Vascular malformation: mea, lalau mai, symptoms,ʻike, a me ka ohe.

Inā ma ka kaʻina hana o embryonic? Acaeoey ua o Nyos i ke kahua o ka circulatory'ōnaehana, ka vascular malformation ua hana. Kēia mea he pololei ole pilina o na aa koko a me arteries, i hoike mai ai ia ia iho i loko o adolescence. Ua pau hoʻomaka me headaches, migraines a me ke kāʻili 'ana. I loa hoopii, na keiki i ke kāʻili 'ana.

ka wehewehena

vascular 'ole kekahi ma ka circulatory nenoaiu. Kekahi mau pūhaka, kekahi mea muscular pā, kekahi i kiwikā, akā, i nā mea a pau i pili i kekahi i kekahi mea i loko o ka ua kaʻina. Inā no kekahi kumu o ka hoʻokumu 'ano o ke kaʻina, ua wāwahiʻia, i nā conglomerates i hanaia convoluted moku, kapaʻia malformations.

Nō kāu, keia congenital kāna hana o ike kumu. Ua lŘlŘ ka umikumamaiwa mai o hoʻokahi haneri tausani nā pēpē i kēlā me kēia makahiki. Hiki i malformation aihue maʻi pale, oOeEIAOO ka spinal kaula a me ka lolo'aʻaʻa, e hana i ka aneurysm, a i ka hahauʻana a me ka hemorrhage meninges. Loa pinepine complications hana ana i ka oʻo makahiki, ma hope o nā makahiki hoʻokahi kanahā.

Mea Maluna

He nui na ano apau loa e hiki ke lawe i ka vascular malformation. No kā lākou systematization hana aponoia ma ka 1996 o ka Amelika Mea Maluna ISSVA. Kona kumu o koena unuhi mai nā Mea Maluna - ke kaawale ana o a pau na anomalies ma ka hikoko, a malformations.

1. Vascular hikoko:
   - infantile hemangioma (akaka ma ka kamaliʻi);
   - congenital hemangioma;
   - bunchy hemangioma;
   - veretenopodobnaya hemangioendothelioma;
   - kaposhiformnaya hemangioendothelioma;
   - loaa ma kaʻeho.
2. malformations:
   - capillary (telangiectasias, angoikeratomy);
   - venous (sporadic, glomangioma, Mafuchchi maʻi pale);
   - lymph;
   - arterial;
   - arteriovenous;
   - hui.

Malformation o aa koko

Venous Malformation mea'āno'ē ulu o ke aa koko, ukali ma kā lākou mau pathological mailaila aku. He ka loa, he pono ole i waena o nā mea a pau ano o malformations. Kēia maʻi He congenital, akā, i hoike mai ai ia ia iho i ka wā kamaliʻi, a me ka adulthood. Hoʻololi i ka wahi o ka moku ke lilo i kekahi mea: he ko mākou hopohopo systemic, na nā loko,ʻili, iwi a me nāʻiʻo.

Venous malformations e ia ma luna o kaʻili paha i loko o ke kino e moe pūhaka e kaʻawale ai aeo i loko o kekahi mau kino wahi. Eia hou, ka pilina ka mea, e waiho ana i ka ili luna, i ka oi paʻa kūhohonu loa i ka waihoʻoluʻu o koʻu pomaikai ia.

Aie i ka mea hana ke kinona a me ka waihoʻoluʻu hiki e pioloke me hemangiomas. No ka palena pauʻike, kokoke hōʻemi iki puʻe i ka hapa Hoʻololi '. Malformations i pahee a me ka oluolu, e hoʻololi waihoʻoluʻu. I Ina o ka hanana o'āno'ē moku hohonu i loko o ka kanaka kino externally pathology koko hiki ole ke hōʻike.

Together me ka ulu ana o ka keiki ka a mahuahua malformation, akā, ma lalo o ka aoao o ke kāhea aʻe, e like meʻoki kino, trauma, maʻiʻaʻai, hormonal ai ', ka hanau keiki a menopause, ua hoano e kokololio expansive ulu ana o na moku koko.

Chiari malformation

Kēia vascular malformation, a ua wehewehe aku ma ka haʻahaʻa-e moe ana cerebellar tonsils. Ua ho'ākāka 'ia ka maʻi i loko o ka hopena o umikumamaiwa kenekulia'Aukekulia kauka Hans Chiari, i loko o kona hanohano, a i ka inoa o ka kŰia. He hōʻike 'kekahi o ka loa e like me ka ano o keia anomaly. Aie i ka mea haʻahaʻa henua tonsil alalai mai loli outflow mai o ka lolo a hiki i ka spinal kaula, ka mea hana loa intracranial ka puʻuwai a me ka hoʻonāukiukiʻana mai o ka hooulu ana o ka hydrocephalus.

Chiari malformationʻano iienuaaaony ka pohupani hale cerebellar tonsils ia, a hookuke mai ia lakou ma ka foramen magnum. Kēia hoʻoponoponoʻana o Kamehameha kumu ke anoe o ka spinal Canal, a clinically hoike mai ai ia ia iho i puberty. Ka loa, he pono ole symptoms i headache, tinnitus, unsteady ka wā e hele ana, diplopia, hoʻopōʻino articulation, moni 'ia pilikia, a me kekahi manawa ka luaʻi. No nā pōkiʻi wehewehe aku e ua hoʻemi ka eha, a me ka wela pā lonoaʻili ma ka hoaka o ka hapalua o ke kino a me ka lala.

Chiari malformation lua o type? Acaeoey? Ina mahuahua nui foramen. Ma keia hihia, no ka cerebellar tonsils mai e haule iho, a hāʻule i loko o laila. Ua hiki aku i ka mīkini'opihia o ka spinal kaula a me ka cerebellum pakahi. I ka Ia manawa e hiki symptoms o ka loli ka mālama i loko o ka lolo, naau mā, pohāʻana o ka embryonic digestive'āpana a me urogenital kahua.

spinal kaula

Malformation o ka spinalʻaha - mea he pohihihi keia maʻi e hiki aku ai i ka holumua ai myelopathy. Arteriovenous malformations makemake hoʻonoho ma waena o nā lahilahi a paakiki iwi moe ma ka dorsal ili honua o ka lolo ma ka thoracic a lumbar spine. Ka loa, he pono ole pathology mea, he pono ole i ka makua kanaka.

Ka maʻi kohu i nā symptoms o mau sclerosis a hiki komo i ka neurologist kuleana hūnā '. Aʻoi mea hōʻemi ia lŘlŘ ma hope o rupture ana o na moku koko, a kahe ana ke koko i loko o ka subarachnoid a puni. Nā mea maʻi i mālama kāna hana ikepili koʻikoʻi a me ka Hawaii mau mea, ka hoʻohuikau 'o ka pelvic nā loko. Inā pili ana cortical symptoms, ka maʻi ua lilo hou e like ALS (amyotrophic kīloi paʻewa sclerosis).

Inā ka hoʻomanawanui complains ano o nā okoa neurological kāna hana, pono e kēia ke kauka vascular malformation, a hoʻomaka i ka pilikia makapō nana o ka spine. Na hoailona o ua hoololi vascular lipoma a me ka mea mau o ka mahuahua pigmentation. Oia ke kanaka e hoouna i kaʻume mākenēki resonance kiʻi a me ka lolouila myelography. Kēia e ae e hōʻoia i kaʻike,.

symptoms

Vascular malformation nana e like me ka manawa pōkā pahū a me ka pū panapana liʻiliʻi, a me ka hāmare Ooo hou i loko o nā lima o ke keiki -ʻaʻohe kekahi i ike i ka wā poino, e hoʻomaka. I loko nō o ka mea i ka maʻi o ka congenital anomaly, e hoʻomaka e hoike mai ai ia ia iho, he nui hope. Aia he mau ke ano o ka pele vascular malformations:

- kahe ana ke koko (70% o nā hihia);
- torpid (i loko o ka i koe, 30%).

None o na koho ke ole e noʻonoʻo uʻi no kekahi kanaka i kēiaʻike. Ma ka hihia o hemorrhagic pele i ka hoʻomanawanui loaʻa kiʻekiʻe ke koko, a me ka vascular ka mokuna o ka poe liilii, a me ka ua aia i loko o ka'ā'ī. Ka hapalua o ka poʻe me ka hemorrhagic hahau ana ka hana i kēia 'ano o ka malformation e hiki aku ai i ke kīnā o ke kino a me ka make. Ka pilikia o ke kahe ana ke koko maoli me ka elemakule, a me nā wāhine he hou ololi ka hāpai keiki, a hānau.

Inā he kanaka ana hoʻoneʻe i ka hahau mua, alaila, me ka pahiki 1: i ka makahiki 3, e hou-kahe ana ke koko. A laila, i ke kolu. Eia naʻe, ma hope ekolu Episode, mau ola. Kahi o ka hapalua o nā mea maʻi i huikau kinona e hana intracranial hemorrhages, hematomas a hapa podobolochechnyh tamponade a me ka lolo ventricles.

Ka lua o koho mea he nui pele, a moe hohonu i loko o ka cerebral cortex vascular malformation. Kona symptoms i loa typical:

- convulsive mākaukau 'ole i ke alo o ka epileptiform ho'āhewa wale;
- loa headaches;
- i ke alo o ka nele symptoms like i ka loloʻeho.

syncope

Ua aneane kanaka a pau me ka vascular malformations aia i loko o ka lolo, ma neia hope aku hōʻike syncope ( 'o ia hoʻi, syncope). O ke kumu ho i ka? Aiaiiuie emi i loko o ka cerebral holo. Ma syncope hoomanawanui i kona maka, uhi ia me ke kaheʻana, i kona mau lima a me na wawae, he anu, nawaliwali ka lāʻau ikiʻai a me ka lepo hanu. Ke kaua ana ma kahi o iwakalua kekona, a ma kona hope i ka hoʻomanawanui 'aʻole e hoomanao i kekahi mea.

Kela a me keia makahiki ma laila, he oi ma mua o ka hapalua o ka miliona hou hihia o ka syncope, a me wale i ka hapa uuku wale no o ia mai he maopopo ke kumu-a-kanawai pili. Syncope hiki e kena ae la ia e excessive stimulation o ka carotid sinus, trigeminal neuralgia a glossopharyngeal nā aʻalolo, hooponopono o autonomic insufficiency ko mākou hopohopo'ōnaehana, naau pāpana ka haunaele, a, o ka papa, vascular malformations. 'āno'ē arteries a me aa koko i shunting o ke koko a me ka hōʻeleu i kona pele. E like me ka hopena, i ka lolo ua i noho lawa no kou kino, a ua hoikeia mai kāna hana o ka ike paka i.

complications

E like ma mua o ka malformation hoike mai ai ia ia iho clinically i loko o kānaka ua hūnāʻia, e hoʻomōhala irreversible pathologicalʻike manaʻo. Kēia mea ma muli o ke hypoxic lolo'aʻaʻa hapa, ia dystrophy a me ka make ana. Ke kaumaha ma muli o ka wahi o ka hoʻohuli ai i nā wahi ua mālama i kekahi ano mea nui symptoms (olelo abnormalities, ana, 'no ka naau mai ka neʻe' ana, akamai a me ka 'ole. N.) E hiki anei e epileptic ke kāʻili' ana.

Loa complications hoʻomaka mua i loko o adulthood. 'āno'ē moku koko i lahilahi pā pōhaku, a ua oi prone i fractures, no laila, e hoomanawanui i me malformations hou, he pono ole ischemic hahau ana. Nui conglomerates arteries a me aa koko oOeEIAOO ka'aʻaʻa a puni ia, ma o na la hydrocephalus. Ka noho pilikia loa ka hemorrhage no ka rupture o kekahi mau moku. Ua hiki ole paha i lethal hopena, a pau me ka uuku pahaʻaʻohe hopena. Ua pau hilinaʻi nui ma luna o ka helu o ke kahawai 'o ke koko. Hemorrhagic mapuna mea nui emi i olelo mua iaʻi Outlook, a i recur no manawa.

lapaʻau '

Ka loiloi mua neurological keia hookolokolo ana paha i hōʻike mai i kekahi abnormalities i kanaka me ka vascular malformations. IeAUPIIe, IAa IO ka mea, he pono ka makemakeʻana a me ka loa ia'ku, ninaninau, e kuhikuhi 'aʻe'. Inā ka hoʻomanawanui complains o pinepine loa headaches, tremors, papa'āweʻaweʻa kemika ka haunaele o ka ike paka i a me kaʻole hihiʻo a hele, ia mea he wale, e hoouna aku ia ia, e hoʻomaka neuroimaging. Aloha kau, he kamepiula aʻume mākenēki resonance kiʻi o ka lolo.

I ka loa a me ka piha pololei vascular 'ole hōʻike Akä naÿe angiography. No keia hoomanawanui i loko o ka na carotid artery i injected radiopaque wai, a e i ka moʻo o ka pana pua aku makou. Kēia hana i ka helu ana o complications a me kaʻaoʻao waiwai, nolaila, ua pili wale ma ka hihia o ka pilikia i ka hana ana i kaʻike,.

E nānā i ka māmā holo, alakaʻi a me ka uku o ke koko a hiki i ka pae loli, hoʻohana 'Doppler ultrasound. Kēia papa hana e leie aku mākou eʻike i ke koko hookuuia ma waena o arteries a me aa koko, e hooholo i ke 'ano o ka moku, e hookupaa aku i ka alo ana o aneurysms a me nā complications.

lapaʻau

Ina paha e makemake vascular malformations amenable e? Iaea? Lapaʻau epekema hilinaʻi ma luna o ke 'ano o ka abnormality, kona wahi, ka nui a me ka pulakaumaka o ka mōʻaukala o ka hahau ana.

Aia i ekolu papa kuhikuhi ano o ka lapaʻau.

- hamamaʻoki kino;
- minimally invasive embolization;
- 'ole-invasive radiosurgical lapaau.

No kela a me keia o ia ma laila i nāʻikepili, contraindications, a me ka papa inoa o ka hiki complications.

Ka loa traumatic Ua hamamaʻoki kino. I mea e hele ana i ke ahi, e wehe i ka cranium, klipiruyut ipu, a kela aoao o ia. Oia iʻano mea hiki i loko o ka hihia malformation aia ma luna o ka ili o ka lolo a me ka mea uuku Ana. Ho'āʻo 'o ia e komo i ka hohonu-noho lesions i ka hopena i poho i ka nui heluʻai, a me ka ona e hoʻokūkū.

He aha hiki ke hana ina ka hoʻomanawanui ua kaumaha malformation? Lapaʻau mea endovascular embolization. He He 'ano akahai kaʻina hana, ma a he nui ipu e hanai i ka'āno'ē conglomerate, ua hookomoia he lahilahi catheter ma lalo o X-Ray hooponopono a me ke kauka i loaʻa i ka malformation. A laila, vascular lumen hypoallergenic lawelawe lāʻau e hoopiha i ka loaʻa makahiki, a ālai 'koko i loko o kēia māhele' āina. Eia naʻe, i kēiaʻano hana 'aʻole e hoʻolako loa manaolana i ka moku i oo obliterans. No laila, ka hapanui pinepine ka mea, ua hoʻohana 'ia e like me ka mea manuahi lapaau.

Ka loa holomua papa hana no ka Vascular Malformationsʻana i hana ka hoʻohana cyber pahi (radiosurgery). Ke o Mānoa, no ka papa hana o ka puali ololi e lawelawe radioactive kukuna'āno'ē ipu ahi, mai kekahi pana pua. Ua apono 'oe e koke luku i ka vascular loli, me ka ā' inoʻino kekahi ola'aʻaʻa. Ke kaʻina hana o ka poe paakiki, o ka moku ma ka awelika koko i kekahi mau mahina. Ka pono o ka piha kaawale o complications i loko o ka'emi ko kahua. Akā, aia no na hoʻokau 'ia ka hoʻohana' ana i kēia hana.

1. Ka pono anawaena o na moku e i oi aku mamua o ekolu mau kenimika.
2. Ma ka mōʻaukala e ole e ka hahauʻana a 'ē kahe ana ke koko. Mai ka lahilahi paia a me ka hiki ole ke ku imua o rupture i loko o ka wā mawaena ma waena o ka hooko ana o ke kaʻina hana, a me ka poe paakiki, hope o ka malformation.