Kinikini iwi maʻi: mea, lalau mai, symptoms, lapaʻau, Kāohi

Kinikini mea he congenital maʻi pathology i ua hoikea mai oia, e eiei? Osteosclerosis loa o skeletal iwi a me ka hohonu loli ma ka kalipuna-phosphorus pūnao. Ka maʻi He'āina pohihihi keia. Ua Ua hōʻike mua i loko o 1904 ma ka German surgeon a me ka radiologist Albers-Schoenberg (Albers-Schonberg NE). Kinikini mai ia lŘlŘ loa i loko o nā mea a pau makahiki waeʻano, ma ka'āina a pau ma luna o ka honua, like i loko o nā sexes.

I ka maʻi i ka helu o synonyms - congenital osteosclerosis, osteopetrosis, a me ka dysplasia giperostaticheskaya Albers-Schonberg maʻi. Mai hookahuli ai i ke kinikini maʻi, a he maʻi pale i kapaia "kinikiniʻili." I ka kinikini iwi maʻi i loko o ka iwi hoʻomaka e paka keu olelo hoopomaikai waiwai, e like me ka pono me ia ma ka medullary Canal hoʻomaka e kūkulu i kekahi anuanu iwi. A kinikini kapaia congenital ili vazonevroz na moku i loko o kaʻili, loa pinepine 'ia i loko o nā keiki a me ka hoike mai ai ia reticular pūkoʻa ia ma luna o kaʻili ia iho i ka bluish waihoʻoluʻu ma hope o I hoopio ai hoi. Ma hope o lalana ana ia ia i ka symptom nalo. Ua hoi ia lŘlŘ i loko o nā mākua kinikiniʻili me ka lahilahi kukui ili ka poe i pilikia i na moku ke koko.

Ke etiology o keia maʻi mea IKE OLE IA. Ma ka hapanui ikeia hihia o ka maʻi ia i ke kinikini ohana ano, a ua i hiki mai ia hanauna aku ia hanauna aku. Kona inoa kinikini maʻi aie he kūikawā kiʻi o ka X-na kukuna o ka iwi, a ua denoted ma ka hana homogeneity a me kaʻoi iwi nuʻa, e like me ka nele o ka iwi 'ole. Pēlā ka manaʻo i iwi i i ka pōhaku keʻokeʻo.

Aia he mau ano o ka maʻi kinikini:

- e kahe ana me ka ole i nanaia lapaʻau symptoms, diagnosed wale ma ka X-Ray keia hookolokolo ana;

- hoike mai ai ia ia iho i loko o kakahiaka kamaliʻi, ua hai symptoms.

Ke kumu nui hiʻona o ka maʻi o ke ana a me ka hapa, hōʻoʻoleʻa nō o ka trabecular iwi. Ma ka loiloi mua ke kahua o ka maʻi wale sclerotized omo iwi i loko o ka iwi metaphyses, a i lalo i loko o kaʻike ākea'āpana. Eia kekahi, ia akulla kaiʻewaʻewa sila cranial iwi, pili i ka heluna paranasal lua, o ka oi aku iniiaiie a me ka frontal. Make ua i hooleiiaʻi mawaho, a iwi ā mai, ka mea, ua pu ma ka 'aʻe' ana o ka pele a me ka niho? Acaeoey - hoʻololi i kā lākou 'ole, insufficiently ulu aʻa, obliterating na auwai a me cavities o ka niho. Loa pinepine hoʻomanawanui iki mai imi 'inikua noonoo meaʻeha ma ka lala a me ka luhi i ka wa e hele ana. Kinikini iwi maʻi kekahi he kūlana e loli ai i ka ulu ana o ka vascular oihana, e like me excessive ulu o'āno'ē iwi'aʻaʻa ke kiʻekiʻe o replaces ka hematopoietic'aʻaʻa.

Best hualoaʻa maʻi ana mamora i loaa i loko o ko lākou aʻo nō transplants (transplants) iwi ka lolo. He oiaio, pono ka hana ana o keia maʻi i ole a ianoiyuaa a nei. Iapaau ana o keia maʻi uaʻano nui nona ma e hooikaika ana i ka muscular a me ko mākou hopohopo nenoai, a laweia aku la oia ma ka hapanui hihia like outpatients. E hoomanawanui i hōʻike physiotherapy, lomilomi a me kaʻau. Kino e e he piha, waiwai ma ka kumumea oihana mua a me nā wikamina, pono e noho i loko o ka 'ike no, me ka waiū, hawaiian hua a me ka lau, hua maoli a me kaʻai Piʻihonua. Children me kēiaʻike, kekahi manawa hoouna aku la i ka sanatorium lapaau.

Ke kumu o epekema no ka pale maʻi kinikini pili paa ana perinatal PalekanaEND_LINK gestation 8 pule. E pale aku i ka hanana o ka iwi deformities, a e halihaliia oia iwaho pathological fractures hōʻeuʻeu examinations ma orthopedics.