Ola kinoMaʻi a me nā kūlana

Congenital abnormalities. arteriovenous malformation

Arteriovenous malformation - plexus ua crimped a me ka lahilahi-paʻa moku, a interconnect na aa koko a me arteries. O kŰia ke hana ma kekahi hapa o ke kino. Naʻe, i ka nui pilikia mea malformation o ka lolo moku.

Ke mau kumu o ka ulu ana o ka moku'āina ua i hookupaaia. Arteriovenous malformation, paha i ka hereditary ano, a ua manaoia e e he congenital maʻi. Penei, e loaa ana mai o keia maʻi, pilikia o ka maʻi i loa kiʻekiʻe i waena o hoahanau. Ua hōʻike 'poe akamai i kekahi mea i kuleana no ka maʻamau ulu ana i na moku ke koko i loko o nā nā'ōewe ma i mutations ke kāhea i ka ulana. Eia kekahi, syndromes ike ia, koe wale no keia maʻi nā kāna hana o ka mana o nā nā loko, a nenoai, e like me ka 'aʻe' ana o kā lākou 'ole.

E like me ka hopena o mutations i loko o nā'ōewe i ka pae'āina ma ke ana a me ka ulu ana o vascular keena hoʻololi i kā lākou mau ho okumu i, ma ka pau endothelial keena naʻau i ka pā pōhaku. Nolaila, o ka maʻamau capillary aʻeo ka hoʻolele 'ia mea kuleana no ka hoonohonoho hou ana i metabolic huahana, kinoea a me ka mahuaola i hana. Ua hiki aku i ka mea i ka halepaahao kahi i loko o ke aupuni 'a ua ka arteriovenous malformation, mai i loaa i ka pono nui o ka oxygen, a me ka pili waiwai. Penei, kā lākou hana ua kupikipikio.

Pilikua arteriovenous malformation hoʻonāukiukiʻana mai o ka ho'ēmiʻana o ke koko na lako a hiki i ka puni mau mea. Oia ka kŰia ma ka lapaau ua loaa ka inoa "aihue kŰia". Hoemiia ke koko lako ia lŘlŘ aie i ka outflow ana o na moku i ke koko i loko o pathological.

Eia kekahi, ma o ka 'ole me ka maʻamau arterial'ōnaehana, capillary a me venous puʻe kulu ia lŘlŘ ke kiʻekiʻe mai na arteries i aa koko. Ma ka hihia o ka ulana i ua waiho waho kiʻekiʻe nui iho la ia. No ka mea, o ka venous 'ole' aʻole i 'ae' ia he kiʻekiʻe puʻe hoolilo, aia no he manawa kūpono o ke kahe ana ke koko a me ka ho okumu fracture.

I ka interlacing wahi i loko o ka lolo, e hoʻoikaika i subarachnoid hemorrhage, hemorrhage ma ka lolo waiwai, a me ventricles. Ma na hihia a pau, i ke ano pinepine huikau ma ka mahuahua o intracranial puʻe, kena ae la ma ka panina o ka outflow alanui no cerebrospinal loli, likeʻole kāna hana o ka cranial nā aʻalolo.

IeAUPIIe, IAa IO ulana i symptoms hilinaʻi ma luna o kona wahi a me ka nui.

vascular malformation i ke ano hiʻona - he headache. Ka waiʻona ma ke e like i ka migraine, i ka lāʻau ikiʻai wale, a hoʻokahi-kapakahi.

Ma kekahi mau hihia, e hoʻomōhala ke kāʻili 'ana. Me ka nui o ka nui malformation e hōʻike hoailona o cerebral koko na lako i loko o ka palapala o ka lōlō.

I ka subarachnoid hemorrhage nā mea maʻi haha loa headache, pōniuniu, e like me ka pono me retching, ka luaʻi. Ma kekahi mau hihia, e hoomanawanui i lilo aku ike paka, haule i loko o ka coma. Aia i kekahi lōlō o nā wāwae, lima, blurred hihiʻo, ana, 'olelo, a me ka hikiʻole, e lawe mai purposeful ka neʻe' ana. I loa pohihihi keia hihia, i ka wa a ka poe uuku a nui o ka hemorrhage, he ano e asymptomatic.

O ka papa kuhikuhi hana o ka hana maikaʻiʻole o pathological vascular ulana i kaʻoki kino. Ma keia hihia, loaʻa nō kekahi mau ano o ka hana.

Iloko o ka lehulehu 'uao i craniotomy a me ka piha ana o ka malformation. Endovascular catheter hana komo ai ka lawelawe ana i ke kahua o ka pathology. A laila, hoʻohana kūikawā ipu lawe ano hānai interlacing artery. I ka hua radiosurgery hookahi irradiation pathological wahi, e hiki aku ai i ka make ana o ka hoololi moku.

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