Ola kino, Maʻi a me nā kūlana
Systemic vasculitis: symptoms a me ka lapaau. Vasculitis - He aha ka i kēia maʻi?
Vasculitis - He aha ka i kēia maʻi, a he aha ka mea i luna 'i ke kino i loko o kēiaʻano?
vascular maʻi
Ke koko moku aie i nā hopena maikaʻi 'aʻe i lilo i ko lakou kuleana pili i, i loli ai i ka ano o ka mea a pau meaola.
Systemic vasculitis - maʻi a i pili me ka'āno'ē vascular pā pōhaku. Ma ka keia kahua i kekahi mauʻano o kēia maʻi.
Ano o systemic maʻi
Ikeia laha 'o vascular pathological loli:
- I ka make ana o na Hoʻohana kanaka o ka arteries meakino a uuku-caliber kapa periarthritis nodosa.
- Maʻi i loli ai kuhikuhi na arteries a me nā ipu koko o ka naehana'āpana a me ia maʻiʻaʻai, konāhuaʻelua a me wale laila, ua ho'ākāka 'ia me Wegener ka granulomatosis.
- Systemic vasculitis, nona symptoms hoike pathology o na ipu o ke kino nui (ka hapanui pinepine - na arteries o ke poo), kapaʻia kanaka nunui aeea kino arteritis.
- Hoʻoʻino keʻano o ka hanaʻana i loko o ka arteries nui, a me ka aorta ua hoakakaia like me ka maʻi Takayasu, a me aortoarteriit nonspecific.
- E like me ka nānā 'ole pathology o muscular type arteries, laila, i ka maʻi hoakakaia like thromboangiitis obliterans.
- Systemic maʻi i ka pu ma symptoms e like me stomatitis, he lesion nā'aʻaʻa o ka waha a me ka wahine mucosa, e like me nā loli i loko o ka maka ua, ua kapaia "Behcet ka maʻi pale."
- Allergic vasculitis.
A pau o ka mea ma luna pepa i pili i kekahi mau mea, lalau mai i hoʻonāukiukiʻana mai o nā loli i loko o ka pā pōhaku o nā ipu koko a me ka 'aʻe' ana o kā lākou mau hana.
Nā kumu o ka maʻi
E hoʻoholo i ka holomua o ka naauao a me ka lapaau kāohi ana, ia mea e pono ke ike i ke kumu keia a ua pathological loli o na moku. Ma ia ka hihia, systemic vasculitis hiki i ka maikaʻi hope no ka hoʻomanawanui.
'Aʻole loa aʻo i nā kumumea i ka hoʻonāukiukiʻana i kēia maʻi, akā, kekahi mau kumu ke kumu ia i ke ea.
- Systemic vasculitis like ke kino o ka naoh i ka hoʻohana 'ana i kekahi mau lapaʻauʻia. hiki i Pathological loli o ka moku pā hoʻonāukiuki i kekahi mea hoʻomaʻi maʻi ia i lōʻihiʻaʻa lapaau.
- Systemic vasculitis like me ka complication o kekahi mauʻano pākīkē infectious maʻi i i ua hoolilo.
- Koko moku hiki ke lukuia iloko o ia maʻi like kū'ē arthritis, systemic lupus erythematosus, hoʻoʻino keʻano o ka hanaʻana i loko o ka thyroid, maʻi autoimmune pathologies, Schwartz-Jampel maʻi pale, a me kēlā wā i kēia wā glomerulonephritis.
A pau kēia mau kumumea ho oholo i ka systemic vasculitis. Symptoms a me ka lapaʻau o ka maʻi ua e mau loa ana me ua hoʻopili, no ka mea, kekahi o na hoikeana o ka maʻi i loko o ka latent palapala, oiai kekahi poe, conversely, e hookuke, e kakau i ka hewaʻike.
He aha ka hana i loko o ke kino? pathogenesis
Ke pathology o ka vascular'ōnaehana entail nā palapala loli i loko o ke kino, i mea hōʻike ma kekahi mau kahua o ka hoʻonaʻauao o ka maʻi. Ka wahi mea i na wahi ka hopuʻia hoʻoʻino kaʻina me ka mahope loa ia'na o ko lākou mau pā.
Kēlā me kēiaʻano o ka vasculitis hooku iho la ia i loaa mai a me kona mau ano.
He aha loli ua pu ma kela ano keia ano?
- I ka wā o ka maʻi pale Behcet malama symptoms ma ku una ha i ka lua, me ka nui stomatitis, a puka mai me ka relapses. I ka lua o ka aoao o ka hoailona hiki ke kapaia ulcers ma ka scrotum i loko o nā kānaka a me nā wāhine - ma ka vagina a me ka vulva. Eia kekahi mucosa, i kēia 'ano o ka vasculitis i ka loli iki ana degere e loli ai'ōnohi a poʻopoʻo.
- Thromboangiitis obliterans ua pu ma ka hoopii ana o nā mea maʻi, i ka ulu ana o ka lameness 'ole ulia numbness i loko o nā lima.
- Aortoarteriit haawi nonspecific 'ole e like me kaʻeha ma nāʻaoʻao lalo a me luna, hoʻi eha, a ua hāʻawiʻia i loko o ka opu, e like me ka pono me maʻule hou ihola nō a me kāna hana pili i ka maka.
Other ano, ke kaumaha ma muli o ka oolea, e kokoke i ka ia symptoms, akā, he pono ka kanaka hoʻokokoke i ka lapaau.
symptomatic kiʻi
Symptomatology vascular maʻi hiki hoʻololi i kou kiʻi, ke kaumaha ma muli mea o ka IIeEeAIEUAA kaʻina hana a me ka pathologies e pili ana i ia mau mea.
Vasculitis pono ili rashes, a pathological haunaele ma ka'emi'ōnaehana entail mahuahua pā lonoaʻili, a e hoano e mai hypersensitivity i haʻahaʻa pā lonoaʻili a me kona piha e kaawale aku.
A hiki i ke koko holo ana o na ipu lolo, ma laila e ana hahau ana a me ka naau ino. Allergic vasculitis hoike mai ai ia me typical me ka allergic naoh i ka stimulus.
Na hoailona o ka vascular pathology
Aia i kekahi, he pono ole symptoms o kekahi 'ano o ka vasculitis nei:
- ka helehelena a piha lilo o ka ikaika loa ka makemake;
- nawaliwali meaola i akaka ole ke kumu, a ua hele pu me ia e apathy;
- kokololio luhi, nā kino a me ka pono;
- ke kiekie kino mahana - haʻahaʻa-papa, i kekahi manawa wale nō ke hele mai e febrile;
- haikeaʻili, pili i ka 'aʻe' ana o kekahi mau holo i loko o ke kino.
He aha'ē aʻe no ka systemic vasculitis? He aha ka i kēia maʻi, a pehea e pale aku ia, hiki ke loaʻa ma luna o kekahi, he pono ole hiʻona. No ka laʻana, ka mea nodularʻano o ka vasculitis hoike aku Muscle aching a pau ma luna o ke kino. Pain kŰlń ao i ka houpo, hoʻonāukiuki ke kaupaonaʻana poho, intestinal kāna hana, ka luaʻi, nausea, a, me ia i kaʻilihune, ka noʻonoʻo 'kāna hana.
Wegner ka granulomatosis, ka hoʻonāukiukiʻana mai i loko o ka nasal lua, a oi kaʻoi loa, i loko o kona poli - pus, ke koko a me ka mucus. ulcerative keʻano o ka hanaʻana ke'ākoʻakoʻa ma ka nasal mucosa. A laila, i ka cough i, umaumaʻeha, pokole o ka hanu, hakuʻala ole a me na mea e ae.
ili lesions
I ka pathological keʻano o ka hanaʻana i loko o ka ipu, kena ae la ia e ka allergic naoh, a laila, i kēia 'ano o ka vasculitis kapa ili. Pehea o ka ili vasculitis?
Poe e ka maʻi i kekahi mauʻano o ka pele.
- ka muaʻano - nodosa necrotic a Werther-Dyumlinga hoikeia aku ai e dermal ioauoa ma ka ili ano me ka bluish eleele malu;
- lua - allergic arteriollit Ruiter, i hoike mai ai ia typical eritrematoznymi rashes ma luna o kaʻili, a pēlā hoʻi me hemorrhagic crusts, ulcers, erosions me ka hope necrosis.
ʻike, o systemic vascular maʻi
Ke koho ana o PalekanaEND_LINK ano E e ma muli o ka mea mawaho hoikeana o vasculitis, akā, no ka hoʻoholo kona wahi huna ano o ka io i ka hou ana i loko o ka anamanaʻo.
E hoʻoiliʻia kekahi ikehu hoomanawanui e lawe i kekahi koko ho'āʻo e hooholo i ka loli i loko ona. laupaʻi nā hoailona o ka hemoglobin mea me ka nui loa haʻahaʻa ma mua o ka wā maʻamau, ka mea Hōʻike i ka hoʻomaka o ka anemic keʻano o ka hanaʻana i loko o ke kino - he complication nui o vascular pathology.
Kākaʻikahi ka, akā, e hana ia i kaʻike, "systemic vasculitis" ua kau ma luna o ke kumu o ka Ikepili o ka mimi, ina e huai ae ulaula koko keena, a keʻokeʻo koko keena.
Ka lua o ka mea o loko waiwai, akā,ʻaʻole emi nui no kaʻike,, he biopsy. No keia hopena, i ke ahonui no microscopic ninaninau e lawe i kauwahi o ka moku'aʻaʻa.
Systemic vasculitis. Symptoms a me ka lapaʻau
Ke kaumaha ma muli paha ia mea allergic vasculitis paha haumāna lapaʻau ua hoakakaia pākahi, a me ka mea, ua kauoha ole wale no o ka iapaau ana o kekahi mau 'maʻi, akā, no hoi no ka hoihoi hou ia ana o ka holoʻokoʻa kino, i kaʻino wale poino ma ke kāʻei kua o vascular pathology.
Ka pahuhopu o ka lapaau o ka piha hoʻopau o symptoms o ka maʻi, normalization o na moku ke koko a me ka holo.
Ai 'i mea mana ma ka systemic vasculitis:
- corticosteroid lapaʻauʻia;
- chemotherapeutic konohiki;
- immunosuppressants.
I ka oiʻano pākīkē vasculitis pono e hoʻomaka mālama nui malama a me ka lapaau. He mea pono i ka hihia o ka malfunction o ka nui nā loko e like me ka naau, akepaa, maʻiʻaʻai, puʻupaʻa. Ma keia hihia, he hoʻomanawanui resuscitation hahai ma symptomatic lapaau.
ili vasculitis pono e hana i outpatient paha i loko o ka haukapila, ke kaumaha ma muli o ka progressiveness o ka pathological kaʻina. Mana i loko o kēia maʻi, e ia i ka hopena o ka'ano'ē readjustment i ka paena o ka maʻiʻaʻai, a ia lŘlŘ mua i loko o ka maʻi ke kahua.
E e hahai ke hoomanawanui me ka moe e maha ai, a lawe i nā kēia lapaʻauʻia:
- antihistamines, a me ka hoʻokō ka lapaʻauʻia no ka vasculitis mea "Promethazine", "Diphenhydramine", "Fenkarol";
- kalipuna hoomakaukau microelement - 10% kalipuna koloriside ka pahu kui a gluconate pāʻoihana;
- rutin, ascorbicʻakika.
I ka inefficiency pili hou Ka Uluwehi O Ke'āpana hana e hoʻohana hormonal hoomakaukau e like me na laau "prednisolone" a me ka "Dexamethasone".
A i ka maʻi ua pu ma ka ulcer a me ka necrotic keʻano o ka hanaʻana, i ka iapaau ana kikowaena topical noi o ka mea poni glucocorticoid (poni "Boron-naftalan" "methyluracyl" a me na mea e ae), epitelioplasticheskie hoomakaukau.
I ka lōʻihi-makahiki, akā, ineffective lapaau i loko o ka papa o ka hoʻohana 'ana o angiotroficheskih kālā. Kēia ka lapaʻauʻia "dobesilate kalipuna", "ksantinola nicotinate" a me na mea e ae.
He aha ka ka prognosis o kēia maʻi?
Ke prognosis hilinaʻi nui ma luna o ke 'ano o ka vasculitis a me ka oolea o ka maʻi. Iʻike, a me ke ake hana hiki me ka nui loa hooloihi i ke ola o ka hoʻomanawanui. He nui ka hana i kaʻike, a me ka hoʻomohala i kekahi e pono ai ke kanaka regimen. Oe e pono koho i ka lapaʻauʻia, a me ka laʻau heluna i mea e pale aku complications a me kaʻaoʻao 'ole.
He mea hiki ole ke kilokilo i ka hope o na maʻi like systemic vasculitis. Iapaau ana e paha i ke hoʻomau ola. Nō kāu, i ka maʻi mea maʻi, a ua hahai aku ia manawa o ka exacerbation ma ka manawa o ke kala. Mai vasculitis pinepine ole loa ola. Man mau puʻe wale akula kēlā, e kipa i ke kauka a me ka hooponopono ana symptoms.
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