Ola kino, Maʻi a me nā kūlana
Polycystic hakuʻala
Polycystic hakuʻala maʻi o ia i mea nui a me ka loa maʻi, IeAUPIIe, IAa IO he mau-ala kaʻina hana, akā, ka mea, o ka hakuʻala i ke loli i ka loli iki ana degere. I ka maʻi ua hoikea mai oia, i loko o ka hoʻonuiʻana o nā pūʻulu hakuʻala cysts, i mea poepoe pouches me ke koʻana koko wai. Kokoke manawa, polycystic hakuʻala maʻi e hoʻomōhala ana i loko o ke alo o ka aaiaoe predisposition.
Hanana cysts 'ana pili i ka hanana o ka haunaele o ka hakuʻala tubules i kuleana no ka mimi auaiaea. E like me ka hopena, hāʻule pahū wale i kekahi o ia blindly, e alakai ana i kā lākou piha iie wai, a laila mimi. Ma maʻamau ana, i ka hakuʻala, ka mimi ma hope o ke pa a ke ku i loko o kaʻaʻa puʻuwai tubules ua hoouna mai ai i kaʻohiʻana i ke leki uea, a mai ia ma ka puna nui a me ka uuku o ka hakuʻala, a komo i ka ureter ua laila excreted mai ke kino.
E hoomaopopo i ka nui pepa elua o polycystic hakuʻala pu ole, type hooilina. Ka palapala mua ka oi, he pono ole ma ka kamaliʻi, loaʻa i ke keiki, e like me ka rula, koke ma hope o ka hānau, a kapa aku la polycystic autosomal recessive hakuʻala maʻi, i ka lua o ka loa pinepine helu kuhi puke ma waena o nā makahiki o 35-40 makahiki, a ua kapaʻia autosomal Hoʻohaku polycystic hakuʻala maʻi. Autosomal Hoʻohaku ano o ka polycystic me na thousandth noho ana o ka Honua, a me ka mea kekahi o ka loa, he pono ole aaiaoe maʻi. Aia nō a puni 11-12 miliona. People loaa mai i kēia maʻi. I ka 90% o ka autosomal Hoʻohaku polycystic palapala ili mai o nā mākua, i ka i koe, 10% - i ka hopena o ka noho'na makaainana i ulu mutations.
Loa pinepine, polycystic hakuʻala maʻi ua diagnosed i loko o kanaka ma waena o nā makahiki o ka iwakalua a hiki i na makahiki hookahi kanaha. I ka maʻi e hoʻomōhala ana i ke kiʻekiʻe, kokoke mai ka hanau ana, a me ka mea pilikia wale hoʻomaka ma ka adulthood. I ka maʻi i like hoʻomaopop 'ana i loko o nā kānaka a me nā wāhine, he mea hiki ole i ka hōʻike a kaʻawale kekahi pae o ka lehulehu, e loaa ana mai o ka maʻi oi pinepine ma mua o na mea e ae.
polycystic hakuʻala maʻi: symptoms.
Eia naʻe, ka mea mua symptoms o polycystic hakuʻala maʻi i hiki ole ke hoolaulea ia me ka maʻi: kiʻekiʻe ke koko, luhi, hoopaa hoi i kaʻeha ma ka lumbar aina, kāna hana no nā mea'ōnaehana mānowai koko'ōnaehana, pinepine urination, pinepine i kawili pu ia me ke koko. Pae holomua Lālā paʻa ano pu ma ke ano o polycystic bulge i loko o ka abdomen. Pinepine lawa no ia, e like me ka ke kākoʻo 'maʻi hou pili pyelonephritis, i hana' ano kūpono no ka? Aneii o pathogens.
I Ina o ka 'inoʻino loa i ka parenchyma, e hoomanawanui i ka mahina i ka ikaika pono o ka makewai, a hoʻopau nui dala o ka wai, e like me ka loli ana e polycystic puʻupaʻa mea hou hiki ke ponoʻole noʻonoʻo mimi. I ka hopena o keia 'ole o ka derivation oʻaneʻane pau kinowai hoʻi.
Ke kumu nui weliweli o ka hooulu ana o polycystic hakuʻala mai, ma a nā puʻupaʻa mea i hiki i ka pololei i, e lawe mai lākou i hana '.
polycystic hakuʻala maʻi: lapaau.
ʻano nui makeʻe kulana lapaau o ka maʻi ua hoemi ia i ka hakakā maʻiʻaʻa puʻuwai insufficiency a me ka haumāna maʻiʻaʻai o nā puʻupaʻa. Ma ke alo o nā complications e like me eiei? Glomerunefrit waeia steroid hormones a me ke alo o ka hypertension - antihypertensives. Ma kekahi hihia i kaʻoki lāʻau lapaʻau lapaʻau ua paipaiʻia, i mea hoʻokaʻawale resection cystic cavities ia ho me mechanical iaʻi o ka mimi outflow, a paipai i ka mea hōʻemi o kaʻaʻa puʻuwai perfusion. Eia hou, nā mea maʻi e pakele excessive physical exertion, luliluli, lōʻihi loihi, oe e makaala ia oukou iho i ke anu a me nā mea palahēhē, i mau kanaka hoʻoponopono i ke ano o na niho a me ka puʻu.
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