Ho okumu'epekema

Peroxisome kuleana pili i. Zellweger maʻi pale

I kēia lā, ua kono oe e noonoo peroxisome kuleana pili i. He aha waiwai ka mea, i loko o ka hīnaʻi manu? ke uku i hoʻolohe i ka mea i ka maʻi hiki ke 'akomi i me ke kōkua o kēia organelle.

Ua i loko o ka kakaʻina, ka mea, ua ike i na peroxisomes - ia organelles. Ka halepaahao, ma ka huli, ka hapa o ka incredibly Ka Uluwehi O Ke akamai o nā mea a pau e hoopuni iho la iā mākou. O ke kanaka ua haku o ke keena, no a loaʻa nō he helu nui loa. A me ka halepaahao ua i mai o ke ahiahi liʻiliʻi loa, akā, e ae ia e alakai i kuokoa ke ola,ʻo ia hoʻi, e hui me ka ho okumu ana i luna 'kanu'ōiwi nā mea i pono. An hoohalike no keia mea i ka simplest hookahi-aa? Mea, a ia oukou paha i lohe ai ma ka kālaimeaola aʻo ma ke kula.

Mua mākou helu, a wehewehe i ka papa peroxisome, ua pono e maopopo mea ia mea, a pehea e hana.

peroxisomes

Mau organelles hou like moku vacuoles, kā lākou ka nui o lalo 1.5 micron. Peroxisome hoʻopuniʻia e ka lahilahiʻili lahilahi, a me ka mea hoʻokaʻawale i nā microgranules loko, mai ke kipi 'ia o ka mea a pau halepaahao. He aha hiki mākou e loaʻa i loko o ka organelle? Aia o ka Kora naʻEsau, ka mea, ua i kapaia ka nucleoid. He nui no ka maopopo i ka mea i keia aoao o ka peroxisomes mai i pili i ka nukelea 'ole a me nucleoid koʻohune. Mai hookahuli ai i këia mau manaÿo. a ia mea pinepine no laila, i ka 'akomi i nā hale mimicking nā pōaka nucleoid ciia. Ka mea, i hana mai fibrils a me nā paipu. ʻO kāna mau 'ōlelo o kēia organelle hoʻokaʻawale, mai ka peroxisomes, uratoksidoza na loko ia. 'O kēia kekahi o nā nā'ūhū. Ano, ke hāpai hou e noonoo i ka peroxisome hana i loko o ka halepaahao. Akā, ma mua ia, he kokoke nana i ka 'ole.

'ole

Ano, aole makou e hai aku i peroxisomes, me nā hale a me nā hana (e nānā papaaina) e e noonoo no hoi e mākou. I hoʻomaka me mākou e hāʻawi aku i ka kākoʻo kiʻi i loko o ka palapala o ka papaʻaina. Next, kākau mai ma au mamuli o ka 'ole a me ka hana ana o peroxisomes. Ka papaʻaina hiki ke hanaʻia e mākou, akā, nui ka mea, e hoailona oukou i ka peroxisome'ōpū mai, a oia no ka nucleotide.

Mua 15 loaʻa he peroxisome nā'ūhū. E ka nana aku ma kekahi. Kahiāuli i ka mea nui o ia mea:

  • peroxidase;
  • catalase;
  • oksidoza;
  • uratroksidaza.

A me ka papa laila hanaʻia i ka nucleotide? Kona kūlana mea e Punk mau ia nā'ūhū. E ka nānā i ke kaʻina hana o ka ho okumu i peraksisom. Ka mea, hoʻo'ōpuʻu mai na EPS, no laila mākou e hiki ke olelo aku nei au i ka wahi o ka i? Iecaianoaaiiuo o keia organelle - he CSE. Nā'ūhū i hua mai i loko:

  • EPS;
  • hyaloplasm.

Eia ka mea, Ua nui e möakäka hou i ka mea i kaʻili lahilahi, ina he wiwi, akā, ka mea, aole i komo iloko o ka Ion, a me ka haʻahaʻa hakakino kaumaha substrates. Ano, ua hiki i ka hana o peroxisomes noʻonoʻo. Outset keia organelle ia mea o ka mea nui no ka halepaahao.

oihana

Peroxisome oihana e like penei:

  • 'okesaside o ke aloha 'ona;
  • momomaʻakika'okesaside;
  • biosynthesis plasmalogens;
  • isoprenoid biosynthesis ma na holoholona;
  • biosynthesis o ka naʻokoko;
  • NDR2 kumuʻiʻo IIeEeAIEUAA;
  • hooponopono o systemic li nui;
  • ke kōkua ma ka kaʻina hana o ka hanu i loko o kanu keena, a no laila, ma luna o.

Kēia papa inoa He loa lōʻihi, no ka mea, ka mea,ʻaʻole i maopopo hoomaopopo i kekahi mau hana. Ano, ua kaumaha i ka wahi hou e kamailio e pili ana i kumuʻiʻo hoʻololi kemikala. He nui ka ike i kēia mau organelles pihaʻi me māhele e like me:

  • DNA;
  • ribosome.

Alaila, ke kumuʻiʻo hoʻololi kemikala ia lŘlŘ i loko o ka nucleus. Next o ka waiwai o ka mea maloko kaiapuni o peroxisomes. Pehea i ka 'ōlelo o ka waiwai? Ma ka 'oihana C-maʻi maika i. Ke kaʻina o keia ka mākaʻana ka loa pōkole, he 3'aminoʻakika residues.

Ka waiwai i loko o ka lapaʻau ninaninau

Mākou i noʻonoʻo i loko o ka pauku mua, i kuleana pili i ua hanaʻia e peroxisomes. Ano, he iki e pili ana i ka lapaʻauʻikepili mākaʻikaʻi organelle. Ano, ua kamailio iki e pili ana i ka maʻi i kapaia - Zellweger maʻi pale. He loa ka maʻi nui, ka mea, ua kena ae la ia e ka 'aʻe' ana o kumuʻiʻo waiwai. Nolaila, peroxisomes kaawale, o ka halepaahao, a me ka meaola like me ka a pau ia akullaʻikepili huʻi ole organelles. People e ae aku, mai kēia mau kāna hana i ka pilikia a me ka hana ana o kekahi mea nui kinoʻaneʻi loaʻa:

  • lolo;
  • ake;
  • puʻupaʻaʻelua.

Children ka poe i hanau me keia maʻi pale hiki ole ke ola i ka lōʻihi manawa, a hāʻawi pio e haʻalele mākou honua ma hope o ka loa pōkole iaʻu. I ka maʻi ua pili me ka mutation o ka organelle. Ua mea no hoi e hiki, a emi pilikia ano o ka maʻi.

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