Ola kino, Maʻi a me nā kūlana
Pehea hana myasthenic hoʻoponopono ulia? lapaʻau
Kekahi ulia - ka mea, o ke kanaka ana, i ka i koke, hoʻomaka koke deteriorating papa o ka maʻi, i ka symptoms o ke ola-na olelo hooweliweli au, piʻi pū loa koke. Myasthenic a cholinergic ka hoʻoponopono ulia, o ka hoa o ka myasthenia gravis, i mea no ka mea, i ka hoʻomanawanui i nalo hanu a me kona naau papani iho la i ko lakou pepehi ana. I kekahi manawa, he kanaka ka ola literally heluia minuke, a 'inikua a kokoke kanaka e loaʻa i ka pono, e i manawa e kōkua. No ke aha la ua worsening, ia mehe mea, mea,ʻaʻole he make maʻi myasthenia gravis? Mākou e kaumaha aku i ka mea 'ōlelo maopopo, e hai aku i keia mea a pau e ike: na kumu o myasthenic a me ka cholinergic ka hoʻoponopono ulia,? Aaieou, pilikia malama i ka poe me ka mea a ka mea pilikia i hiki mai ai. Paha kekahi pani ia iā mākou, inā koke ma ka amo paha wale ma luna o ka alanui ia e ia ino, i ka 'ike i loko o kēia' atikala e kōkua hoola ola.
myasthenia
I ka moʻolelo e pili ana i ka hahau ana hoʻomaka 'ana ma ka wehewehe i ka manaʻo o ka myasthenia gravis. I kekahi manawa, lawe a puni i kēia maʻi mawaho o ka uku wahi, e like me ka loaa ana mai myasthenia mau ohumu o ka luhi, lethargy, hiki ole ke hana i kekahi physical hana, e ka easiest.
Myasthenic ulia e hoʻomōhala ana i ma luna o ke kāʻei kua o kekahi mau maʻi, a he like symptoms ia ia, wale hoike ana ia lakou iho i ka nui loa i mua i alakaʻi ai i ka make ana o ka hola 40% o nā mea maʻi. Ano, ina no ka iapaau ana ua hoʻomaka koke, make hiki ke käpae '. I makemake makemake, e hoailona oukou i ka myasthenia maʻi 10 kanaka i loko o kēlā 100 tausani kanaka o ka Honua, a ua loli ana na wahine ma ia 3 mau manawa oi pinepine ma mua o nā kānaka. Myasthenia gravis hiki hoike mai ai ia ia iho i loko o ka wā kamaliʻi, akā, ua hihia, ua pohihihi keia. Ua Uaʻano nui malamaia i loko o nā mea maʻi mai ka 20 makahiki, a mai i ka pala elemakule.
Nā symptoms o myasthenia gravis
Me ka myasthenia gravis, ina ia mea i loaʻa i loko o kanaka, myasthenic ulia hiki ole ana. Naʻe, ka mea, i kekahi manawa lawe ma kekahi'ē aʻe ka maʻi i like symptoms, e laʻa me, e like me ka hua lethargy, nawaliwali, luhi. Additional symptoms i na kamalii uuku:
- palupalu lihilihi, loa kekahi 'i loko o ke ahiahi, a me ka hōʻemiʻana i loko o ke kakahiaka o ka po o ka koena ma hope;
- palua hihiʻo;
- a no ka maluhiluhi, ma hope oʻike mau kiʻekiʻe luhi wahie, no nā kanaka, e like me pii na anuunuu;
- ka loiloi mua bulbar symptoms (nasal leo helehelena ma hope o kaʻai, a me ka laua kamailio ana lōʻihi, ole ma ka puana ana o kanaka palapala);
-ʻano bulbar nā hōʻailona (ole ma ka moni 'ia, pinepine ka hakui o);
- autonomic dysfunction (intestinal paresis, tachycardia);
- lehalehu t hiʻona (ma ka lae hohonu loa wrinkles, ano lehalehu tʻa);
- excessive salivation;
- pilikia i ka malama i ke poo;
- pilikia i loko o ka holoholo.
A kiʻiona hiʻona o ka myasthenia - a pau o ka luna symptoms, ua ino loa ma hope o physical exertion, a ma ke ahiahi, a ma hope o ke koena maikai e hoemi ole loa iʻa.
Symptomatology o myasthenic hoʻoponopono ulia
Inā poino kekahi kanaka mai ka myasthenia gravis, ma lalo o kekahi mau kumu, ka mea i lilo he myasthenic hoʻoponopono ulia. Nā symptoms o ka nń ku maʻi, o ka oi aku e like me tachycardia, kiʻekiʻe luhi nui Muscle (naehana hanu, cardiac), salivation, i ka mea ia manawa e ikaika. ʻO kēia mau hiʻona e typical no ka ulia:
- lōlō o na nāʻiʻo o ka moni 'ia a me ka' ōlelo, no laila, e hiki ke komo i loko o ka naehana'āpana mucus, tuha, ka ai;
- gasp;
- ikaika manaʻo pīhoihoi, a panic ku i ka hemahema o ka lewa;
- he anu hou;
- i kekahi manawa noho'na makaainana i ulu urination a me / ai defecation;
- kahe o ka ike paka i;
- malooʻili;
- ke koko, Lele;
- dilated haumana;
- huʻi naau e hemahema, i mea he 'aʻe' ana o ka naau.
Myasthenic ulia mea o kekahi mau degere:
- oluolu;
-ʻawelike;
- kaumaha;
- ka uila.
Ka oko ao moe ma ka poe ikaika no lakou hoike ana mai ma luna o symptoms. No mea pepehi uila, a kaumaha ulia ma i ke kanaka loa koke, ma ka pono o ka mau o ka minuke, e hoʻomōhala ana i nawaliwali o ka ÷ naehana hanu nāʻiʻo a me ka moni 'ia. Hanu i kokololio ma mua, he makaʻulaʻula, o Kepakailiula i ka puʻe, naau i kela kīnā ma kahi o 160 kui iho oe a no minuke. A laila, i ka hanu hoʻomaka e e keʻakeʻa, a i nalo loa, i kona maka huli uliuli (ma ka lapaau ia ua kapaia cyanosis), i ka'aloʻahiʻa emi, lāʻau ikiʻai wale māhunehune palpable.
Kumu o myasthenic hoʻoponopono ulia
Myasthenia gravis hiki e congenital a loaa. Ka mua ua kauoha ae la ia e ka mutation i loko o nā nā'ōewe. Ka lua e hoʻomōhala ana i ka wā i kekahi kanaka i:
- pilikia a me ka thymus gland;
- kekahi ano o ka maʻi 'aʻai (e like, umauma, akemāmā, ovaries);
- hyperthyroidism;
- encephalitis lethargic.
E kū'ē i ke kāʻei kua o kēia mau maʻi myasthenic ulia hiki ana i loko o ka kēia hihia.
- huʻi infectious maʻi, a me SARS, maʻi palū, bronchitis;
- hana;
- he ikaika manaʻoʻike stress;
- High physical mama no hoi;
- e lawe i kekahi mau laau lapaau (e like, tranquilizers);
- hormonal kāna hana;
- alahele myasthenia hoʻomanawanui iki mai e lawe i ka huaale, ke kue o ka iapaau ana papa.
cholinergic hoʻoponopono ulia
Myasthenic ulia a cholinergic pinepine ana i loko o laua, i mea no ke aha la he mea hewa i loko o ka differentiation, a, me ka a no o ka lapaau. Eia naʻe, i kēia mau mau i kekahi mau mea like mawaho hoike ana mai o ka moku'āina, kena ae la ia e kekahi mau kumu, a iʻokoʻa etiology.
Penei, ka wā myasthenic ulia cholinergic receptors emi i ka pa apŘ o kaʻili lahilahi ma muli o kā lākou i ka make, a me ka mea i koe i ko lakou kuleana pili i hoololi. A cholinergic ulia ia lŘlŘ ka wā excessive ho'ā hope o cholinergic receptors (o ka nicotinic a / a muscarinic). Holo i ka? Eaia kaʻina hana o ka hoomakaukau ana no ka iapaau ana o ka myasthenia gravis ma kiʻekiʻe nā māhele, e like me ka pono i mea e 'ana paha i loko o kēia maʻi.
Diagnose i ka ulia mea i oluolu, no ka mea, coincide me ka myasthenic kona papa kuhikuhiE symptoms. Kōkua pono e hoʻoholo i ka hana i ke kanaka, e like me ka hiʻona e ia kona kulana, ano o cholinergic ka hoʻoponopono ulia: ka hoʻomanawanui hōʻike hoailona o ka intoxication: opu ache, wehe ka luaʻi, diarrhea kaʻina kānāwai. No ka myasthenic ulia wehewehe aku e nā mea a pau, koe ka poe symptoms.
Ka lua o ka hiʻona mea he cholinergic ulia - worsening symptoms o myasthenia gravis me ka hoʻokō i physical hana, akā, ma hope o ka lalau cholinesterase ai '.
hui hoʻoponopono ulia
He keʻano ola a me ke ola pilikia o pathology. Ua hiehie myasthenic ka hoʻoponopono ulia a me ka cholinergic, e hoike ana i kekahi manawa, a pau aku ana i ua hoike me na symptoms. Kēia i mea paakiki e hooponoponoʻike, akā, he nui - lapaʻau, no ka mea, ua mau lapaʻauʻia e hoola mai myasthenic ka hoʻoponopono ulia, cholinergic hou aggravate. A hiki i ka hui pele crises maopopo mau kūlana:
1. myasthenic. Nā mea maʻi i malama haʻi bulbar kāna hana, naehana pilikia, physical hana ke kumu no ka luhi, akā, i ka hooko ana o ka ai '( "Klamin", "Neostigmine")' aʻole i i adverse reactions.
2. Cholinergic wehewehe aku ma symptoms o intoxication.
Hou Ua hoike ia haumāna crises pinepine ana i loko o kanaka, ka poe i lawe mua i keia ai i kela manawa pilikia i loko o na kamalii uuku.
Hiki e manaʻo pü 'hui ulia o ia mau hiʻona hoike ana:
- e hoomanawanui i maopopo mālama pilikia ha a me ka bulbar kue a me Hawaii hana o ka lala hoʻololi uuku;
- aole i nui i lalau ka lapaʻauʻia ho'ēmi i kā pathological symptoms, e like me hou Hawaii hope a aneane kōkua stabilize hanu.
lapaʻau '
E pale hewa a koke hoike lākou huahana kōkua ma ka hoʻoponopono ulia myasthenic, ka mea, he pono e waiho aku i kaʻike, a hiki i ka hoʻomanawanui pono. I kaulana ma luna, kekahi symptoms i e noho myasthenic ulia i loko o ka maʻi i pili i ka myasthenia gravis (e laʻa me, pilikia hanu, ole Heartbeat). Symptomatology cholinergic manawa pilikia like i ka mea hoano e i intoxication, a me kekahi mau pilikia a me ka digestive'āpana. Inā he hoomanawanui i ka AEeAaOA, hiki ke hāʻawi 'ike e pili ana i ke alo o kona myasthenia a me ka lapaau, e lawe mai ia lakou, oleloʻike, ua nui Nohie. E differentiate i ke 'ano o ka hoʻoponopono ulia, kauka hana prozerinovuyu hāpana.
Special pilikia o kaʻike, e malama i ka hui hahau ana. I mea e hoʻoholo kona hewa-ole o ka pae mua ua lawe mai lapaʻau Ka Ikepili o ka hoomanawanui, e like me electrophysiological auhau o ka ole, i loaa mai ma ka loaa ana anticholinesterase ai '.
Ka loa imua o ke kanaka gravis (ma mua o ka ulia) ua 'akomi i ka mea o ka electromyography, Me Tomography, pharmacological a me ka immunological ho'āʻo ma.
Pilikia ka mālama i loko o myasthenic a me ka cholinergic hoʻoponopono ulia
Inā he hoomanawanui me ka myasthenia koke deteriorated (hiki mai ka hoʻoponopono ulia), ma ke ola hele ma luna o ka minuke. I ka papa kuhikuhiE mea i pono e hana a puni - koke i kapa aku ai i ka ambulance. Eia naʻe, i loko o ko makou ike maopopo, he mau manawa, i ka wa hana kūikawā malama ua hoolohi. Pehea hiki mākou e kōkua i ka make i loko o ia o ka hihia? Mua, ho'āʻo e hoolako ia ia i ka hanu, e lawe aku oe i ka mucus mai o kona puu. E like me na rula, pono e loaa mai ka myasthenia oe e i ka leo o ka ina ka mea, i ka maʻi, a me ka ai '(e like me "Neostigmine") a me ka' ohe. Inā he mea i ka poe ola, ana me ka hikiwawe e loaa, he kanaka me ka myasthenic ulia mea pono ke hana i ka pahu kui e like me ka 'ike i loko o ka leo.
Hele mai i ka hoʻopakeleʻana, e koi kauka e hospitalize i ka hoomanawanui i loko o kekahi mea o ka urgency, a ma o ka mālama nui malama mokuna, ma ka mālama nui pilikia iapaau ana:
- hoomaopopo ana i ka airway;
- lako hou i ka o oxygen;
- Lako a me mechanical hoʻokomo ea.
Inā ka hoʻomanawanui i ole symptoms o cholinergic ka hoʻoponopono ulia (ka luaʻi, diarrhea), hoʻolauna i ka i kēia lapaau: "Neostigmine", "Atropine". Ma ke alo o nā symptoms o intoxication pilikia lapaʻau ia mea wā hōʻike wale nō i loko o ka ventilator, a ma ka ka pahu kui o kēia mau ai ', "Atropine", "immunoglobulin", e like me kekahi' ē aʻe 'inikua manaʻo.
lapaʻau
Inā he kanaka i ka myasthenic ka hoʻoponopono ulia, hana maikaʻiʻole ma hope o pilikia lapaʻau lawe mai ma luna o ke kumu o ka lapaʻau a me ka keʻena hoʻokolohua ho'āʻo ma, a kālailai i nāʻano o ka maʻi. Mechanical hoʻokomo ea ( 'o ia hoʻi,ʻimi hoʻopunipuni hoʻokomo ea o na ia maʻiʻaʻai), ke kaumaha ma muli o ka lapaʻau' ana o ka hoomanawanui, e like me ka hoike ana o ke alo o ke o oxygen i loko o ke koko hiki ke lawe mai i ka lāʻeono, akā, inā i ka hoʻomanawanui ma hope o 16 a no laila, hola a oi ka mea, he maikaʻi naoh i "Neostigmine" ventilator aʻe . Nui, i ke kaʻina hana ka mea nui ventilator a me ka pane maʻalahi, e noi ana mākau alu ka mālamaʻana o nā respirators,% i loko o ka haku mele 'ana o ke koko kinoea, koko holo, wela, loli koena i loko o ke kino a me na mea e ae.
An maikaʻi hana e Makuakane me nā 'ano o nā crises i na kamalii uuku o ka hoonohonoho hou plasmapheresis. A pau keia koko mea hōʻikeʻikeʻuʻuku ua lawe mai, mai ka Central (ole kuʻekuʻe aku) aa koko, centrifuged, i ka loli i loko o kona mau pou wai koko aʻimi hoʻopunipuni. Kēia papa hana, oia ke maikaʻi hualoaʻa - i loko o ka mau o ka hola o ka hoʻomanawanui ka ke ano ua hou nui. Plasmapheresis ua hana mai ka papa 7 a hiki i 14 mau lā.
Kekahi o na kuʻina o ka iapaau ana ka lāʻau Inc. E like me ka hoike ana o na nā mea maʻi wahi i immunoglobulins, antioxidants, anticholinesterase ai ', a ma ka alo o ka li nui - antibiotics.
I ka olelo wanana a me ka Kāohi
He kanakolu a kanaha makahiki aku nei, ua hanaia he pinepine ona nā haumāna i loko o nā mea maʻi me ka myasthenia i exacerbation o ka maʻi. Ano, i ka make ana, i ua hoemi e 12 manawa. Oe i ka maopopo i kekahi manawa, mai kā mākou hana me oe hilinaʻi nui ma luna o ke kanaka o ke ola, a loaa he myasthenic hoʻoponopono ulia. Pilikia kōkua E e hāʻawi loa koke. Nolaila, ina koke ma ke alanui, me ka lehulehu amo, wahi ke ike i ke kanaka e hoʻomaka i ke kinai iho, e pono e kapa aku i kekahi ambulance koke.
Myasthenia hoʻomanawanui iki mai ia lakou iho pono i like me ka helu o nā ana, e pale aku i ka hoʻoponopono ulia:
- e ma lalo o ke kauka i ka hooponopono, a me ka ikaika like me ka mea i hoakakaia lapaʻau;
- pale k ‰ ia, ko mākou hopohopo breakdowns;
- hiki kiai e ku e ia infectious maʻi;
- mai, mai kiola aku la i kou kino intoxication;
- i kaʻai, e like me ʻai waiwai ma ka potasiuma (e like, uala mau kīʻaha, waina maloʻo).
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