Ola kinoMaʻi a me nā kūlana

Systemic vasculitis: symptoms a me ka lapaau. Vasculitis - He aha ka i kēia maʻi?

Vasculitis - He aha ka i kēia maʻi, a he aha ka mea i luna 'i ke kino i loko o kēiaʻano?

vascular maʻi

Ke koko moku aie i nā hopena maikaʻi 'aʻe i lilo i ko lakou kuleana pili i, i loli ai i ka ano o ka mea a pau meaola.

Systemic vasculitis - maʻi a i pili me ka'āno'ē vascular pā pōhaku. Ma ka keia kahua i kekahi mauʻano o kēia maʻi.

Ano o systemic maʻi

Ikeia laha 'o vascular pathological loli:

  1. I ka make ana o na Hoʻohana kanaka o ka arteries meakino a uuku-caliber kapa periarthritis nodosa.
  2. Maʻi i loli ai kuhikuhi na arteries a me nā ipu koko o ka naehana'āpana a me ia maʻiʻaʻai, konāhuaʻelua a me wale laila, ua ho'ākāka 'ia me Wegener ka granulomatosis.
  3. Systemic vasculitis, nona symptoms hoike pathology o na ipu o ke kino nui (ka hapanui pinepine - na arteries o ke poo), kapaʻia kanaka nunui aeea kino arteritis.
  4. Hoʻoʻino keʻano o ka hanaʻana i loko o ka arteries nui, a me ka aorta ua hoakakaia like me ka maʻi Takayasu, a me aortoarteriit nonspecific.
  5. E like me ka nānā 'ole pathology o muscular type arteries, laila, i ka maʻi hoakakaia like thromboangiitis obliterans.
  6. Systemic maʻi i ka pu ma symptoms e like me stomatitis, he lesion nā'aʻaʻa o ka waha a me ka wahine mucosa, e like me nā loli i loko o ka maka ua, ua kapaia "Behcet ka maʻi pale."
  7. Allergic vasculitis.

A pau o ka mea ma luna pepa i pili i kekahi mau mea, lalau mai i hoʻonāukiukiʻana mai o nā loli i loko o ka pā pōhaku o nā ipu koko a me ka 'aʻe' ana o kā lākou mau hana.

Nā kumu o ka maʻi

E hoʻoholo i ka holomua o ka naauao a me ka lapaau kāohi ana, ia mea e pono ke ike i ke kumu keia a ua pathological loli o na moku. Ma ia ka hihia, systemic vasculitis hiki i ka maikaʻi hope no ka hoʻomanawanui.

'Aʻole loa aʻo i nā kumumea i ka hoʻonāukiukiʻana i kēia maʻi, akā, kekahi mau kumu ke kumu ia i ke ea.

  1. Systemic vasculitis like ke kino o ka naoh i ka hoʻohana 'ana i kekahi mau lapaʻauʻia. hiki i Pathological loli o ka moku pā hoʻonāukiuki i kekahi mea hoʻomaʻi maʻi ia i lōʻihiʻaʻa lapaau.
  2. Systemic vasculitis like me ka complication o kekahi mauʻano pākīkē infectious maʻi i i ua hoolilo.
  3. Koko moku hiki ke lukuia iloko o ia maʻi like kū'ē arthritis, systemic lupus erythematosus, hoʻoʻino keʻano o ka hanaʻana i loko o ka thyroid, maʻi autoimmune pathologies, Schwartz-Jampel maʻi pale, a me kēlā wā i kēia wā glomerulonephritis.

A pau kēia mau kumumea ho oholo i ka systemic vasculitis. Symptoms a me ka lapaʻau o ka maʻi ua e mau loa ana me ua hoʻopili, no ka mea, kekahi o na hoikeana o ka maʻi i loko o ka latent palapala, oiai kekahi poe, conversely, e hookuke, e kakau i ka hewaʻike.

He aha ka hana i loko o ke kino? pathogenesis

Ke pathology o ka vascular'ōnaehana entail nā palapala loli i loko o ke kino, i mea hōʻike ma kekahi mau kahua o ka hoʻonaʻauao o ka maʻi. Ka wahi mea i na wahi ka hopuʻia hoʻoʻino kaʻina me ka mahope loa ia'na o ko lākou mau pā.

Kēlā me kēiaʻano o ka vasculitis hooku iho la ia i loaa mai a me kona mau ano.

He aha loli ua pu ma kela ano keia ano?

  1. I ka wā o ka maʻi pale Behcet malama symptoms ma ku una ha i ka lua, me ka nui stomatitis, a puka mai me ka relapses. I ka lua o ka aoao o ka hoailona hiki ke kapaia ulcers ma ka scrotum i loko o nā kānaka a me nā wāhine - ma ka vagina a me ka vulva. Eia kekahi mucosa, i kēia 'ano o ka vasculitis i ka loli iki ana degere e loli ai'ōnohi a poʻopoʻo.
  2. Thromboangiitis obliterans ua pu ma ka hoopii ana o nā mea maʻi, i ka ulu ana o ka lameness 'ole ulia numbness i loko o nā lima.
  3. Aortoarteriit haawi nonspecific 'ole e like me kaʻeha ma nāʻaoʻao lalo a me luna, hoʻi eha, a ua hāʻawiʻia i loko o ka opu, e like me ka pono me maʻule hou ihola nō a me kāna hana pili i ka maka.

Other ano, ke kaumaha ma muli o ka oolea, e kokoke i ka ia symptoms, akā, he pono ka kanaka hoʻokokoke i ka lapaau.

symptomatic kiʻi

Symptomatology vascular maʻi hiki hoʻololi i kou kiʻi, ke kaumaha ma muli mea o ka IIeEeAIEUAA kaʻina hana a me ka pathologies e pili ana i ia mau mea.

Vasculitis pono ili rashes, a pathological haunaele ma ka'emi'ōnaehana entail mahuahua pā lonoaʻili, a e hoano e mai hypersensitivity i haʻahaʻa pā lonoaʻili a me kona piha e kaawale aku.

A hiki i ke koko holo ana o na ipu lolo, ma laila e ana hahau ana a me ka naau ino. Allergic vasculitis hoike mai ai ia me typical me ka allergic naoh i ka stimulus.

Na hoailona o ka vascular pathology

Aia i kekahi, he pono ole symptoms o kekahi 'ano o ka vasculitis nei:

  • ka helehelena a piha lilo o ka ikaika loa ka makemake;
  • nawaliwali meaola i akaka ole ke kumu, a ua hele pu me ia e apathy;
  • kokololio luhi, nā kino a me ka pono;
  • ke kiekie kino mahana - haʻahaʻa-papa, i kekahi manawa wale nō ke hele mai e febrile;
  • haikeaʻili, pili i ka 'aʻe' ana o kekahi mau holo i loko o ke kino.

He aha'ē aʻe no ka systemic vasculitis? He aha ka i kēia maʻi, a pehea e pale aku ia, hiki ke loaʻa ma luna o kekahi, he pono ole hiʻona. No ka laʻana, ka mea nodularʻano o ka vasculitis hoike aku Muscle aching a pau ma luna o ke kino. Pain kŰlń ao i ka houpo, hoʻonāukiuki ke kaupaonaʻana poho, intestinal kāna hana, ka luaʻi, nausea, a, me ia i kaʻilihune, ka noʻonoʻo 'kāna hana.

Wegner ka granulomatosis, ka hoʻonāukiukiʻana mai i loko o ka nasal lua, a oi kaʻoi loa, i loko o kona poli - pus, ke koko a me ka mucus. ulcerative keʻano o ka hanaʻana ke'ākoʻakoʻa ma ka nasal mucosa. A laila, i ka cough i, umaumaʻeha, pokole o ka hanu, hakuʻala ole a me na mea e ae.

ili lesions

I ka pathological keʻano o ka hanaʻana i loko o ka ipu, kena ae la ia e ka allergic naoh, a laila, i kēia 'ano o ka vasculitis kapa ili. Pehea o ka ili vasculitis?

Poe e ka maʻi i kekahi mauʻano o ka pele.

  • ka muaʻano - nodosa necrotic a Werther-Dyumlinga hoikeia aku ai e dermal ioauoa ma ka ili ano me ka bluish eleele malu;
  • lua - allergic arteriollit Ruiter, i hoike mai ai ia typical eritrematoznymi rashes ma luna o kaʻili, a pēlā hoʻi me hemorrhagic crusts, ulcers, erosions me ka hope necrosis.

ʻike, o systemic vascular maʻi

Ke koho ana o PalekanaEND_LINK ano E e ma muli o ka mea mawaho hoikeana o vasculitis, akā, no ka hoʻoholo kona wahi huna ano o ka io i ka hou ana i loko o ka anamanaʻo.

E hoʻoiliʻia kekahi ikehu hoomanawanui e lawe i kekahi koko ho'āʻo e hooholo i ka loli i loko ona. laupaʻi nā hoailona o ka hemoglobin mea me ka nui loa haʻahaʻa ma mua o ka wā maʻamau, ka mea Hōʻike i ka hoʻomaka o ka anemic keʻano o ka hanaʻana i loko o ke kino - he complication nui o vascular pathology.

Kākaʻikahi ka, akā, e hana ia i kaʻike, "systemic vasculitis" ua kau ma luna o ke kumu o ka Ikepili o ka mimi, ina e huai ae ulaula koko keena, a keʻokeʻo koko keena.

Ka lua o ka mea o loko waiwai, akā,ʻaʻole emi nui no kaʻike,, he biopsy. No keia hopena, i ke ahonui no microscopic ninaninau e lawe i kauwahi o ka moku'aʻaʻa.

Systemic vasculitis. Symptoms a me ka lapaʻau

Ke kaumaha ma muli paha ia mea allergic vasculitis paha haumāna lapaʻau ua hoakakaia pākahi, a me ka mea, ua kauoha ole wale no o ka iapaau ana o kekahi mau 'maʻi, akā, no hoi no ka hoihoi hou ia ana o ka holoʻokoʻa kino, i kaʻino wale poino ma ke kāʻei kua o vascular pathology.

Ka pahuhopu o ka lapaau o ka piha hoʻopau o symptoms o ka maʻi, normalization o na moku ke koko a me ka holo.

Ai 'i mea mana ma ka systemic vasculitis:

  • corticosteroid lapaʻauʻia;
  • chemotherapeutic konohiki;
  • immunosuppressants.

I ka oiʻano pākīkē vasculitis pono e hoʻomaka mālama nui malama a me ka lapaau. He mea pono i ka hihia o ka malfunction o ka nui nā loko e like me ka naau, akepaa, maʻiʻaʻai, puʻupaʻa. Ma keia hihia, he hoʻomanawanui resuscitation hahai ma symptomatic lapaau.

ili vasculitis pono e hana i outpatient paha i loko o ka haukapila, ke kaumaha ma muli o ka progressiveness o ka pathological kaʻina. Mana i loko o kēia maʻi, e ia i ka hopena o ka'ano'ē readjustment i ka paena o ka maʻiʻaʻai, a ia lŘlŘ mua i loko o ka maʻi ke kahua.

E e hahai ke hoomanawanui me ka moe e maha ai, a lawe i nā kēia lapaʻauʻia:

  • antihistamines, a me ka hoʻokō ka lapaʻauʻia no ka vasculitis mea "Promethazine", "Diphenhydramine", "Fenkarol";
  • kalipuna hoomakaukau microelement - 10% kalipuna koloriside ka pahu kui a gluconate pāʻoihana;
  • rutin, ascorbicʻakika.

I ka inefficiency pili hou Ka Uluwehi O Ke'āpana hana e hoʻohana hormonal hoomakaukau e like me na laau "prednisolone" a me ka "Dexamethasone".

A i ka maʻi ua pu ma ka ulcer a me ka necrotic keʻano o ka hanaʻana, i ka iapaau ana kikowaena topical noi o ka mea poni glucocorticoid (poni "Boron-naftalan" "methyluracyl" a me na mea e ae), epitelioplasticheskie hoomakaukau.

I ka lōʻihi-makahiki, akā, ineffective lapaau i loko o ka papa o ka hoʻohana 'ana o angiotroficheskih kālā. Kēia ka lapaʻauʻia "dobesilate kalipuna", "ksantinola nicotinate" a me na mea e ae.

He aha ka ka prognosis o kēia maʻi?

Ke prognosis hilinaʻi nui ma luna o ke 'ano o ka vasculitis a me ka oolea o ka maʻi. Iʻike, a me ke ake hana hiki me ka nui loa hooloihi i ke ola o ka hoʻomanawanui. He nui ka hana i kaʻike, a me ka hoʻomohala i kekahi e pono ai ke kanaka regimen. Oe e pono koho i ka lapaʻauʻia, a me ka laʻau heluna i mea e pale aku complications a me kaʻaoʻao 'ole.

He mea hiki ole ke kilokilo i ka hope o na maʻi like systemic vasculitis. Iapaau ana e paha i ke hoʻomau ola. Nō kāu, i ka maʻi mea maʻi, a ua hahai aku ia manawa o ka exacerbation ma ka manawa o ke kala. Mai vasculitis pinepine ole loa ola. Man mau puʻe wale akula kēlā, e kipa i ke kauka a me ka hooponopono ana symptoms.

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