lefgrena maʻi pale pinepine e hoʻomōhala ana i loko o na kaikamahine (20-35 makahiki). Children pele ka mea, e ole e maʻi. Lefgrena maʻi pale hoʻomaka ke hākilo loa, a laila, ke kiʻekiʻe o ka lapaʻau hoikeana e lakou lawe wahi. Pinepine, aia no he ano papa o ka maʻi.

Ma waho mea hoʻomaʻi a me ka mea koʻohune pähola o? Acaeoey o sarcoidosis, he mea no hoi i ka manaoio i ka maʻi e hoʻomōhala ana i loko o kanaka i ka lōʻihi manawa ma ka hui 'ana me yiaeaiiacaaeneiie Nine Inch i loko o nā hale hana. Oe E Mai lilo maka o, a me ka hereditary ololi. I mea no ke aha la polyetiological sarcoidosis mea he autoimmune maʻi.

lapaʻau hoike ana

Lefgrena maʻi pale ma ka sarcoidosis hoike mai ai ia polisimptomno. Lapaʻau hoikeana hoʻomaka ke hākilo loa. Ke kanaka i erythema nodosum ma ke kino, ka mea, i ka welelau o e hohola ai i nāʻaoʻao, hoʻi, opu a me ka'ā'ī. Aka wahi i ka'ololaha kinona, kā lākou anawaena e hiki mai i ka 6 kenimika. It E e kaulana ia ma ka wahi o ka ho okumu ana o erythema, aole ia e ana necrosis.

O ka papa hoike ana ua manaoia e ia i ka pio ana o bronchial a me ka tracheal glands. Ua ho i ka pilikia nui no ka hoʻomanawanui:

  • he cough;
  • kēlā wā i kēia wā, a mahuahua nui kino mehana;
  • deteriorating ola;
  • he mea po kaheʻana;
  • deteriorating mea e like ai o ka hiamoe ana;
  • ke kaupaona lilo ia lŘlŘ;
  • kekahi kanaka ka hoao ana i ka iini.

Hope Lefgrena maʻi pale ua wehewehe aku ma lesions o na ami. Ka mea, e ola edematous a me ka hoʻoneʻe deteriorates. Objectively, kekahi hiki e hoailona oukou i ka nani o ka lymph aka wahi i loko o ka'ā'ī, a me nā armpits.

Pehea e diagnose?

Lefgrena maʻi pale ua hoʻokumu ma luna o ke kumu o ke keʻena hoʻokolohua lapaʻau 'ana a me ka ninaninau ana i ka hoʻomanawanui ka kino. Erythema nodosum Radio nui i ka diagnosing kēiaʻano o ka sarcoidosis. Eia naʻe, pono e ike okoa ke kauka mai tuberculosis maʻi a dermatovenereological maʻi puʻuwai.

Keʻena hoʻokolohua koko e ho'āʻo ai, e hōʻike:

  • mahuahua ma ESR;
  • leukocytosis;
  • i ka helehelena o ka gamma globulin.

Ma ka X-Ray kiʻi hiki ke ike i ke ano hoonee aku lymph aka wahi, e like me fibrous hoʻokomo kālā. Kēia kōkua e eʻoiaʻiʻo i loko o ka hihia o ke akemāmā maʻi.

Weakly hoikeia ma ka palapala koi i ka bronchoscopy me biopsy. I ka hiki ole i ka hoʻopaʻa 'ana o akemāmā'aʻaʻa ke ano histological' ole o ka sarcoidosis: kaʻimiʻana hehee wale epithelioid granulomas.

Prognosis a me complications o ka maʻi

Pākahi kahe Lefgrena maʻi pale. Pehea la ka loihi a me ka mea mau i nā Time] ke wale pane i kekahi mau ana hoʻohālike. Ua ua ike ia i ka mua o ka kanaka, ka poe ilihune prognosis. Inā 'oe e ole pili i ka manawa, e ike i ke Kauka, ka maʻi pale ua hoolohi a oia Ka hui ma complications:

  • bronchial iaʻi;
  • naehana insufficiency;
  • ka hooulu ana o ka "pulmonary naau";
  • emphysema;
  • he mea koʻohune flora.

Naehana hanu ole e hoʻomōhala ai ma hope o bronchial iaʻi. Ke hoomanawanui i ka ke ano ua kiʻekiʻe o deteriorating me na ia maʻiʻaʻai hoʻomaka e auou caiaiai e connective'aʻaʻa, ke kaʻina i ana spontaneously ma hope 1-2 makahiki.

Ke kiʻekiʻe, ka mea naʻau hoʻomaka e hoomahuahua i aie i ka muli o ka oxygen i loko o ke koko. Akā, mākou e ole kāpae'ōlelo i ka hoʻopiʻi kū'ē 'ana no ka' inikua kōkua, no ka mea, e Lefgrena maʻi pale ka treatable.

lapaʻau

Eia naʻe, Medco hiki ole loa ke hoola ia sarcoidosis, no ka ua i ike maopopo kona etiology. Akā, na kumu i hoakaka ia kūikawā Inc i mea hiki ke hooki i ka hooulu ana kaʻina hana, kanaka hoʻoponopono Lefgrena maʻi pale. Lapaʻau hoʻomaka me ka mākaʻikaʻi steroidal Anati-hoʻoʻino ai 'no ka haahaa e hoʻonele. I hoakakaia wikamina eiiieaenu, antioxidants, immunosuppressants.

I ka papa o ka lapaau mau ka awelika o ka 8 mahina. Ua pau hilinaʻi nui ma luna o na ano kanaka o ka'ōnaehana paleʻea nenoaiu. E Uwao OAXA 'inikua ponopono-i no ka mea maʻi kauka pulmunologom, maikaʻi loa ia mau 5 makahiki.

He aha ka ke Kāohiʻana?

E pale aku i ka ulu ana o ka sarcoidosis, e mua lawe malama o ko lākouʻaoʻao o ke ola. Meaʻai e e 'O ke kaulike, hoʻohui pū bipi kūpaluʻia, nā polokina, carbohydrates ma ka kaʻoi loa lākiō.

People predisposed e sarcoidosis, e haawi aku i ka uiki e, i ka hui 'ana meʻano pākīkē Nine Inch waiwai.

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