Ola kino, Maʻi a me nā kūlana
WPW kŰia: mea, lalau mai, symptoms,ʻike, a me ka lapaʻau
WPW maʻi pale ua kapaia pathology i loko o ke aʻalolo olona, o ka naau Muscle i ke kumu no ke kāʻili 'ana a me ka tachycardia aie a hiki i ka hooholo ana o ka excitation o ke aʻalolo impulse ma hou pōkole mau kuamoo i mea ole i loko o ke ola i ke naʻau.
Ka mua hai
I ka 1930, 'inikua epekema Wolff Parkinson White a me ka mea mua, e wehewehe i nā hōʻailona a me nā hoikeana o ka maʻi paleʻano papa hana, i hope i haawiia mai i ka inoa o ka SVC maʻi pale (WPW). Aia mea e like me ka mea i WPW-kŰia. Mākou i manao ia i loko o kēia 'atikala.
Maʻamau, na olona, i loko o ka naʻau, ua'emi lawelawe excitation ka lāʻau ikiʻai e hana i kekahi ala hele, i hoakakaʻaʻahu, a gradual hoi o ka makana o ka momentum. Neaiae hanauna hoʻomaka ma ka sinus'āina i loko o ka atrium akau hiki i ka od wahi (atrioventricular wahi) i loko o ka atrioventricular ciia, alaila, na wawae o kona pūʻolo ma Purkinje olona, excitation ua pū i hiki i nā mea a pau Muscle olona, o ka naau ventricles, a ua he lōʻihiʻaoʻao hoʻolako i ka wahi a me ka synchronous contraction ka holoʻokoʻa naau Muscle.
Kumu a me nā symptoms
Inā WPW maʻi pale nā aʻalolo impulse excitation mai na atria a hiki i ka ventricles kŰlń ao he pōkole ke ala a hiki i ka ai-kapaia mea nana i ulana Kent, piliwaiwai ka atrioventricular (af) wahi. Ia mea, i ka nalu o ka excitation mea nui māmā ma mua i loko o ka maʻamau pāpana o ke Kal, a no ke aha la he mau incoordination o ka ka ho'ēmiʻana o ka naʻau Muscle, a me acee? Iuo oeiia o arrhythmia.
Ia mea i ke ala o ka naau pepe lāʻau ikiʻai wale.
Similar anomalies i loko o ka 'ole o ka naʻau i congenital, a ua hanaʻia wale nō ke ma muli o ke hereditary ke kanana nei'ōewe paha ma lalo o ka aoao o nā aʻe, he kūlana mea e pono ai i ke kūpono' ana o ke kanaka embryo naau.
Fetus manawa e noho hou atrioventricular apo, a me ka olona,, i loko o 20-22-la pule o thinner a nalo loa. Inā na olona, i waihonakala, eia anatomical aku ana WPW maʻi pale. A hereditary ano o ka WPW-maʻi pale ua wehewehe aku ma ka helu nui o ka af pili 'o Randy, mā a me nā anomalies i loko o ka' ole o ka naʻau. Eia naʻe, wale ma ka adulthood kānāwai i loko naʻe o ka congenital anatomical abnormalities, ka mua symptoms o WPW-maʻi pale. O na hihia a pau, i ke alo o ka 70% o ka maʻi pale ua diagnosed i loko o nā kānaka.
na hoailona o ka pathology
Ka loa, he pono ole symptoms o ka hiki alo o WPW maʻi pale i ka penei:
- E manao ana ikaika a me ka pinepine palpitations, i na keiki ke kapa aku ai "o Kepakailiula a kuʻi naau."
- Koke pōniuniu.
- Unexplainable syncope,ʻano nui i loko o kamalii mai a me ka adolescence.
- Ua eʻeha ma ka naʻau, a me ka tinglingʻoki eha ia ana.
- Aloha o ka suffocation, loa pokole o ka hanu i ka manawa'ōpio wale nō.
- Nā pēpē i hiki ke hoole hanai ana oia i hiki profuse sweating, ikaika nawaliwali, mahuahua naau ana ma ke kamepiula i 200-300 kui iho oe a no minuke.
Pehea e hōʻike maʻi?
A hailona ana o kanaka, ka poe i nui'āno'ē olona, ma ka cardiac Muscle, ka WPW maʻi pale ua diagnosed wale ka wā hanaia cardiac echocardiography. Decipheringʻoiaʻiʻo, e hāʻawi aku i ka hopena.
Oia nā moku halihali mokulele maʻi pale mai i hana eha iaʻi mai bouts o tachycardia a fibrillation, a i hiki e me ka ike ole o ka alo ana o abnormalities i loko o ka naʻau.
Kēia asymptomatic mālama i loko o 35-40% o nā hōʻike 'nā moku halihali mokulele o ka maʻi pale. Mehana pele o WPW maʻi pale ua wehewehe aku ma recurrent pōkole-makahiki tachycardia paha fibrillation, i koke hele me ke kōkua. E hoʻopau hopu i loko o ka hihia o ka meakino umekaumaha WPW maʻi pale kauoha antiarrhythmic ai 'ole kekahi' ano o ka blockers o cardiac excitation.
I Ina o ka hoʻolōʻihiʻia ke kāʻili 'ana i kūpono kou e wehe' ia i medically huikau a me kāna hana contractions o ka naau a me ka Muscle atrial kolili diagnosed loa degere o ka maʻi pale, a paipaiʻoki kino.
maʻi paleʻAno
WPW maʻi pale a me ka naau e hoʻolaha e like me ke alapine (frequency), a oi loa aku hoi ka muli o kela lapaʻau na hoailona, a ua māheleʻia i loko o ka kēia mau 'ano:
- Hoike mai ka wā o ka electrocardiogram mea mau keia aaeuoa nalu, a me ATS-tachycardia a me ka sinus pāpana hōʻike sporadically.
- Ao pau - ua wehewehe aku ma transient ventricular mālama '-excitation.
- Hūnāʻia - wehewehe episodic AVR-tachycardia, a ma ka moku'āina o ke koena ua ole diagnosed.
Pehea'ē aʻe hiki diagnose i ka maʻi pale?
Me ka electrocardiogram e diagnose hiki WPW-maʻi pale mea hiki ma ka hoʻolohe i ka naau kani, a e lilo 'ana o ka' aoʻao o arrhythmic ma ke ano maoli, e like me ka ole Kal.
Ma waho aʻeo ia ECGʻike, o WPW maʻi pale i ua hoʻonānā hoʻohana i ka hana lawe manaʻo me nā uila aʻa lolo, ma ka ultrasound a me ka echocardiography, me ka hoʻokomo 'ia' o ka haumāna kahi nā uila aʻa lolo i loko o ka esophagus me mahope omńkalakala i nā hualoaʻa ma ka pou impulses, e like me luna 'electrophysiological ninaninau, a haawi mai i ka loa pololei ho i loaʻa i loko o ka cardiac Muscle Kent kaola a apono 'mai, e waiho aku i ka makeʻe kulana aʻoki lāʻau lapaʻau lapaau.
WPW-kŰia
I ka wā o nā ana no ke alo o WPW maʻi pale i oi aku mamua o 30% o ka hōʻike 'nā moku halihali mokulele maʻi pale i kekahi hoopii ma ka naau ola i ole ua poe Setoiko. Aie i ka helu nui o ia asymptomatic, i ka makahiki 1980, I paʻi koi i hookaawale WPW maʻi pale me ka kekahi lapaʻau kiʻi, a me WPW-kŰia.
About keia kŰia, ka mea, ua manao ia ma luna o electrocardiogram naʻau sinus pāpana i na hoailona o ka premature ventricular excitation, akā, na kanaka e ole pathological Hawaii a me atrioventricular tachycardia i malama.
I loko nō o kēia, i ka wa a ka kŰia WPW i ka pilikia o ka complications ka loa kiʻekiʻe, e hoʻonāukiuki i kekahi hopena - kino ai 'ole mea naʻau stress, ka waiʻona, hele i ka malihini Leeuwerikplein cii - hiki i ka hoike ana mai o adverse symptoms o WPW maʻi pale. Ma ka makua heluna i loko o 0,3% o ka hihia o WPW-kŰia mea ona, ua hookolokolo keiki hōʻike lapaʻau make i loko o 2% o ka hihia.
'Ikepili helu WPW kŰia i loko o na keiki
Lōʻihi-ʻia ka mālamaʻana no aneane 20 eao no kekahi pūʻulu nui o na keiki i i diagnosed naau WPW maʻi pale, makahiki keiki i ka makahiki 18, hoike mai ka i kēia hopena.
- 8% o nā keiki ua hoano e ulia hookahi o ABP-tachycardia;
- 8,2% o na kanaka ua hoano e ka transient kŰia hoʻololi WPW maʻi pale;
- 8.5% o transient lilo o ka ike paka i ana;
- 2% o na keiki i ka manawa o ka anamanaʻo mua i mua, waiho wale aku lapaʻau make;
- 1,2% - wale keikikane - make koke ana manaʻo au;
- wale 9% o na keiki me ka WPW kŰia hoike nalowale ana o na hoailona aeaiiuo.
Pehea mea pepehi kŰia WPW?
Mai kēia mau oeeo? Ia mea hoike ana i ke alo, a hiki unsafe o WPW kŰia. Kēia kiʻekiʻe pakeneka o adverse symptoms a me pathologies i noho 'ana kamaliʻi, oia ke kumu e kuhi ia me ka minamina kino ai a me ka mea naʻau stress, me ke ano o ka mālamaʻana a me ka pākōlea ana me ka elemakule a me keia pakeneka mea i hoʻoweliweli' ia ola, e wale hoʻonui.
Children me ka WPW kŰia e ole komo i loko o ka 'oihana haʻuki, a malalo i mau stress kumumea. E e lawe kaiapuni i abrupt aniau hoʻololi ai paha hanana, e hookomo ana loa mea naʻau outbursts. A pau o kēia mau kumumea i e loa paha, e alakai i ka mea maʻi a me ka make. Mea i hoʻokumu i ka alo o ka WPW maʻi pale paha kŰia, i hea mai no ka oihana koa hana.
Lapaau a me ke ola ana o ka maʻi pale
Symptoms a me nā nohoʻana i pinepine interrelated. He nui lapaʻauʻia e höʻike aku ka naau ho'āhewa wale , kena ae la ia e ka WPW maʻi pale, a me ka nui loa emi i ka hoike ana o kona symptoms.
blocker ai 'pūʻulu normalizes ke alapine (frequency) o contractions o ka naau Muscle. Eia naʻe, ma ka laulā o ia mau mea ua hoike mai i ka pae ana o 50-60% wale, aʻaʻole hiki ke hoʻohana i mau hypotension a me ka asthma.
Antiarrhythmics muli o kona kulana i ka pilina paʻa paʻapū ho'āhewa wale AVR-tachycardia, normalize naau ana i ka 80% o nā mea maʻi, akā, no hoi i ka helu ana o contraindications i loko o ka hihia o ka hypotension, naau pepehi, a me ka naau maʻi, kamalii a me ka adolescence. Kekahi kalipuna blockers loa contraindicated i loko o ka WPW maʻi pale, e like me ke kiʻi ma ka hope o ka hoʻoponopono hou 'EYI o ke aʻalolo impulse, ka mea e nele i loko o ka atria, a he kaumaha, a irreversible hopena.
Nō hoʻi, ma kekahi hihia, no ka hoʻohanaʻana i ai 'ATP pae malama i ka hopena maikaʻi ia ma luna o ka atrial contraction. Aia nō i 'ole-lāʻau' ano o ke ola ana o symptoms.
Ke Muscle nā aʻalolo impulses kekahi, ma ke aloha o a me ka parasympathetic olona. Ka muaʻano o olona, haʻalele no ka naau, i ka lua o kaʻano o nā 'aʻole hoʻi i ka naʻau ana, e like me keʻano o ka vagus nā aʻalolo nervus vagus, a me kekahi kapa vagal reflex. ʻo ia hoʻi, ke ho'ā hope o kaʻoi loa kēiaʻano o ka reflexes, e haawi aku i ka hopena o ka noaaeeecaoee o ka naau. Ke easiest ala e haʻalele vagal impulses o ka ai-kapaia reflex Aschner i hoʻonāukiuki 20-30-kekona he akahai hoʻopā aku i ka'ōnohi a poʻopoʻo ka a pinepine kōkua e hooki tachycardia.
Nō hoʻi, i ka vagus nā aʻalolo ua pono ka ho'ā 'ia paha e ka hanu-ana a me ka anakahi uila abdominal nāʻiʻo, no laila, i ka kŰia o WPW maʻi pale a pono e hana Yoga, a ha kino.
E hoʻomaka hana poi pu neaiaea ma ka'ūholo uila hookomoia i loko o ka esophagus, loa ka pono aɃe kaumaha hooloihi ae i tachycardia, akā, i kekahi manawa, e alakai ana ia i ka fibrillation o ka naʻau, no laila, hana ma kūikawā cabinets i hoʻolako pono me ka defibrillator.
Defibrillation ua hana wale i loko o ua hanahana loa hoopii, ka wā loa hoʻoweliweli 'ana i ke ola, akā, ka mea pinepine kōkua e hoʻopau pilikia hotbeds o ka haole impulses ma cardiac'aʻaʻa a normalize naau pāpana hana.
Operative lapaau WPW maʻi pale a me kā lākou mau mea
Inā ia akulla kŰia WPW ECG hana ana iaoia o ka hoʻopau ua pili wale nō i loko o loaʻa kekahi wahi, i hiki, me ka pinepine, a hooloihi ae i tachycardia, i hiki ole ke hoonee aku i ka lapaʻauʻia, e like me ka pono me ka hoʻokumu hihia o ka ulia cardiac make, hoahanau o ke ahonui a me ka 'oihana kumu.
ʻoki lāʻau lapaʻau lapaʻau ua waiho wale ma luna o ka muli o ka hulina a me ka piha ninaninau, a haawi mai i ka loa pololei kiʻi o ka pathological'aʻaʻa nā hale o ka naau. No laila, 'oe e noʻonoʻo e pili i ka e hoohana ia ana me ka kŰia WPW.
Ke hana ua hana ka hoʻohana 'ana i ka kūikawā'ūholo uila, a ua hookomoia ma ka femoral artery i ka naau Muscle ma ka X-Ray kilo, a ma kekahi mau wahi produces radioprizhiganie a ablation, nā aʻalolo olona.
Ua hiki ke kriorazrushenie i pathological nā aʻalolo olona. A me ka mea, i loko o nā hihia a pau o ka hana ka hoʻokōʻana ihoiho 95%. Relapses i hoʻomaka ai ma muli o ke kāpili luku e paa foci, a ma ke alo o nä unuhi nāʻoihana'ē aʻe neural nā'aʻaʻa. Ma ona iho, i ka hana hiki e hana ma lalo o kaiakū anesthesia, kokoke e koko ole, 'aʻole e i complications, i ka loa pōkole ke ola au, a no ia mea, hiki ke lawe mai i kekahi mau makahiki.
Cardiac-oaio? A ma Moscow
Institute o keʻoki kino. A. V. Vishnevskogo - i ka haaheo o ko wahi lulu lapaau, he laekahi iauaeoia no ka lapaau a me kaʻike,, e lawelawe ai noiʻi, mahi 'kiʻekiʻe-ʻenehana lapaʻau' ana a me nā hanana cardiacʻoki kino. FGBU "aeiaioaoneiai Center o mea'ōnaehana mānowai kokoʻoki kino ia. A. N. Bakuleva "hanaʻia 'inikua, iao? A me ka papa hana hoʻonaʻauao o ka polokalamu" mea'ōnaehana mānowai kokoʻoki kino. "
Russian Cardiology Research a? Iecaianoaaiiie Complex e lawelawe ai ana a me ka hana o ka naau maʻi i loko o kiʻekiʻe-ʻenehana honua pae. Ma "cardoid" oaio oe ke undergo i ka piha cardiac loiloi, loaa i kekahi mea e like ai pākōlea lapaʻau ma ka outpatient manawa. Cardiological Center ma Moscow hana pono, no laila, inā 'oe i ka pono no kaʻoki lāʻau lapaʻau' uao i ka hana, e hiki ole kānalua.
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