Ola kino, Maʻi a me nā kūlana
Thrombocytopenic purpura i loko o nā mākua:ʻike, kumu a me ka lapaʻau
Thrombocytopenic purpura i loko o nā mākua - mea he kāna hana i hiki ke alakai i kokololio muli o ka nui paopao koke mai oia, a kahe ana ke koko. E like me ka rula, i ke koko poho mea ku pono i ka halawai haule ma ka platelet helu - na keena e hoʻonui i kona clotting.
Kekahi kumu o keia pathology ua i kapaia'ōnaehana paleʻea thrombocytopenia. Ua loli ai i nā mākua a me nā keiki, akā, ma ka opiopio nā mea maʻi e like ke ano ana e hoʻomōhala ana i loko o ke kāʻei kua o ka mea hoʻomaʻi maʻiʻaʻai a me ka noonoo ana ma kona iho me ka pono no ka kūikawā lapaau. Ma nā mākua, i ka maʻi i loko o ka hapanui o na hihia o ka lōʻihi kekahi.
Inā 'oe i ole hoailona o ke kahe ana ke koko a me ka platelet helu, naʻe haʻahaʻa, akā, ma ka rula, kupono, i ke kauka e loa paha e ole i koi' lapaau. Ma pohihihi keia hoopii, nae, o ka helu ana o platelets moe a hiki i ka pilikia palena iki, ma o na la ola-hooweliweli maloko kahe ana ke koko. No ka iapaau ana o kēia mau complications koi koke 'inikua' uao.
symptoms
Thrombocytopenic purpura i loko o nā mākua (kiʻi ma luna) ua mau pu ma mawaho hoikeana o ka maʻi. Ma ka hihia o typical symptoms i na kēia mau hoailona o ka maʻi.
- nui kokololio ho okumu o ka nui i pēpē (hematoma);
- superficial kahe ana ke koko i loko o kaʻili i ka oi ana e like me ka poʻe noʻonoʻoʻole moku, ulaula-poni kiko (petechiae) o, a ua IIeEeAIEUIeXAIIUE ka hapanui ma luna o nā wāwae;
- kahe ana ke koko mai ka nui aʻe ana paha ihu;
- i ke alo o ke koko ma ka mimi a noho;
- unusually kaumaha menstrual kahe ana ke koko.
I ka wa e ike i kekahi kauka
Thrombocytopenic purpura i loko o nā mākua e ia he mea e hopohopo nei, a ma keia ina ia mea maikaʻi, e hana i koho ma ka mua a hiki i ka palapala hōʻoia no hoʻomalu.
Inā 'oe i hoomaka ai e kahe mau, kahea aku "ambulance." Typical no keia maʻi kahe ana ke koko hiki ole ke hoi malalo o koʻike mau mea, mai ka hale kini puʻe wale paha typical ano o ke koko i pau ka moni. No kekahi laʻana,ʻaʻoleʻoe e kōkua i ka physical puʻe ma ka kūpono 'āpana o ke kino. Poe akamai i paipai aku, e huli ana i ke kōkua o ke kauka me ka hikiwawe e loaa.
kumu
Idiopathic thrombocytopenic purpura i loko o nā mākua i kekahi manawa? Acaeoey? No ka mea, i ke kino o ka'ōnaehana paleʻea'ōnaehana kuhihewa ho'āhewa wale, a pepehi platelets. Kaʻia "idiopathic" 'o ia hoʻi "Hawaiʻi no ka ike kumu"; thrombocytopenia no laila, i emi iho ma ka manawa, kahi kauka i hiki i ka hoʻoholo 'ana i triggered lawa ponoʻole naoh o ka'ōnaehana paleʻea nenoaiu.
Nā keiki i ke kāʻei kua pathology ka IeAUPIIe, IAa IO uuku, mai ka kāna hana i e ka hapanui o ka infectious maʻi (mumps a maʻi palū). Ua Ua ea ae ka hana i ka maʻiʻaʻai ma loko o ka maʻamau functioning o ka'ōnaehana paleʻea nenoaiu.
E hoomahuahua oe i platelet disintegration
Inā ka loiloi muaʻike, i thrombocytopenic purpura i loko o nā mākua, i ke? Aaieou (lapaʻau hoikeana) ua pili, IeAUPIIe, IAa IO me ka'ōnaehana paleʻea kāna hana. ʻO nā mea'aʻaʻa paʻa i ka platelets, omaka ia me na keena e e luku. Spleen ke hoʻololi i ka hana me ka mawaho nā mea palahēhē, ka lāʻau lapaʻau kino ke hoʻomaopopo iho, a lawe aku oe i na platelets mai ke kino. E like me ka hopena o keia erroneous i ka hoʻomaopopo pono i loko o ke koko circulates nui uuku helu o platelets ma e like me ke kūmau.
Normal platelet helu ka ÷ 150 a hiki i 450 tausani keena no microliter o ai hoʻolahaʻia ke koko. People diagnosed me "thrombocytopenic purpura" (nā mākua) Ka Ikepili hōʻike keena wale 20,000 koi 'ia. Mai platelets paipai koko clotting, hoemi i ko lakou helu maoli i ka pilikia o ke kahe ana ke koko a me na kahe ana ke koko. I ka nui o ka 10 tausani aeea me kill. Me ia he nui emi i loko o ka helu ana o platelets kūloko ma hemorrhage hiki ia oe hoʻomaka e like me kekahi trauma.
kamepiula kumumea
Thrombocytopenic purpura i loko o nā mākua (Photo hoʻohana ma o ka hoʻomaka o keia 'atikala, hōʻike ka mawaho hoikeana o ka maʻi) ua loaʻa i kekahi makahiki, naʻe, ua hōʻike' epekema mau kamepiula kumumea e hoomahuahua i ka likelihood o ulu i ka maʻi symptoms. Ka mea, e:
- Moe ano pono'ī. Ma nā wāhine, i kēia kāna hana ua diagnosed ma awelika elua i ekolu mau manawa hou aku pinepine ma mua o nā kānaka.
- Nei, he mea hoʻomaʻi infectious maʻi. Mumps,ʻo Waimānalo a me ka ÷ naehana hanu nā mea palahēhē i alakai i ke ano o ke ano symptoms o thrombocytopenia, akā, me ka pilina me nā mea hoʻomaʻi loaʻa loa pinepine i loko o nā keiki.
Ka mea, e pale aku i ka pilikia o complications. Ka loa nui o ia - keia mea he lolo hemorrhage, a hiki e ona.
hāpai keiki
ʻOiai thrombocytopenic purpura i loko o nā mākua diagnosed a hiki i ka hapai wahine, i ke kūlana o ke keiki ola ia pathology makuwahine i loko o ka hapanui hihia ua i loli. Poe akamai, akā naʻe, ka mea, ua waiho ia e kaha i ke kiʻekiʻe o platelets i loko o ke koko o ke keiki koke ma hope o ka hanau ana.
Inā 'oe e hapai, akā, i ka hoao ana hualoaʻa hōʻike i ka emi ma platelet helu, oe e ma kamepiula like me ka pahiki o ka puka ikaika o ka postpartum hemorrhage ka loa kiʻekiʻe. Ma ia mau hihia, he mea he gynecologist paha ka haukapila, kauka e kūkākūkā pūʻoe i ka loaʻa therapies ua pakele na keiki.
lapaʻau '
Ke kauka ua hiki ia e ka pololeiʻike, "thrombocytopenic purpura" (nā mākua), e ke hanaʻike, ma ka palena pau rula. It e e koke noho aliʻi mai nā hiki kumu o ke kahe ana ke koko a me ka emi ka helu o platelets - e laʻa me, maʻi maʻi a meʻaoʻao 'ole o ka ai' ia e 'oe.
Ke hoʻomalu, e ninau aku au ia oe i na ninau e pili ana i kou 'inikua mōʻaukala, e paka ka loiloi mua' inikua keia hookolokolo ana a me ka ae i hoʻokohu 'ia hoʻokahi a oi maʻamau PalekanaEND_LINK ho'āʻo ma. Ka hope nā:
- Piha koko helu. Ma muli o ka hāpana ia mai o ka hoomanawanui ka koko me ka nānā 'nohona ma lākiō o ke koko keena, a he mau helu o platelets. I ka thrombocytopenia hope aiao mea abnormally haʻahaʻa, hoʻowahāwahā i ka mea i ka pae ana o keʻokeʻo a me kaʻulaʻula koko aeee e koe i kaʻawelike.
- Lapaʻau Ka Ikepili o ke koko. Ua like ua pinepine hana e hoʻokūpaʻa i ke kiʻekiʻe o nā platelets loaa mai ma ka huina koko Ka Ikepili. A hoʻomanawanui specimen ua kau ma luna o ka kūikawā aniani kiʻiaka, a hookolokolo aku la ia ma lalo o ka microscope.
- Ka Ikepili o ka iwi ka lolo. Kēia noiʻi iaoiaeii ua wale paipai no kanaka makua hoʻomanawanui iki mai i kaʻike, mua o "thrombocytopenic purpura" (nā mākua muli o ia i kekahi hanana Ua oi kūpono, ka mea, e hiki pono e tolerate i ke kaʻina hana).
Platelets i hua mai la i loko o ka iwi lolo - ka palupalu, a naele ia'aʻaʻa ma ka waena konu o ka iwi nui. Ma kekahi mau hihia, i ke kauka e wehe i ka hāpana o ka iwi'aʻaʻa aia i loko o ka iwi lolo biopsy hana. Kekahi hoʻomalu makemake e lawe Eia kekahi laʻana no Ka Ikepili ma ke kaʻina hana i kapaia "wehena," a laila, wehe 'ia mai ka iwi lolo wale i ka hapa o ka kinowai ke keʻena. Loa pinepine, ua mālamaʻia nā kaʻina hana mau ka poʻe, a ua collectively kapaia "iwi lolo Ka Ikepili."
Idiopathic thrombocytopenic purpura iwi lolo Ua noa mai pathologies, e like me ka ho'ēmiʻana i loko o platelet helu kena ae la ma ka make ana o na keena ma ka koko a me ka dysfunction o ka spleen, aʻaʻohe pilikia me ka? Iecaianoaaiiie o platelets.
lapaʻau
Easy thrombocytopenic purpura i loko o nā mākua, ka mea,ʻaʻole reliably hookupaaia na kumu o ka a, IeAUPIIe, IAa IO 'aʻole i koi' ilepili lapaʻau -ʻano mau ike e ke kauka, a mai ka manawa i ka manawa, e kaha i ke kiʻekiʻe o platelets. Children aneane aole koi lapaau, a me ka hāʻule pohō wale holo iho. Mākua, akā naʻe, e noi aku i ka hoʻokō lapaau ina keʻano ua lilo loa ai hoʻolōʻihiʻia (maʻi) külana.
Nā Papahana O Ka Inc mea okoa, a lauwili mai ka lapaʻauʻia ka ulu ana ka paepaeʻana platelet helu ma mua o keʻoki kino, e wehe i ka spleen (splenectomy). He kupono e kūkākūkā me kou kauka ma mua lapaʻau koho pu me nā pono a me nā keakea o ka hana. Kekahi e hoomanawanui i loaʻa i kaʻaoʻao ona mai lawe lapaʻauʻia hoopakele mai ia ia aku he leo, a discomfort ma mua o ka mea maoli hopena o ka maʻi.
lapaʻauʻia
Ke kauka, e kūkākūkā pūʻoe i kaʻaoʻao ona, a me ka laʻau heluna o ka lapaʻauʻia a me dietary pakuʻi ai i au e lawe i ka manawa. Paha kekahi o ia mau mea kōkua emi i ka pae ana o platelets i loko o ka hoʻolahaʻia ke koko. Kēiaʻaoʻao 'ole i aspirin, "Ibuprofen", "Ginkgo biloba" a me ka "Warfarin".
Ka papa kuhikuhiE papa
A hiki aku i kaʻike, ua hookupaa iho la ia e "thrombocytopenic purpura" i loko o nā mākua, lapaʻau e iloko o kona lawe ana i ka kēia lāʻau:
1. lapaʻauʻia e uhi i ka'ōnaehana paleʻea nenoaiu. He nui nā mea maʻi i loko o ka kakahiaka Inc hookuu una corticosteroids e like me "Prednisone". Hoemi'ōnaehana paleʻea'ōnaehana haʻawina, keia k paipai 'ia ka platelet helu. Once ka pono 'ilikai ua hiki aku kaʻoluʻolu kiʻekiʻe o, e ia ma lalo o ka hooponopono ana o kekahi kahuna lapaau ke kiʻekiʻe o lawe i ka lapaʻauʻia ana. I ka papa o ka lapaʻau i mai elua i eono pule.
Ka pilikia mea i thrombocytopenic purpura i loko o nā mākua, nā symptoms o ka i hele mai ai i mea ole ma hope o ka loaa ana "Prednisone" hiki mai hoʻi i ka pauʻana o ka Inc. Kauka pele i koi 'ia i ka hou papa o corticosteroids, nae, ua hana hiki ole ke hoomau loa no ka meaʻaoʻao hopena o keia ka lapaʻauʻiaʻano. I ka hiki overdose cataract, mahuahua koko kō pae, mahuahua pilikia o infectious maʻi a me ka osteoporosis (hoʻonāwaliwali maoli nō o nā iwi).
2. ka pahu kui, e hoomahuahua i ka huina helu o ke koko keena. Inā corticosteroids e ole ke kōkua, kauka i hoakaka ia i ka pahu kui o ka'ōnaehana paleʻea globulin. Kēia lāʻau 'ua i hoʻohana' ia ma ka hihia ma ka hoʻomanawanui hōʻike loa kahe ana ke koko e pono kokeʻoki lāʻau lapaʻau 'uao. Ke kanawai mau no ka mau o ka pule. Mawaena o ka mea e hikiʻaoʻao ole - headaches, ka luaʻi, a me ka haahaa ke koko.
3. mea haʻilula keimikala hōʻeleu i platelet? Iecaianoaaiiuo. Ai 'e like me "Romiplostim" a me ka "Eltrombopag" ( "PROMAKTIV"), e kokua i ka iwi lolo e paka hou platelets. Ma ka palapala o kaʻaoʻao 'ole paha e headache, pōniuniu, nausea a me ka luaʻi.
4. Nā immunosuppressants. "Rituximab" ( "Rituxan ') ho'ēmi i kā ke ka nui ana o ka'āno'ē pane o ka'ōnaehana paleʻea'ōnaehana i nā hualoaʻa ma ka maʻamau platelets e luku. Loaʻaʻiaʻaoʻao waiwai nā ili poʻe noʻonoʻoʻole, haʻahaʻa ke koko,, ke kuni, a me ka nui puʻu.
Inā ai 'i powerless
Inā (a me kekahi manawa mai i kōkua i ka makua no kou kino e like me na kumu o ke ola i ke Aloha Hawaii, ae ho'āʻo ana ka waiʻona, a lawe ka lapaʻauʻia, e pakele no ka pilikia) oe i holopono nō thrombocytopenic purpura, he kauka e waiho akuʻoki kino. No kona wehe 'ana o ka spleen (splenectomy) hoʻomaka koke eliminates ka pathology, e like me ka surgeonʻoki i ka papa kuhikuhiE mea make o nā platelets. E hoʻomanaʻo naʻe, i oe u i pilikia o postoperative complications. Eia hou kekahi, kanaka me ka spleen mau i loko o ka māhuahua pilikia o ka aoao hana infectious ka maʻi.
'ano like ki ina hana like
Inā, no ka ola 'ole' ē aʻe kumu, e hiki ole ke hoʻolimalima hale i keʻoki kino, ke hoʻomalu i koi 'ia ke komo' ana o ka hou lapaau - no ka laʻana, "azathioprine" ( "Azathioprine", "Azasan"). Eia naʻe oi potent ai 'Komo oi loaʻaoʻao ole. "Azathioprine", ma ka nui, ke kumu no ka hoomahuahua i loko o ke kino wela, headaches, nausea, ka luaʻi, a me ka Muscle eha.
Me ka maʻi hainā
Oe i diagnosed me "thrombocytopenic purpura"? Ma nā mākua, pono ka hanana o kēia maʻi i ka loli ma ka Aloha Hawaii. Mai ka maʻi ua pu ma ka māhuahua pilikia o ke kahe ana ke koko, loaʻa palena papaha mea pepehi hui 'haʻuki (mokomoko,ʻoihana kaua, pôpeku) a pehea e hiki ke lawe mālama o ke kino iho.
Similar articles
Trending Now